Small heat-shock protein HSPB3 promotes myogenesis by regulating the lamin B receptor

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RNA-Seq analysis reveals pluripotency-associated genes and their interaction networks in human embryonic stem cells

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Skeletal Muscle Extracellular Matrix – What Do We Know About Its Composition, Regulation, and Physiological Roles? A Narrative Review

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Stbd1 promotes glycogen clustering during endoplasmic reticulum stress and supports survival of mouse myoblasts

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Rhabdomyosarcoma

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Metascape provides a biologist-oriented resource for the analysis of systems-level datasets

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Histone hyperacetylation disrupts core gene regulatory architecture in rhabdomyosarcoma

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Novel SBF2 mutations and clinical spectrum of Charcot-Marie-Tooth neuropathy type 4B2

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Small heat shock protein B3 (HSPB3 ) mutation in an axonal Charcot-Marie-Tooth disease family

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Small heat shock proteins: Simplicity meets complexity

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Shaping proteostasis at the cellular, tissue, and organismal level

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ER stress and the unfolded protein response in neurodegeneration

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Aberrant Compartment Formation by HSPB2 Mislocalizes Lamin A and Compromises Nuclear Integrity and Function

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Myogenic regulatory transcription factors regulate growth in rhabdomyosarcoma

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Lamin B Receptor: Interplay between Structure, Function and Localization

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Dynamics and Structure-Function Relationships of the Lamin B Receptor (LBR)

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HSPB3 protein is expressed in motoneurons and induces their survival after lesion-induced degeneration

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The extracellular matrix: Tools and insights for the “omics” era

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A Remodeled Hsp90 Molecular Chaperone Ensemble with the Novel Cochaperone Aarsd1 Is Required for Muscle Differentiation

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Differentiation of control and ALS mutant human iPSCs into functional skeletal muscle cells, a tool for the study of neuromuscolar diseases

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A Differentiation Transcription Factor Establishes Muscle-Specific Proteostasis in Caenorhabditis elegans

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The Lamin B receptor is essential for cholesterol synthesis and perturbed by disease-causing mutations

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Hanging on for the ride: Adhesion to the extracellular matrix mediates cellular responses in skeletal muscle morphogenesis and disease

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ALS mutant FUS proteins are recruited into stress granules in induced pluripotent stem cell-derived motoneurons

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Recessive hereditary motor and sensory neuropathy caused byIGHMBP2gene mutation

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LBR and Lamin A/C Sequentially Tether Peripheral Heterochromatin and Inversely Regulate Differentiation

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SET binding factor 1 (SBF1) mutation causes Charcot-Marie-Tooth disease type 4B3

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Inner nuclear membrane proteins: impact on human disease

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The Role of Intrinsically Disordered Regions in the Structure and Functioning of Small Heat Shock Proteins

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Transcriptional regulation of small HSP—HSF1 and beyond

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Notch3 and Mef2c Proteins Are Mutually Antagonistic via Mkp1 Protein and miR-1/206 MicroRNAs in Differentiating Myoblasts

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Mutations in the satellite cell gene MEGF10 cause a recessive congenital myopathy with minicores

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Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response

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From loss to gain: role for SUN1 in laminopathies

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The Unfolded Protein Response Mediates Adaptation to Exercise in Skeletal Muscle through a PGC-1α/ATF6α Complex

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The extracellular matrix dimension of skeletal muscle development

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Transcriptional mechanisms regulating skeletal muscle differentiation, growth and homeostasis

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Overview of the Matrisome--An Inventory of Extracellular Matrix Constituents and Functions

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The unfolded protein response is activated in skeletal muscle by high-fat feeding: potential role in the downregulation of protein synthesis

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Interfering with the connection between the nucleus and the cytoskeleton affects nuclear rotation, mechanotransduction and myogenesis

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Fusion Gene–Negative Alveolar Rhabdomyosarcoma Is Clinically and Molecularly Indistinguishable From Embryonal Rhabdomyosarcoma

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Mutant small heat shock protein B3 causes motor neuropathy: Utility of a candidate gene approach

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Impact of ageing on muscle cell regeneration

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The Small Heat-Shock Proteins HSPB2 and HSPB3 Form Well-defined Heterooligomers in a Unique 3 to 1 Subunit Ratio

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Novel Subtype-Specific Genes Identify Distinct Subpopulations of Callosal Projection Neurons

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BAC TransgeneOmics: a high-throughput method for exploration of protein function in mammals

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RNA association or phosphorylation of the RS domain prevents aggregation of RS domain-containing proteins

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