OXPHOS mutations and neurodegeneration

Physiological regulation of cardiac contractility by endogenous reactive oxygen species

(2012) Á. Perjés et al.   Acta Physiologica

Trolox-Sensitive Reactive Oxygen Species Regulate Mitochondrial Morphology, Oxidative Phosphorylation and Cytosolic Calcium Handling in Healthy Cells

(2012) Felix Distelmaier et al.   ANTIOXIDANTS & REDOX SIGNALING

Mitochondrion-Derived Reactive Oxygen Species Lead to Enhanced Amyloid Beta Formation

(2012) Kristina Leuner et al.   ANTIOXIDANTS & REDOX SIGNALING

Role of Mitochondrial Ca2+ in the Regulation of Cellular Energetics

(2012) Brian Glancy et al.   BIOCHEMISTRY

Metabolic consequences of NDUFS4 gene deletion in immortalized mouse embryonic fibroblasts

(2012) Federica Valsecchi et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Compensatory upregulation of respiratory chain complexes III and IV in isolated deficiency of ATP synthase due to TMEM70 mutation

(2012) Vendula Havlíčková Karbanová et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Preservation of NADH ubiquinone-oxidoreductase activity by Src kinase-mediated phosphorylation of NDUFB10

(2012) Etienne Hebert-Chatelain et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Bioenergetic role of mitochondrial fusion and fission

(2012) Benedikt Westermann   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Reprint of: Biogenesis of the cytochrome bc1 complex and role of assembly factors

(2012) Pamela M. Smith et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Regulation of mammalian mitochondrial translation by post-translational modifications

(2012) Emine C. Koc et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

Adaptation of respiratory chain biogenesis to cytochrome c oxidase deficiency caused by SURF1 gene mutations

(2012) Nikola Kovářová et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Mitochondria: In Sickness and in Health

(2012) Jodi Nunnari et al.   CELL

NDUFA4 Is a Subunit of Complex IV of the Mammalian Electron Transport Chain

(2012) Eduardo Balsa et al.   Cell Metabolism

Supersizing the Mitochondrial Respiratory Chain

(2012) Eric A. Shoubridge   Cell Metabolism

Identification of a Protein Mediating Respiratory Supercomplex Stability

(2012) Yu-Chan Chen et al.   Cell Metabolism

Mitochondrial Complex I Plays an Essential Role in Human Respirasome Assembly

(2012) David Moreno-Lastres et al.   Cell Metabolism

Rcf1 Mediates Cytochrome Oxidase Assembly and Respirasome Formation, Revealing Heterogeneity of the Enzyme Complex

(2012) Milena Vukotic et al.   Cell Metabolism

Reactive oxygen species (ROS) homeostasis and redox regulation in cellular signaling

(2012) Paul D. Ray et al.   CELLULAR SIGNALLING

Mitochondrial changes within axons in multiple sclerosis

(2012) Graham R. Campbell et al.   CURRENT OPINION IN NEUROLOGY

Nonsense mutations in the COX1 subunit impair the stability of respiratory chain complexes rather than their assembly

(2012) Hue-Tran Hornig-Do et al.   EMBO JOURNAL

Mitochondrial quality control: a matter of life and death for neurons

(2012) Elena I Rugarli et al.   EMBO JOURNAL

Shaping the role of mitochondria in the pathogenesis of Huntington's disease

(2012) Veronica Costa et al.   EMBO JOURNAL

The intracellular redox state is a core determinant of mitochondrial fusion

(2012) Timothy Shutt et al.   EMBO REPORTS

Mitochondrial respiratory chain dysfunction: Implications in neurodegeneration

(2012) María Morán et al.   FREE RADICAL BIOLOGY AND MEDICINE

Mitochondrial Complex II Can Generate Reactive Oxygen Species at High Rates in Both the Forward and Reverse Reactions

(2012) Casey L. Quinlan et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mitochondrial division ensures the survival of postmitotic neurons by suppressing oxidative damage

(2012) Yusuke Kageyama et al.   JOURNAL OF CELL BIOLOGY

Mitochondrial redox signalling at a glance

(2012) Yvonne Collins et al.   JOURNAL OF CELL SCIENCE

White-Matter Astrocytes, Axonal Energy Metabolism, and Axonal Degeneration in Multiple Sclerosis

(2012) Melissa Cambron et al.   JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM

