Impact of CFTR Modulators on Beta-Cell Function in Children and Young Adults with Cystic Fibrosis

Lumacaftor/ivacaftor in cystic fibrosis: effects on glucose metabolism and insulin secretion

(2021) C. Colombo et al.   JOURNAL OF ENDOCRINOLOGICAL INVESTIGATION

The effect of elexacaftor/tezacaftor/ivacaftor (ETI) on glycemia in adults with cystic fibrosis

(2021) Kevin J. Scully et al.   Journal of Cystic Fibrosis

Elexacaftor–Tezacaftor–Ivacaftor Therapy for Cystic Fibrosis Patients with The F508del/Unknown Genotype

(2021) Marika Comegna et al.   Antibiotics-Basel

Effect of one-year lumacaftor–ivacaftor treatment on glucose tolerance abnormalities in cystic fibrosis patients

(2020) Bastien Misgault et al.   Journal of Cystic Fibrosis

Lumacaftor/ivacaftor therapy fails to increase insulin secretion in F508del/F508del CF patients

(2020) Amir Moheet et al.   Journal of Cystic Fibrosis

Glucose tolerance stages in Cystic Fibrosis are idenfied by a unique pattern of defects of Beta-cell function

(2020) Claudia Piona et al.   JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM

A current review of the safety of cystic fibrosis transmembrane conductance regulator modulators

(2020) Elizabeth Marie Gavioli et al.   JOURNAL OF CLINICAL PHARMACY AND THERAPEUTICS

Heterogeneous expression of CFTR in insulin-secreting β-cells of the normal human islet

(2020) Mauricio Di Fulvio et al.   PLoS One

Central role of the β-cell in driving regression of diabetes after liver transplantation in cirrhotic patients

(2019) Valeria Grancini et al.   JOURNAL OF HEPATOLOGY

Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries

(2019) Nataliya Volkova et al.   Journal of Cystic Fibrosis

Hypothesis: Role of Reduced Hepatic Insulin Clearance in the Pathogenesis of Type 2 Diabetes

(2019) Richard N. Bergman et al.   DIABETES

Standardization of Spirometry 2019 Update. An Official American Thoracic Society and European Respiratory Society Technical Statement

(2019) Brian L. Graham et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Chloride transporters and channels in β-cell physiology: revisiting a 40-year-old model

(2019) Mauricio Di Fulvio et al.   BIOCHEMICAL SOCIETY TRANSACTIONS

In situ analysis reveals that CFTR is expressed in only a small minority of β-cells in normal adult human pancreas

(2019) Michael G White et al.   JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM

Effect of Lumacaftor/Ivacaftor on glucose metabolism and insulin secretion in Phe508del homozygous cystic fibrosis patients

(2018) Jan C. Thomassen et al.   Journal of Cystic Fibrosis

CFTR modulator theratyping: Current status, gaps and future directions

(2018) John Paul Clancy et al.   Journal of Cystic Fibrosis

Islet Hormone and Incretin Secretion in Cystic Fibrosis Following 4-months of Ivacaftor Therapy

(2018) Andrea Kelly et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

ISPAD Clinical Practice Consensus Guidelines 2018 Compendium Management of cystic fibrosis related diabetes in children and adolescents

(2018) Antoinette Moran et al.   PEDIATRIC DIABETES

CFTR silencing in pancreatic β-cells reveals a functional impact on glucose-stimulated insulin secretion and oxidative stress response

(2016) Thierry Ntimbane et al.   AMERICAN JOURNAL OF PHYSIOLOGY-ENDOCRINOLOGY AND METABOLISM

Abnormal Glucose Tolerance in Infants and Young Children with Cystic Fibrosis

(2016) Yaling Yi et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

CFTR and Anoctamin 1 (ANO1) contribute to cAMP amplified exocytosis and insulin secretion in human and murine pancreatic beta-cells

(2014) Anna Edlund et al.   BMC Medicine

Glucose-induced electrical activities and insulin secretion in pancreatic islet β-cells are modulated by CFTR

(2014) Jing Hui Guo et al.   Nature Communications

Glucose Derangements in Very Young Children With Cystic Fibrosis and Pancreatic Insufficiency

(2012) E. Mozzillo et al.   DIABETES CARE

Effects of Rosiglitazone, Glyburide, and Metformin on  -Cell Function and Insulin Sensitivity in ADOPT

(2011) S. E. Kahn et al.   DIABETES

Identification of insulin secretory defects and insulin resistance during oral glucose tolerance test in a cohort of cystic fibrosis patients

(2011) A Battezzati et al.   EUROPEAN JOURNAL OF ENDOCRINOLOGY

Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality

(2009) A. Moran et al.   DIABETES CARE

Shortcomings of current models of glucose-induced insulin secretion

(2009) J. C. Henquin et al.   DIABETES OBESITY & METABOLISM

Mechanisms of glucose intolerance in cystic fibrosis

(2009) K. Mohan et al.   DIABETIC MEDICINE