Pseudomonas aeruginosa in Cystic Fibrosis Patients With G551D-CFTR Treated With Ivacaftor

Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis

(2014) Steven M. Rowe et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Antibacterial properties of the CFTR potentiator ivacaftor

(2014) Leah R. Reznikov et al.   Journal of Cystic Fibrosis

The predictive potential of the sweat chloride test in cystic fibrosis patients with the G551D mutation

(2013) Verena I. Seliger et al.   Journal of Cystic Fibrosis

Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung

(2012) Alejandro A. Pezzulo et al.   NATURE

Clearance of initial mucoidPseudomonas aeruginosain patients with cystic fibrosis

(2012) Robert Bradley Troxler et al.   PEDIATRIC PULMONOLOGY

Comparative Efficacy and Safety of 4 Randomized Regimens to Treat Early Pseudomonas aeruginosa Infection in Children With Cystic Fibrosis

(2011) Miriam M. Treggiari   ARCHIVES OF PEDIATRICS & ADOLESCENT MEDICINE

A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation

(2011) Bonnie W. Ramsey et al.   NEW ENGLAND JOURNAL OF MEDICINE

Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis

(2011) Nicole Mayer-Hamblett et al.   PEDIATRIC PULMONOLOGY

The Changing Microbial Epidemiology in Cystic Fibrosis

(2010) J. J. LiPuma   CLINICAL MICROBIOLOGY REVIEWS

Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTRMutation

(2010) Frank J. Accurso et al.   NEW ENGLAND JOURNAL OF MEDICINE

Respiratory Microbiology of Patients With Cystic Fibrosis in the United States, 1995 to 2005

(2009) Samiya Razvi et al.   CHEST

Occurrence and relevance of filamentous fungi in respiratory secretions of patients with cystic fibrosis – a review

(2009) Marc Pihet et al.   MEDICAL MYCOLOGY

Acquisition and eradication of P. aeruginosa in young children with cystic fibrosis

(2008) T. A. Douglas et al.   EUROPEAN RESPIRATORY JOURNAL

Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience

(2008) C.R. Hansen et al.   Journal of Cystic Fibrosis