Brain Energy Metabolism and Blood Flow Differences in Healthy Aging

(2012) Joel Aanerud et al.   JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM

The Psychiatric Manifestations of Mitochondrial Disorders

(2012) Rebecca E. Anglin et al.   JOURNAL OF CLINICAL PSYCHIATRY

Glutathione/thioredoxin systems modulate mitochondrial H2O2emission: An experimental-computational study

(2012) Miguel Antonio Aon et al.   JOURNAL OF GENERAL PHYSIOLOGY

Reactive oxygen/nitrogen species and their functional correlations in neurodegenerative diseases

(2012) Mahesh Ramalingam et al.   JOURNAL OF NEURAL TRANSMISSION

Mitochondrial diseases

(2012) Anthony HV Schapira   LANCET

Multiple proteins with essential mitochondrial functions have glycosylated isoforms

(2012) Amanda R. Burnham-Marusich et al.   MITOCHONDRION

Rcf1 and Rcf2, Members of the Hypoxia-Induced Gene 1 Protein Family, Are Critical Components of the Mitochondrial Cytochrome bc1-Cytochrome c Oxidase Supercomplex

(2012) V. Strogolova et al.   MOLECULAR AND CELLULAR BIOLOGY

Sealing the Mitochondrial Respirasome

(2012) D. R. Winge   MOLECULAR AND CELLULAR BIOLOGY

Metabolic Communication between Astrocytes and Neurons via Bicarbonate-Responsive Soluble Adenylyl Cyclase

(2012) Hyun B. Choi et al.   NEURON

Synaptic Energy Use and Supply

(2012) Julia J. Harris et al.   NEURON

Monogenic Mitochondrial Disorders

(2012) Werner J.H. Koopman et al.   NEW ENGLAND JOURNAL OF MEDICINE

Mitochondrial nucleoid interacting proteins support mitochondrial protein synthesis

(2012) J. He et al.   NUCLEIC ACIDS RESEARCH

Altered Anesthetic Sensitivity of Mice Lacking Ndufs4, a Subunit of Mitochondrial Complex I

(2012) Albert Quintana et al.   PLoS One

Multiple phosphorylations of cytochrome c oxidase and their functions

(2012) Stefan Helling et al.   PROTEOMICS

Epilepsy in mitochondrial disorders

(2012) Josef Finsterer et al.   SEIZURE-EUROPEAN JOURNAL OF EPILEPSY

The Genetics of Mitochondrial Disease

(2012) Ryan Davis et al.   SEMINARS IN NEUROLOGY

Therapies in inborn errors of oxidative metabolism

(2012) Manuel Schiff et al.   TRENDS IN ENDOCRINOLOGY AND METABOLISM

Mitochondrial proticity and ROS signaling: lessons from the uncoupling proteins

(2012) Ryan J. Mailloux et al.   TRENDS IN ENDOCRINOLOGY AND METABOLISM

Mitochondria as a central sensor for axonal degenerative stimuli

(2012) Felipe A. Court et al.   TRENDS IN NEUROSCIENCES

Intracellular temperature mapping with a fluorescent polymeric thermometer and fluorescence lifetime imaging microscopy

(2012) Kohki Okabe et al.   Nature Communications

Mutations in Iron-Sulfur Cluster Scaffold Genes NFU1 and BOLA3 Cause a Fatal Deficiency of Multiple Respiratory Chain and 2-Oxoacid Dehydrogenase Enzymes

(2011) Jessie M. Cameron et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Aerobic Glycolysis: Meeting the Metabolic Requirements of Cell Proliferation

(2011) Sophia Y. Lunt et al.   Annual Review of Cell and Developmental Biology

Lessons in Fluctuation Correlation Spectroscopy

(2011) Michelle A. Digman et al.   Annual Review of Physical Chemistry

Strategic Role for Mitochondria in Alzheimer's Disease and Cancer

(2011) Louise Hedskog et al.   ANTIOXIDANTS & REDOX SIGNALING

Alzheimer's Disease: Redox Dysregulation As a Common Denominator for Diverse Pathogenic Mechanisms

(2011) Rommy von Bernhardi et al.   ANTIOXIDANTS & REDOX SIGNALING

Mitochondria and Cell Bioenergetics: Increasingly Recognized Components and a Possible Etiologic Cause of Alzheimer's Disease

(2011) Russell H. Swerdlow   ANTIOXIDANTS & REDOX SIGNALING

Mitochondrial Thiols in Antioxidant Protection and Redox Signaling: Distinct Roles for Glutathionylation and Other Thiol Modifications

(2011) Michael P. Murphy   ANTIOXIDANTS & REDOX SIGNALING

Redox Regulation of Mitochondrial Function

(2011) Diane E. Handy et al.   ANTIOXIDANTS & REDOX SIGNALING

Mitophagy: A Complex Mechanism of Mitochondrial Removal

(2011) Ivana Novak   ANTIOXIDANTS & REDOX SIGNALING

Why does mitochondrial complex I have so many subunits?

