Directly converted patient-specific induced neurons mirror the neuropathology of FUS with disrupted nuclear localization in amyotrophic lateral sclerosis
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Title
Directly converted patient-specific induced neurons mirror the neuropathology of FUS with disrupted nuclear localization in amyotrophic lateral sclerosis
Authors
Keywords
Amyotrophic lateral sclerosis, Fused in sarcoma, Human cell models, Induced neuron, Nuclear localization signal, Stress granules, Neuronal cytoplasmic inclusion
Journal
Molecular Neurodegeneration
Volume 11, Issue 1, Pages -
Publisher
Springer Nature
Online
2016-01-22
DOI
10.1186/s13024-016-0075-6
References
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