Metabolomic responses to lumacaftor/ivacaftor in cystic fibrosis

Complex Relation Between Diet and Phospholipid Fatty Acids in Children With Cystic Fibrosis

(2017) Sara Moukarzel et al.   JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION

Plasma metabolomics in adults with cystic fibrosis during a pulmonary exacerbation: A pilot randomized study of high-dose vitamin D 3 administration

(2017) Jessica A. Alvarez et al.   METABOLISM-CLINICAL AND EXPERIMENTAL

Changes in Lipids and Inflammatory Markers after Consuming Diets High in Red Meat or Dairy for Four Weeks

(2017) Kirsty Turner et al.   Nutrients

Ivacaftor-Induced Proteomic Changes Suggest Monocyte Defects May Contribute to the Pathogenesis of Cystic Fibrosis

(2016) Katherine B. Hisert et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Metabolomic biomarkers predictive of early structural lung disease in cystic fibrosis

(2016) Charles R. Esther et al.   EUROPEAN RESPIRATORY JOURNAL

Feasibility of Early Detection of Cystic Fibrosis Acute Pulmonary Exacerbations by Exhaled Breath Condensate Metabolomics: A Pilot Study

(2016) Xiaoling Zang et al.   JOURNAL OF PROTEOME RESEARCH

Cystic fibrosis

(2016) J Stuart Elborn   LANCET

Efficacy and safety of lumacaftor/ivacaftor combination therapy in patients with cystic fibrosis homozygous for Phe508del CFTR by pulmonary function subgroup: a pooled analysis

(2016) J Stuart Elborn et al.   Lancet Respiratory Medicine

Metabolomics of pulmonary exacerbations reveals the personalized nature of cystic fibrosis disease

(2016) Robert A. Quinn et al.   PeerJ

Metabolomic Evaluation of Neutrophilic Airway Inflammation in Cystic Fibrosis

(2015) Charles R. Esther et al.   CHEST

Microbial, host and xenobiotic diversity in the cystic fibrosis sputum metabolome

(2015) Robert A Quinn et al.   ISME Journal

Cystic fibrosis and the role of gastrointestinal outcome measures in the new era of therapeutic CFTR modulation

(2015) Frank A.J.A. Bodewes et al.   Journal of Cystic Fibrosis

Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR

(2015) Claire E. Wainwright et al.   NEW ENGLAND JOURNAL OF MEDICINE

Metabolomics analysis identifies novel plasma biomarkers of cystic fibrosis pulmonary exacerbation

(2015) Theresa A. Laguna et al.   PEDIATRIC PULMONOLOGY

Lumacaftor/ivacaftor for patients homozygous for Phe508del-CFTR: should we curb our enthusiasm?

(2015) A. M. Jones et al.   THORAX

Nuclear Magnetic Resonance–based Metabolomics Discriminates Primary Ciliary Dyskinesia from Cystic Fibrosis

(2014) Paolo Montuschi et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Precision microbiome reconstitution restores bile acid mediated resistance to Clostridium difficile

(2014) Charlie G. Buffie et al.   NATURE

Antibiotic-induced shifts in the mouse gut microbiome and metabolome increase susceptibility to Clostridium difficile infection

(2014) Casey M. Theriot et al.   Nature Communications

Xenobiotics Shape the Physiology and Gene Expression of the Active Human Gut Microbiome

(2013) Corinne Ferrier Maurice et al.   CELL

Serum metabolomics indicate altered cellular energy metabolism in children with cystic fibrosis

(2013) Elizabeth Joseloff et al.   PEDIATRIC PULMONOLOGY

Microbiota and Metabolite Profiling Reveal Specific Alterations in Bacterial Community Structure and Environment in the Cystic Fibrosis Airway during Exacerbation

(2013) Kate B. Twomey et al.   PLoS One

Dietary-fat-induced taurocholic acid promotes pathobiont expansion and colitis in Il10 −/− mice

(2012) Suzanne Devkota et al.   NATURE

Structure, function and diversity of the healthy human microbiome

(2012)   NATURE

A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation

(2011) Bonnie W. Ramsey et al.   NEW ENGLAND JOURNAL OF MEDICINE

NMR spectroscopy metabolomic profiling of exhaled breath condensate in patients with stable and unstable cystic fibrosis

(2011) Paolo Montuschi et al.   THORAX

Metabolomic Profiling Reveals Biochemical Pathways and Biomarkers Associated with Pathogenesis in Cystic Fibrosis Cells

(2010) Diana R. Wetmore et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Metabolomics of Volatile Organic Compounds in Cystic Fibrosis Patients and Controls

(2010) Charlotte M H H T Robroeks et al.   PEDIATRIC RESEARCH

Metabolomic analysis of bronchoalveolar lavage fluid from cystic fibrosis patients

(2009) Justyna E. Wolak et al.   BIOMARKERS

Ceramide accumulation mediates inflammation, cell death and infection susceptibility in cystic fibrosis

(2008) Volker Teichgräber et al.   NATURE MEDICINE