(2011) Judy Hirst   BIOCHEMICAL JOURNAL

A scaffold of accessory subunits links the peripheral arm and the distal proton-pumping module of mitochondrial complex I

(2011) Heike Angerer et al.   BIOCHEMICAL JOURNAL

Autophagy, mitochondria and oxidative stress: cross-talk and redox signalling

(2011) Jisun Lee et al.   BIOCHEMICAL JOURNAL

Defective mitochondrial translation differently affects the live cell dynamics of complex I subunits

(2011) Cindy E.J. Dieteren et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Gating and regulation of the cytochrome c oxidase proton pump

(2011) Shelagh Ferguson-Miller et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Mitochondrial transcription: Lessons from mouse models

(2011) Susana Peralta et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

Nucleus-encoded regulators of mitochondrial function: Integration of respiratory chain expression, nutrient sensing and metabolic stress

(2011) Richard C. Scarpulla   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

Manganese superoxide dismutase, MnSOD and its mimics

(2011) Sumitra Miriyala et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Molecules and roles of mitochondrial calcium signaling

(2011) Cristina Mammucari et al.   BIOFACTORS

Cardiolipin Affects the Supramolecular Organization of ATP Synthase in Mitochondria

(2011) Devrim Acehan et al.   BIOPHYSICAL JOURNAL

Assembly factors as a new class of disease genes for mitochondrial complex I deficiency: cause, pathology and treatment options

(2011) Jessica Nouws et al.   BRAIN

Unraveling the Biological Roles of Reactive Oxygen Species

(2011) Michael P. Murphy et al.   Cell Metabolism

Brain Energy Metabolism: Focus on Astrocyte-Neuron Metabolic Cooperation

(2011) Mireille Bélanger et al.   Cell Metabolism

Caspase cleavage of cytochrome c1 disrupts mitochondrial function and enhances cytochrome c release

(2011) Yushan Zhu et al.   CELL RESEARCH

Redox Regulation of Mitochondrial ATP Synthase

(2011) Sheng-Bing Wang et al.   CIRCULATION RESEARCH

Respiratory complex I: ‘steam engine’ of the cell?

(2011) Rouslan G Efremov et al.   CURRENT OPINION IN STRUCTURAL BIOLOGY

Cellular stress response pathways and ageing: intricate molecular relationships

(2011) Nikos Kourtis et al.   EMBO JOURNAL

Arrangement of electron transport chain components in bovine mitochondrial supercomplex I1III2IV1

(2011) Thorsten Althoff et al.   EMBO JOURNAL

Mitochondria in innate immunity

(2011) Damien Arnoult et al.   EMBO REPORTS

Respiratory chain complex I, a main regulatory target of the cAMP/PKA pathway is defective in different human diseases

(2011) Sergio Papa et al.   FEBS LETTERS

Differentiation of SH-SY5Y cells to a neuronal phenotype changes cellular bioenergetics and the response to oxidative stress

(2011) Lonnie Schneider et al.   FREE RADICAL BIOLOGY AND MEDICINE

Rotation and structure of FoF1-ATP synthase

(2011) D. Okuno et al.   JOURNAL OF BIOCHEMISTRY

Mitochondrial pathobiology in ALS

(2011) Lee J. Martin   JOURNAL OF BIOENERGETICS AND BIOMEMBRANES

Quantitative Mapping of Reversible Mitochondrial Complex I Cysteine Oxidation in a Parkinson Disease Mouse Model

(2011) Steven R. Danielson et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The Mechanism of Superoxide Production by the Antimycin-inhibited Mitochondrial Q-cycle

(2011) Casey L. Quinlan et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The Composition of Plant Mitochondrial Supercomplexes Changes with Oxygen Availability

