- Home
- Publications
- Publication Search
- Publication Details
Title
Recent advances in α-1-antitrypsin deficiency-related lung disease
Authors
Keywords
-
Journal
Expert Review of Respiratory Medicine
Volume 7, Issue 3, Pages 213-230
Publisher
Informa UK Limited
Online
2013-06-04
DOI
10.1586/ers.13.20
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- Significance of Bronchiectasis in Patients with α1-Antitrypsin Deficiency
- (2013) Edward D. Chan et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- α 1 -Antitrypsin Phenotypes and Associated Serum Protein Concentrations in a Large Clinical Population
- (2013) Joshua A. Bornhorst et al. CHEST
- Detection of Alpha-1 Antitrypsin Deficiency in the US
- (2012) Michael Campos et al. AMERICAN JOURNAL OF MEDICINE
- Endobronchial valve deployment in severe α-1 antitrypsin deficiency emphysema: a case series
- (2012) Mary Majella Tuohy et al. Clinical Respiratory Journal
- A Randomised, Placebo-Controlled, Dose-Finding Study Of AZD9668, An Oral Inhibitor of Neutrophil Elastase, in Patients with Chronic Obstructive Pulmonary Disease Treated with Tiotropium
- (2012) Claus Vogelmeier et al. COPD-Journal of Chronic Obstructive Pulmonary Disease
- Randomised controlled trial for emphysema with a selective agonist of the γ-type retinoic acid receptor
- (2012) Jan Stolk et al. EUROPEAN RESPIRATORY JOURNAL
- Proteinase 3 activity in sputum from subjects with alpha-1-antitrypsin deficiency and COPD
- (2012) Nicola J. Sinden et al. EUROPEAN RESPIRATORY JOURNAL
- Efficacy, safety and effect on biomarkers of AZD9668 in cystic fibrosis
- (2012) J. Stuart Elborn et al. EUROPEAN RESPIRATORY JOURNAL
- Sustained miRNA-mediated Knockdown of Mutant AAT With Simultaneous Augmentation of Wild-type AAT Has Minimal Effect on Global Liver miRNA Profiles
- (2012) Christian Mueller et al. MOLECULAR THERAPY
- Persistent Systemic Inflammation is Associated with Poor Clinical Outcomes in COPD: A Novel Phenotype
- (2012) Alvar Agustí et al. PLoS One
- Association of IREB2 and CHRNA3 polymorphisms with airflow obstruction in severe alpha-1 antitrypsin deficiency
- (2012) Woo Jin Kim et al. RESPIRATORY RESEARCH
- Clinical validity of plasma and urinary desmosine as biomarkers for chronic obstructive pulmonary disease
- (2012) Jeffrey T-J Huang et al. THORAX
- Rare alpha-1-antitrypsin variants: are they really so rare?
- (2012) Francisco Rodriguez-Frias et al. Therapeutic Advances in Respiratory Disease
- Prevalence of α1-antitrypsin deficiency alleles PI*S and PI*Z worldwide and effective screening for each of the five phenotypic classes PI*MS, PI*MZ, PI*SS, PI*SZ, and PI*ZZ: a comprehensive review
- (2012) Frederick J. de Serres et al. Therapeutic Advances in Respiratory Disease
- Long-term Variability of Desmosine/Isodesmosine as Biomarker in Alpha-1-antritrypsin Deficiency–related COPD
- (2011) Laura Fregonese et al. COPD-Journal of Chronic Obstructive Pulmonary Disease
- Molecular basis of α1-antitrypsin deficiency revealed by the structure of a domain-swapped trimer
- (2011) Masayuki Yamasaki et al. EMBO REPORTS
- Total desmosines in plasma and urine correlate with lung function
- (2011) C.A. Lindberg et al. EUROPEAN RESPIRATORY JOURNAL
- Matrix metalloproteinases in COPD
- (2011) A. Churg et al. EUROPEAN RESPIRATORY JOURNAL
- Phase 2 Clinical Trial of a Recombinant Adeno-Associated Viral Vector Expressing α1-Antitrypsin: Interim Results
- (2011) Terence R. Flotte et al. HUMAN GENE THERAPY
- Targeted gene correction of α1-antitrypsin deficiency in induced pluripotent stem cells
- (2011) Kosuke Yusa et al. NATURE
- The fibrinogen cleavage product A -Val360, a specific marker of neutrophil elastase activity in vivo
- (2011) R. I. Carter et al. THORAX
- The role of proteases, endoplasmic reticulum stress andSERPINA1heterozygosity in lung disease and α-1 anti-trypsin deficiency
- (2011) Catherine M Greene et al. Expert Review of Respiratory Medicine
- Alpha1-antitrypsin deficiency-related alleles Z and S and the risk of Wegener's granulomatosis
- (2010) Alfred D. Mahr et al. ARTHRITIS AND RHEUMATISM
- α; 1 -Antitrypsin Protease Inhibitor MZ Heterozygosity Is Associated With Airflow Obstruction in Two Large Cohorts
- (2010) Inga-Cecilie Sørheim et al. CHEST
