Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis
Published 2014 View Full Article
- Home
- Publications
- Publication Search
- Publication Details
Title
Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis
Authors
Keywords
-
Journal
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
Volume 190, Issue 2, Pages 175-184
Publisher
American Thoracic Society
Online
2014-06-14
DOI
10.1164/rccm.201404-0703oc
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with aG551DMutation
- (2013) Jane C. Davies et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Change in Sweat Chloride as a Clinical End Point in Cystic Fibrosis Clinical Trials
- (2013) Anthony G. Durmowicz et al. CHEST
- Multisite Comparison of Mucociliary and Cough Clearance Measures Using Standardized Methods
- (2013) William D. Bennett et al. Journal of Aerosol Medicine and Pulmonary Drug Delivery
- Defining the disease liability of variants in the cystic fibrosis transmembrane conductance regulator gene
- (2013) Patrick R Sosnay et al. NATURE GENETICS
- Sixty-five years since the New York heat wave: Advances in sweat testing for cystic fibrosis
- (2013) Jake T.B. Collie et al. PEDIATRIC PULMONOLOGY
- Inflammation and Airway Microbiota during Cystic Fibrosis Pulmonary Exacerbations
- (2013) Edith T. Zemanick et al. PLoS One
- The Cystic Fibrosis Intestine
- (2013) R. C. De Lisle et al. Cold Spring Harbor Perspectives in Medicine
- Personalized Medicine in Cystic Fibrosis
- (2012) John P. Clancy et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- β-Adrenergic Sweat Secretion as a Diagnostic Test for Cystic Fibrosis
- (2012) Paul Quinton et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Sputum Biomarkers of Inflammation and Lung Function Decline in Children with Cystic Fibrosis
- (2012) Scott D. Sagel et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Gastrointestinal Complications of Cystic Fibrosis
- (2012) Daniel Gelfond et al. Clinical Gastroenterology and Hepatology
- Intestinal pH and Gastrointestinal Transit Profiles in Cystic Fibrosis Patients Measured by Wireless Motility Capsule
- (2012) Daniel Gelfond et al. DIGESTIVE DISEASES AND SCIENCES
- Regulatory Aspects of Phase 3 Endpoints for New Inhaled Antibiotics for Cystic Fibrosis Patients with Chronic Pseudomonas aeruginosa Infections
- (2012) Alan Bruce Montgomery et al. Journal of Aerosol Medicine and Pulmonary Drug Delivery
- Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype
- (2012) Jenny K. Gustafsson et al. JOURNAL OF EXPERIMENTAL MEDICINE
- Intractable cough in a preterm infant with ventriculoperitoneal shunt
- (2012) Ronen Bar-Yoseph et al. PEDIATRIC PULMONOLOGY
- Progress in cystic fibrosis and the CF Therapeutics Development Network
- (2012) Steven M Rowe et al. THORAX
- A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation
- (2011) Bonnie W. Ramsey et al. NEW ENGLAND JOURNAL OF MEDICINE
- Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis
- (2011) Nicole Mayer-Hamblett et al. PEDIATRIC PULMONOLOGY
- Role of epithelial HCO3− transport in mucin secretion: lessons from cystic fibrosis
- (2010) Paul M. Quinton AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY
- Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTRMutation
- (2010) Frank J. Accurso et al. NEW ENGLAND JOURNAL OF MEDICINE
- Airway Microbiota and Pathogen Abundance in Age-Stratified Cystic Fibrosis Patients
- (2010) Michael J. Cox et al. PLoS One
- Determination of the Minimal Clinically Important Difference Scores for the Cystic Fibrosis Questionnaire-Revised Respiratory Symptom Scale in Two Populations of Patients With Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
- (2009) Alexandra L. Quittner et al. CHEST
- Patient-reported respiratory symptoms in cystic fibrosis
- (2009) C.H. Goss et al. Journal of Cystic Fibrosis
Find the ideal target journal for your manuscript
Explore over 38,000 international journals covering a vast array of academic fields.
SearchBecome a Peeref-certified reviewer
The Peeref Institute provides free reviewer training that teaches the core competencies of the academic peer review process.
Get Started