(2011) Santiago J. Ramírez-Aguilar et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Superoxide Is Produced by the Reduced Flavin in Mitochondrial Complex I

(2011) Kenneth R. Pryde et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Evidence for Two Sites of Superoxide Production by Mitochondrial NADH-Ubiquinone Oxidoreductase (Complex I)

(2011) Jason R. Treberg et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Brain Lactate Metabolism: The Discoveries and the Controversies

(2011) Gerald A Dienel   JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM

Mitochondrial ATP synthase: architecture, function and pathology

(2011) An I. Jonckheere et al.   JOURNAL OF INHERITED METABOLIC DISEASE

Restoration of complex V deficiency caused by a novel deletion in the human TMEM70 gene normalizes mitochondrial morphology

(2011) An I. Jonckheere et al.   MITOCHONDRION

There is no evidence that mitochondria are the main source of reactive oxygen species in mammalian cells

(2011) Guy C. Brown et al.   MITOCHONDRION

The power of life—Cytochrome c oxidase takes center stage in metabolic control, cell signalling and survival

(2011) Susanne Arnold   MITOCHONDRION

Pharmacological targeting of mitochondrial complex I deficiency: The cellular level and beyond

(2011) Peggy Roestenberg et al.   MITOCHONDRION

Superresolution Fluorescence Imaging of Mitochondrial Nucleoids Reveals Their Spatial Range, Limits, and Membrane Interaction

(2011) T. A. Brown et al.   MOLECULAR AND CELLULAR BIOLOGY

NOX Isoforms and Reactive Oxygen Species in Vascular Health

(2011) R. M. Touyz et al.   MOLECULAR INTERVENTIONS

Structure of the membrane domain of respiratory complex I

(2011) Rouslan G. Efremov et al.   NATURE

Mechanical modulation of catalytic power on F1-ATPase

(2011) Rikiya Watanabe et al.   Nature Chemical Biology

Super-resolution 3D microscopy of live whole cells using structured illumination

(2011) Lin Shao et al.   NATURE METHODS

Mitochondria: The Next (Neurode)Generation

(2011) Eric A. Schon et al.   NEURON

Quantitative Glucose and ATP Sensing in Mammalian Cells

(2011) Dania C. Liemburg-Apers et al.   PHARMACEUTICAL RESEARCH

The Regulation and Physiology of Mitochondrial Proton Leak

(2011) Ajit S. Divakaruni et al.   PHYSIOLOGY

Region-Specific Expression of Mitochondrial Complex I Genes during Murine Brain Development

(2011) Stefanie Wirtz et al.   PLoS One

Solute diffusion is hindered in the mitochondrial matrix

(2011) C. E. J. Dieteren et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Interaction of complexes I, III, and IV within the bovine respirasome by single particle cryoelectron tomography

(2011) N. V. Dudkina et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Macromolecular organization of ATP synthase and complex I in whole mitochondria

(2011) K. M. Davies et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Computer-aided studies on the regulation of oxidative phosphorylation during work transitions

(2011) Bernard Korzeniewski   PROGRESS IN BIOPHYSICS & MOLECULAR BIOLOGY

Developmental aspects of respiratory chain from fetus to infancy

(2011) Constantin Yanicostas et al.   Seminars in Fetal & Neonatal Medicine

Autofluorescence microscopy: A non-destructive tool to monitor mitochondrial toxicity

(2011) Robim M. Rodrigues et al.   TOXICOLOGY LETTERS

Mitochondrial protein import: from transport pathways to an integrated network

(2011) Thomas Becker et al.   TRENDS IN BIOCHEMICAL SCIENCES

The complexity of cardiolipin in health and disease

(2011) Steven M. Claypool et al.   TRENDS IN BIOCHEMICAL SCIENCES

Design and application of genetically encoded biosensors

(2011) Amy E. Palmer et al.   TRENDS IN BIOTECHNOLOGY

Revisiting the TCA cycle: signaling to tumor formation

(2011) Nuno Raimundo et al.   TRENDS IN MOLECULAR MEDICINE

Nitric oxide in neurodegeneration: potential benefits of non-steroidal anti-inflammatories