- Asthma and COPD in Alpha-1 Antitrypsin Deficiency. Evidence for the Dutch Hypothesis
- (2010) Edward Eden COPD-Journal of Chronic Obstructive Pulmonary Disease
- Laboratory testing of individuals with severe 1-antitrypsin deficiency in three European centres
- (2010) M. Miravitlles et al. EUROPEAN RESPIRATORY JOURNAL
- A novel monoclonal antibody to characterize pathogenic polymers in liver disease associated with α1-antitrypsin deficiency
- (2010) Elena Miranda et al. HEPATOLOGY
- Preclinical Evaluation of a Recombinant Adeno-Associated Virus Vector Expressing Human Alpha-1 Antitrypsin Made Using a Recombinant Herpes Simplex Virus Production Method
- (2010) Jeffrey D. Chulay et al. HUMAN GENE THERAPY
- Adipose tissue-derived mesenchymal stem cell-based liver gene delivery
- (2010) Hong Li et al. JOURNAL OF HEPATOLOGY
- Ex Vivo Transduction and Transplantation of Bone Marrow Cells for Liver Gene Delivery of α1-Antitrypsin
- (2010) Hong Li et al. MOLECULAR THERAPY
- A Randomized Study of Endobronchial Valves for Advanced Emphysema
- (2010) Frank C. Sciurba et al. NEW ENGLAND JOURNAL OF MEDICINE
- Defining the mechanism of polymerization in the serpinopathies
- (2010) U. I. Ekeowa et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Impact of non-linear smoking effects on the identification of gene-by-smoking interactions in COPD genetics studies
- (2010) P. J. Castaldi et al. THORAX
- Establishment of lentiviral-vector-mediated model of human alpha-1 antitrypsin delivery into hepatocyte-like cells differentiated from mesenchymal stem cells
- (2010) Mahboobe Ghaedi et al. TISSUE & CELL
- Augmentation therapy in alpha-1 antitrypsin deficiency: advances and controversies
- (2010) Adriano R. Tonelli et al. Therapeutic Advances in Respiratory Disease
- Conformational Pathology of the Serpins: Themes, Variations, and Therapeutic Strategies
- (2009) Bibek Gooptu et al. Annual Review of Biochemistry
- Phenotypic Differences in Alpha 1 Antitrypsin-Deficient Sibling Pairs May Relate to Genetic Variation
- (2009) Alice M. Wood et al. COPD-Journal of Chronic Obstructive Pulmonary Disease
- Augmentation Therapy for α1Antitrypsin Deficiency: A Meta-Analysis
- (2009) Kenneth R. Chapman et al. COPD-Journal of Chronic Obstructive Pulmonary Disease
- Rate of progression of lung function impairment in 1-antitrypsin deficiency
- (2009) P. A. Dawkins et al. EUROPEAN RESPIRATORY JOURNAL
- Exploring the role of CT densitometry: a randomised study of augmentation therapy in 1-antitrypsin deficiency
- (2009) A. Dirksen et al. EUROPEAN RESPIRATORY JOURNAL
- Mechanisms of emphysema in 1-antitrypsin deficiency: molecular and cellular insights
- (2009) B. Gooptu et al. EUROPEAN RESPIRATORY JOURNAL
- Sustained transgene expression despite T lymphocyte responses in a clinical trial of rAAV1-AAT gene therapy
- (2009) M. L. Brantly et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Sustained Expression of α1-Antitrypsin after Transplantation of Manipulated Hematopoietic Stem Cells
- (2008) Andrew A. Wilson et al. AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY
- Evaluation of COPD Longitudinally to Identify Predictive Surrogate End-points (ECLIPSE)
- (2008) J. Vestbo et al. EUROPEAN RESPIRATORY JOURNAL
- Heritability of Lung Function in Severe Alpha-1 Antitrypsin Deficiency
- (2008) D.L. DeMeo et al. HUMAN HEREDITY
- The molecular aetiology of the serpinopathies
- (2008) M DAVIES et al. INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY
- Small-molecule peptides inhibit Z α1-antitrypsin polymerization
- (2008) Yi-Pin Chang et al. JOURNAL OF CELLULAR AND MOLECULAR MEDICINE
- Crystal structure of a stable dimer reveals the molecular basis of serpin polymerization
- (2008) Masayuki Yamasaki et al. NATURE
- IL10Polymorphisms Are Associated with Airflow Obstruction in Severe α1-Antitrypsin Deficiency
- (2007) Dawn L. DeMeo et al. AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY
Find Funding. Review Successful Grants.
Explore over 25,000 new funding opportunities and over 6,000,000 successful grants.
ExploreFind the ideal target journal for your manuscript
Explore over 38,000 international journals covering a vast array of academic fields.
Search