Neuroimaging of inherited metabolic disorders producing seizures

Both MRI with FLAIR and T2, diffusion and post-contrast T1 imaging, as well as proton MRS, allow for defining an approach to evaluating MRI and MRS in neurometabolic diseases producing seizures. Examples of this approach are given here in a limited number of cases, recognizing that a more comprehensive review is beyond the scope of this paper. (C) 2011 The Japanese Society of Child Neurology. Published by Elsevier B.V. All rights reserved.