(2011) Gayle Helane Doherty   Neuroscience Bulletin

Structural Diversity of Mitochondria

(2010) Carmen A. Mannella   Annals of the New York Academy of Sciences

The Role of Mitochondria in Reactive Oxygen Species Metabolism and Signaling

(2010) Anatoly A. Starkov   Annals of the New York Academy of Sciences

MELAS and l-arginine therapy: pathophysiology of stroke-like episodes

(2010) Yasutoshi Koga et al.   Annals of the New York Academy of Sciences

The Mitochondrial Proteome and Human Disease

(2010) Sarah E. Calvo et al.   Annual Review of Genomics and Human Genetics

Iron–Sulfur Clusters: Biogenesis, Molecular Mechanisms, and Their Functional Significance

(2010) Xiang Ming Xu et al.   ANTIOXIDANTS & REDOX SIGNALING

Detection and manipulation of mitochondrial reactive oxygen species in mammalian cells

(2010) Marleen Forkink et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Structure–function relationships in feedback regulation of energy fluxes in vivo in health and disease: Mitochondrial Interactosome

(2010) Valdur Saks et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

The regulation of OXPHOS by extramitochondrial calcium

(2010) Frank N. Gellerich et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Genetic insights into OXPHOS defect and its role in cancer

(2010) Dhyan Chandra et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Oxidative stress in skin fibroblasts cultures from patients with Parkinson's disease

(2010) Pilar del Hoyo et al.   BMC Neurology

Mitochondrial DNA mutations affect calcium handling in differentiated neurons

(2010) Andrew J. Trevelyan et al.   BRAIN

Mechanism of neurodegeneration of neurons with mitochondrial DNA mutations

(2010) A. Y. Abramov et al.   BRAIN

Calcium clearance and its energy requirements in cerebellar neurons

(2010) Maxim V. Ivannikov et al.   CELL CALCIUM

Machines that learn to segment images: a crucial technology for connectomics

(2010) Viren Jain et al.   CURRENT OPINION IN NEUROBIOLOGY

Pharmacologic effects on mitochondrial function

(2010) Bruce H. Cohen   Developmental Disabilities Research Reviews

The use of neuroimaging in the diagnosis of mitochondrial disease

(2010) Seth D. Friedman et al.   Developmental Disabilities Research Reviews

Ageing alters the supramolecular architecture of OxPhos complexes in rat brain cortex

(2010) Monika Frenzel et al.   EXPERIMENTAL GERONTOLOGY

The sites and topology of mitochondrial superoxide production

(2010) Martin D. Brand   EXPERIMENTAL GERONTOLOGY

Complex I: Inhibitors, inhibition and neurodegeneration

(2010) A.H.V. Schapira   EXPERIMENTAL NEUROLOGY

Nitrosylation and nitration of mitochondrial complex I in Parkinson's disease

(2010) Shankar J. Chinta et al.   FREE RADICAL RESEARCH

Mitochondrial dysfunction and pathology in bipolar disorder and schizophrenia

(2010) Hayley B. Clay et al.   INTERNATIONAL JOURNAL OF DEVELOPMENTAL NEUROSCIENCE

Assembly factors of human mitochondrial complex I and their defects in disease

(2010) Matthew Mckenzie et al.   IUBMB LIFE

Automated microscopy for high-content RNAi screening

(2010) Christian Conrad et al.   JOURNAL OF CELL BIOLOGY

A common pattern of brain MRI imaging in mitochondrial diseases with complex I deficiency

(2010) A. S. Lebre et al.   JOURNAL OF MEDICAL GENETICS

A neurological perspective on mitochondrial disease

(2010) Robert McFarland et al.   LANCET NEUROLOGY

S-Nitrosylation of Drp1 links excessive mitochondrial fission to neuronal injury in neurodegeneration

(2010) Tomohiro Nakamura et al.   MITOCHONDRION

Succinate dehydrogenase – Assembly, regulation and role in human disease

(2010) Jared Rutter et al.   MITOCHONDRION

Complex V TMEM70 deficiency results in mitochondrial nucleoid disorganization

(2010) Jessie M. Cameron et al.   MITOCHONDRION

Five Entry Points of the Mitochondrially Encoded Subunits in Mammalian Complex I Assembly

(2010) E. Perales-Clemente et al.   MOLECULAR AND CELLULAR BIOLOGY

The architecture of respiratory complex I

(2010) Rouslan G. Efremov et al.   NATURE

Piston drives a proton pump

(2010) Tomoko Ohnishi   NATURE

Inventory control: cytochrome c oxidase assembly regulates mitochondrial translation

