Stimulation of mTOR-independent autophagy and mitophagy by rilmenidine exacerbates the phenotype of transgenic TDP-43 mice

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TDP-43 induces mitochondrial damage and activates the mitochondrial unfolded protein response

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Distinct roles for motor neuron autophagy early and late in the SOD1G93Amouse model of ALS

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Autophagic down-regulation in motor neurons remarkably prolongs the survival of ALS mice

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Wild type human TDP-43 potentiates ALS-linked mutant TDP-43 driven progressive motor and cortical neuron degeneration with pathological features of ALS

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Loss and gain of Drosophila TDP-43 impair synaptic efficacy and motor control leading to age-related neurodegeneration by loss-of-function phenotypes

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The ALS disease-associated mutant TDP-43 impairs mitochondrial dynamics and function in motor neurons

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ALS-linked TDP-43 mutations produce aberrant RNA splicing and adult-onset motor neuron disease without aggregation or loss of nuclear TDP-43

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Blood pressure measurements in a transgenic SOD1-G93A mouse model of amyotrophic lateral sclerosis

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Mitochondrial dysfunction in human TDP-43 transfected NSC34 cell lines and the protective effect of dimethoxy curcumin

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Rapamycin treatment augments motor neuron degeneration in SOD1G93Amouse model of amyotrophic lateral sclerosis

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Rilmenidine attenuates toxicity of polyglutamine expansions in a mouse model of Huntington's disease

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Cytoplasmic Mislocalization of TDP-43 Is Toxic to Neurons and Enhanced by a Mutation Associated with Familial Amyotrophic Lateral Sclerosis

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Wild-Type Human TDP-43 Expression Causes TDP-43 Phosphorylation, Mitochondrial Aggregation, Motor Deficits, and Early Mortality in Transgenic Mice

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PINK1/Parkin-mediated mitophagy is dependent on VDAC1 and p62/SQSTM1

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Lithium delays progression of amyotrophic lateral sclerosis

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