Modeling hallmark pathology using motor neurons derived from the family and sporadic amyotrophic lateral sclerosis patient-specific iPS cells

TDP-43 induces p53-mediated cell death of cortical progenitors and immature neurons

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Association of Mutations in TBK1 With Sporadic and Familial Amyotrophic Lateral Sclerosis and Frontotemporal Dementia

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Protein Quality Control and the Amyotrophic Lateral Sclerosis/Frontotemporal Dementia Continuum

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Modeling ALS with motor neurons derived from human induced pluripotent stem cells

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Generation and expansion of highly pure motor neuron progenitors from human pluripotent stem cells

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A cellular model for sporadic ALS using patient-derived induced pluripotent stem cells

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The changing scene of amyotrophic lateral sclerosis

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Neurofilaments at a glance

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Does a loss of TDP-43 function cause neurodegeneration?

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Specification of Midbrain Dopamine Neurons from Primate Pluripotent Stem Cells

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Effect of genetic background on phenotype variability in transgenic mouse models of amyotrophic lateral sclerosis: A window of opportunity in the search for genetic modifiers

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Genetic engineering of human pluripotent cells using TALE nucleases

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How can we improve clinical trials in amyotrophic lateral sclerosis?

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Efficient generation of transgene-free human induced pluripotent stem cells (iPSCs) by temperature-sensitive Sendai virus vectors

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Dysfunction of constitutive and inducible ubiquitin-proteasome system in amyotrophic lateral sclerosis: Implication for protein aggregation and immune response

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The “Dying-Back” Phenomenon of Motor Neurons in ALS

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Erratum: Corrigendum: Highly efficient neural conversion of human ES and iPS cells by dual inhibition of SMAD signaling

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TDP-43 mutant transgenic mice develop features of ALS and frontotemporal lobar degeneration

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Neonatal Neuronal Circuitry Shows Hyperexcitable Disturbance in a Mouse Model of the Adult-Onset Neurodegenerative Disease Amyotrophic Lateral Sclerosis

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TARDBP mutations in amyotrophic lateral sclerosis with TDP-43 neuropathology: a genetic and histopathological analysis

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TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis

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