(2010) David U. Mick et al.   NATURE REVIEWS MOLECULAR CELL BIOLOGY

Nitric oxide and neuronal death

(2010) Guy C. Brown   NITRIC OXIDE-BIOLOGY AND CHEMISTRY

Electron tunneling in respiratory complex I

(2010) T. Hayashi et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Bioenergetic cost of making an adenosine triphosphate molecule in animal mitochondria

(2010) I. N. Watt et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Functional Modules and Structural Basis of Conformational Coupling in Mitochondrial Complex I

(2010) C. Hunte et al.   SCIENCE

Regulation of intermediary metabolism by protein acetylation

(2010) Kun-Liang Guan et al.   TRENDS IN BIOCHEMICAL SCIENCES

Genetic background influences mitochondrial function: modeling mitochondrial disease for therapeutic development

(2010) Paule Bénit et al.   TRENDS IN MOLECULAR MEDICINE

Mitochondrial Encephalopathy, Lactic Acidosis, and Strokelike Episodes

(2009) Douglas M. Sproule et al.   Annals of the New York Academy of Sciences

The Role of Mitochondria in Apoptosis

(2009) Chunxin Wang et al.   Annual Review of Genetics

Nitric Oxide in Cell Survival: A Janus Molecule

(2009) Vittorio Calabrese et al.   ANTIOXIDANTS & REDOX SIGNALING

Mammalian Mitochondrial Complex I: Biogenesis, Regulation, and Reactive Oxygen Species Generation

(2009) Werner J.H. Koopman et al.   ANTIOXIDANTS & REDOX SIGNALING

Nuclear Redox Signaling

(2009) Margarete Lukosz et al.   ANTIOXIDANTS & REDOX SIGNALING

Nitric Oxide, Cytochrome C Oxidase, and the Cellular Response to Hypoxia

(2009) Cormac T. Taylor et al.   ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY

Supramolecular organization of ATP synthase and respiratory chain in mitochondrial membranes

(2009) Ilka Wittig et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Structure and function of mitochondrial supercomplexes

(2009) Natalya V. Dudkina et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Mitochondrial dysfunction and metabolic syndrome—looking for environmental factors

(2009) Hong Kyu Lee et al.   BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS

Mitochondria as ATP consumers in cellular pathology

(2009) Christos Chinopoulos et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Mitochondrial complex I deficiency: from organelle dysfunction to clinical disease

(2009) F. Distelmaier et al.   BRAIN

Transmitochondrial embryonic stem cells containing pathogenic mtDNA mutations are compromised in neuronal differentiation

(2009) D. M.  Kirby et al.   CELL PROLIFERATION

Mitochondrial-targeted fluorescent probes for reactive oxygen species

(2009) Bryan C Dickinson et al.   CURRENT OPINION IN CHEMICAL BIOLOGY

Drugs interfering with mitochondrial disorders

(2009) Josef Finsterer et al.   DRUG AND CHEMICAL TOXICOLOGY

Mitochondrial dynamics in human NADH:ubiquinone oxidoreductase deficiency

(2009) Peter H.G.M. Willems et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

Post-translational modifications of ATP synthase in the heart: biology and function

(2009) Lesley A. Kane et al.   JOURNAL OF BIOENERGETICS AND BIOMEMBRANES

The structure of eukaryotic and prokaryotic complex I

(2009) T. Clason et al.   JOURNAL OF STRUCTURAL BIOLOGY

Essential tremor - Neurodegenerative or nondegenerative disease towards a working definition of ET

(2009) Günther Deuschl et al.   MOVEMENT DISORDERS

Introduction to the Quantitative Analysis of Two-Dimensional Fluorescence Microscopy Images for Cell-Based Screening

(2009) Vebjorn Ljosa et al.   PLoS Computational Biology

Mitochondrial Disorders in the Nervous System

(2008) Salvatore DiMauro et al.   Annual Review of Neuroscience

Ultrastructure of the Mitochondrion and Its Bearing on Function and Bioenergetics

(2008) Giovanni Benard et al.   ANTIOXIDANTS & REDOX SIGNALING

How mitochondria produce reactive oxygen species

(2008) Michael P. Murphy   BIOCHEMICAL JOURNAL

Complex I and energy thresholds in the brain

(2008) Rashmi U. Pathak et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Diseases caused by defects of mitochondrial carriers: A review

