Hepatocytes contribute to residual glucose production in a mouse model for glycogen storage disease type Ia

Clinical and biochemical heterogeneity between patients with glycogen storage disease type IA: the added value of CUSUM for metabolic control

(2017) Fabian Peeks et al.   JOURNAL OF INHERITED METABOLIC DISEASE

A Next Generation Multiscale View of Inborn Errors of Metabolism

(2016) Carmen A. Argmann et al.   Cell Metabolism

Starch Binding Domain-containing Protein 1 Plays a Dominant Role in Glycogen Transport to Lysosomes in Liver

(2016) Tao Sun et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Induction of autophagy improves hepatic lipid metabolism in glucose-6-phosphatase deficiency

(2016) Benjamin L. Farah et al.   JOURNAL OF HEPATOLOGY

Role of glycogen phosphorylase in liver glycogen metabolism

(2015) Loranne Agius   MOLECULAR ASPECTS OF MEDICINE

Dietary carbohydrate and control of hepatic gene expression: mechanistic links from ATP and phosphate ester homeostasis to the carbohydrate-response element-binding protein

(2015) Loranne Agius   PROCEEDINGS OF THE NUTRITION SOCIETY

Targeted deletion of kidney glucose-6 phosphatase leads to nephropathy

(2014) Julie Clar et al.   KIDNEY INTERNATIONAL

Intestinal gluconeogenesis is crucial to maintain a physiological fasting glycemia in the absence of hepatic glucose production in mice

(2013) Armelle Penhoat et al.   METABOLISM-CLINICAL AND EXPERIMENTAL

Control of Blood Glucose in the Absence of Hepatic Glucose Production During Prolonged Fasting in Mice: Induction of Renal and Intestinal Gluconeogenesis by Glucagon

(2011) E. Mutel et al.   DIABETES

Natural History of Hepatocellular Adenoma Formation in Glycogen Storage Disease Type I

(2011) David Q. Wang et al.   JOURNAL OF PEDIATRICS

Starch Binding Domain-containing Protein 1/Genethonin 1 Is a Novel Participant in Glycogen Metabolism

(2010) Sixin Jiang et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Targeted deletion of liver glucose-6 phosphatase mimics glycogen storage disease type 1a including development of multiple adenomas

(2010) Elodie Mutel et al.   JOURNAL OF HEPATOLOGY

Chaperone Activity of Bicyclic Nojirimycin Analogues for Gaucher Mutations in Comparison withN-(n-nonyl)Deoxynojirimycin

(2009) Zhuo Luan et al.   CHEMBIOCHEM

Quantitation of magnetic resonance spectroscopy signals: the jMRUI software package

(2009) D Stefan et al.   MEASUREMENT SCIENCE and TECHNOLOGY

Hepatic anaplerotic outflow fluxes are redirected from gluconeogenesis to lactate synthesis in patients with Type 1a glycogen storage disease

(2009) John G. Jones et al.   METABOLIC ENGINEERING

Glucokinase and molecular aspects of liver glycogen metabolism

(2008) Loranne Agius   BIOCHEMICAL JOURNAL

Inhibition of mitochondrial fatty acid oxidation in vivo only slightly suppresses gluconeogenesis but enhances clearance of glucose in mice

(2008) Terry G. J. Derks et al.   HEPATOLOGY