Cystic fibrosis: An update for clinicians. Part 2: Hepatobiliary and pancreatic manifestations

Delayed release pancrelipase for the treatment of pancreatic exocrine insufficiency associated with cystic fibrosis

(2016) Susan Baker   Therapeutics and Clinical Risk Management

Simultaneous liver–pancreas transplantation for cystic fibrosis-related liver disease: A multicenter experience

(2014) R.H.J. Bandsma et al.   Journal of Cystic Fibrosis

Improved screening for cystic fibrosis-related diabetes by an integrated care team using an algorithm

(2014) Maria Socorro Rayas et al.   PEDIATRIC PULMONOLOGY

Self-reported use of vitamins and other nutritional supplements in adult patients with cystic fibrosis. Is daily practice in concordance with recommendations?

(2013) Francis M. Hollander et al.   INTERNATIONAL JOURNAL FOR VITAMIN AND NUTRITION RESEARCH

Importance of screening with oral glucose tolerance test for early diagnosis of cystic fibrosis-related diabetes mellitus

(2013) Renata Maria Noronha et al.   PEDIATRIC DIABETES

Increased detection of cystic-fibrosis-related diabetes in Australia

(2011) M. Rana et al.   ARCHIVES OF DISEASE IN CHILDHOOD

Outcomes of patients with cystic fibrosis undergoing lung transplantation with and without cystic fibrosis-associated liver cirrhosis*

(2011) E.F. Nash et al.   CLINICAL TRANSPLANTATION

Cystic fibrosis-cirrhosis, portal hypertension, and liver biopsy: Reply

(2011) Peter J. Lewindon et al.   HEPATOLOGY

Noncirrhotic presinusoidal portal hypertension is common in cystic fibrosis-associated liver disease

(2011) Peter Witters et al.   HEPATOLOGY

International phase III trial of liprotamase efficacy and safety in pancreatic-insufficient cystic fibrosis patients

(2011) Drucy Borowitz et al.   Journal of Cystic Fibrosis

Persistent fat malabsorption in cystic fibrosis; lessons from patients and mice

(2011) M. Wouthuyzen-Bakker et al.   Journal of Cystic Fibrosis

Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease

(2011) Dominique Debray et al.   Journal of Cystic Fibrosis

Growth Hormone Therapy Improves Growth in Children with Cystic Fibrosis Related Liver Disease

(2011) M.S. Stalvey et al.   JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM

Low-dose insulin therapy in patients with cystic fibrosis and early-stage insulinopenia prevents deterioration of lung function: a 3-year prospective study

(2011) Stanislava Koloušková et al.   JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM

Benefit of liver transplantation in patients with cystic fibrosis

(2011) Bruno Gridelli   Nature Reviews Gastroenterology & Hepatology

The Etiology of Acute Recurrent Pancreatitis in Children

(2011) Vincenzina Lucidi et al.   PANCREAS

Cystic Fibrosis Related Diabetes (CFRD)-The End Stage of Progressive Insulin Deficiency

(2011) Shihab Hameed et al.   PEDIATRIC PULMONOLOGY

Treatment recommendations for cystic fibrosis-related diabetes: too little, too late?

(2011) B. Nathan et al.   THORAX

Outcome in Cystic Fibrosis Liver Disease

(2010) Marion Rowland et al.   AMERICAN JOURNAL OF GASTROENTEROLOGY

Pathology of Gastrointestinal Organs in a Porcine Model of Cystic Fibrosis

(2010) David K. Meyerholz et al.   AMERICAN JOURNAL OF PATHOLOGY

MRI appearance of the pancreas in patients with cystic fibrosis: a comparison of pancreas volume in diabetic and non-diabetic patients

(2010) I M Sequeiros et al.   BRITISH JOURNAL OF RADIOLOGY

Clinical Care Guidelines for Cystic Fibrosis-Related Diabetes: A position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society

(2010) A. Moran et al.   DIABETES CARE

Type of CFTR Mutation Determines Risk of Pancreatitis in Patients With Cystic Fibrosis

(2010) Chee Y. Ooi et al.   GASTROENTEROLOGY

Importance of hepatic fibrosis in cystic fibrosis and the predictive value of liver biopsy

(2010) Peter J. Lewindon et al.   HEPATOLOGY

Effect of an antioxidant-rich multivitamin supplement in cystic fibrosis

(2010) Scott D. Sagel et al.   Journal of Cystic Fibrosis

Liver transplantation in patients with cystic fibrosis: Analysis of united network for organ sharing data

(2010) Manuel Mendizabal et al.   LIVER TRANSPLANTATION

Independent Contribution of Common CFTR Variants to Chronic Pancreatitis

(2010) Rafael de Cid et al.   PANCREAS

Transient elastography in patients with cystic fibrosis

(2010) Renaud Menten et al.   PEDIATRIC RADIOLOGY

Isolated liver transplantation in children with cystic fibrosis - An Australian experience

(2010) Scott Nightingale et al.   PEDIATRIC TRANSPLANTATION

Tests of pancreatic exocrine function – Clinical significance in pancreatic and non-pancreatic disorders

(2009) Jutta Keller et al.   BEST PRACTICE & RESEARCH IN CLINICAL GASTROENTEROLOGY

Hepatobiliary disease in patients with cystic fibrosis

(2009) Katie Moyer et al.   CURRENT OPINION IN GASTROENTEROLOGY

Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality

(2009) A. Moran et al.   DIABETES CARE

The changing face of the exocrine pancreas in cystic fibrosis: the correlation between pancreatic status, pancreatitis and cystic fibrosis genotype

(2009) Arie Augarten et al.   EUROPEAN JOURNAL OF GASTROENTEROLOGY & HEPATOLOGY

Genetic Modifiers of Liver Disease in Cystic Fibrosis

(2009) Jaclyn R. Bartlett   JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION

Hepatobiliary Abnormalities and Disease in Cystic Fibrosis

(2009) Sidharth Bhardwaj et al.   JOURNAL OF CLINICAL GASTROENTEROLOGY

Exocrine Pancreatic Function Testing in Patients With Cystic Fibrosis and Pancreatic Sufficiency: A Correlation Study

(2009) Amir Weintraub et al.   JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION

Efficacy and Tolerability of Creon for Children in Infants and Toddlers With Pancreatic Exocrine Insufficiency Caused by Cystic Fibrosis

(2009) Carla Colombo et al.   PANCREAS

Persistence of Essential Fatty Acid Deficiency in Cystic Fibrosis Despite Nutritional Therapy

(2009) Luis Aldámiz-Echevarría et al.   PEDIATRIC RESEARCH

Pathophysiological basis of liver disease in cystic fibrosis employing a ΔF508 mouse model

(2008) Folke Freudenberg et al.   AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY

Fibrogenesis in pediatric cholestatic liver disease: Role of taurocholate and hepatocyte-derived monocyte chemotaxis protein-1 in hepatic stellate cell recruitment

(2008) Grant A. Ramm et al.   HEPATOLOGY

Fluid flow induces mechanosensitive ATP release, calcium signalling and Cl−transport in biliary epithelial cells through a PKCζ-dependent pathway

(2008) Kangmee Woo et al.   JOURNAL OF PHYSIOLOGY-LONDON

Comparison of ultrasound and biopsy findings in children with cystic fibrosis related liver disease

(2007) Peter R. Mueller-Abt et al.   Journal of Cystic Fibrosis