(2008) Ferdinando Palmieri   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

The ADP and ATP transport in mitochondria and its carrier

(2008) Martin Klingenberg   BIOCHIMICA ET BIOPHYSICA ACTA-BIOMEMBRANES

Redox imbalance in Parkinson's disease

(2008) Shankar J. Chinta et al.   BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS

A critical approach to the therapy of mitochondrial respiratory chain and oxidative phosphorylation diseases

(2008) Salvatore DiMauro et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Granzyme A Cleaves a Mitochondrial Complex I Protein to Initiate Caspase-Independent Cell Death

(2008) Denis Martinvalet et al.   CELL

A Mitochondrial Protein Compendium Elucidates Complex I Disease Biology

(2008) David J. Pagliarini et al.   CELL

Mitochondrial Ca2+ homeostasis in human NADH:ubiquinone oxidoreductase deficiency☆

(2008) P WILLEMS et al.   CELL CALCIUM

Mice with Mitochondrial Complex I Deficiency Develop a Fatal Encephalomyopathy

(2008) Shane E. Kruse et al.   Cell Metabolism

Age-associated mosaic respiratory chain deficiency causes trans-neuronal degeneration

(2008) E. Dufour et al.   HUMAN MOLECULAR GENETICS

Functional dynamic compartmentalization of respiratory chain intermediate substrates: Implications for the control of energy production and mitochondrial diseases

(2008) G. Benard et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

Subunits of Mitochondrial Complex I Exist as Part of Matrix- and Membrane-associated Subcomplexes in Living Cells

(2008) Cindy E. J. Dieteren et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Lack of Cytochromecin Mouse Fibroblasts Disrupts Assembly/Stability of Respiratory Complexes I and IV

(2008) Uma D. Vempati et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Complex I Function Is Defective in Complex IV-deficientCaenorhabditis elegans

(2008) Wichit Suthammarak et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Protein Tyrosine Nitration of the Flavin Subunit Is Associated with Oxidative Modification of Mitochondrial Complex II in the Post-ischemic Myocardium

(2008) Chwen-Lih Chen et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Complex I within Oxidatively Stressed Bovine Heart Mitochondria Is Glutathionylated on Cys-531 and Cys-704 of the 75-kDa Subunit

(2008) Thomas R. Hurd et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The Mechanism of Mitochondrial Superoxide Production by the Cytochromebc1Complex

(2008) Stefan Dröse et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Cardiolipin provides an essential activating platform for caspase-8 on mitochondria

(2008) Francois Gonzalvez et al.   JOURNAL OF CELL BIOLOGY

Respiratory Complexes III and IV Are Not Essential for the Assembly/Stability of Complex I in Fungi

(2008) Marc F.P.M. Maas et al.   JOURNAL OF MOLECULAR BIOLOGY

Computer-assisted live cell analysis of mitochondrial membrane potential, morphology and calcium handling

(2008) Werner J.H. Koopman et al.   METHODS

Respiratory Active Mitochondrial Supercomplexes

(2008) Rebeca Acín-Pérez et al.   MOLECULAR CELL

Mitochondrial fragmentation in neurodegeneration

(2008) Andrew B. Knott et al.   NATURE REVIEWS NEUROSCIENCE

Generation of Reactive Oxygen Species by Mitochondrial Complex I: Implications in Neurodegeneration

(2008) Romana Fato et al.   NEUROCHEMICAL RESEARCH

Transcriptional Paradigms in Mammalian Mitochondrial Biogenesis and Function

(2008) Richard C. Scarpulla   PHYSIOLOGICAL REVIEWS

Controlling the rates of biochemical reactions and signaling networks by shape and volume changes

(2008) L. Lizana et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Control of mitochondria dynamics and oxidative metabolism by cAMP, AKAPs and the proteasome

(2008) Annalisa Carlucci et al.   TRENDS IN CELL BIOLOGY

The mitochondrial impairment, oxidative stress and neurodegeneration connection: reality or just an attractive hypothesis?

(2008) Hirokazu Fukui et al.   TRENDS IN NEUROSCIENCES

Mitochondrial off targets of drug therapy

(2008) Kendall B. Wallace   TRENDS IN PHARMACOLOGICAL SCIENCES

Investigations of the potential effects of phosphorylation of the MWFE and ESSS subunits on complex I activity and assembly

(2007) N. Yadava et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY