Human mitochondrial AAA+ ATPase SKD3/CLPB assembles into nucleotide-stabilized dodecamers
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Title
Human mitochondrial AAA+ ATPase SKD3/CLPB assembles into nucleotide-stabilized dodecamers
Authors
Keywords
Protein oligomerization, Mitochondrial intermembrane space, 3-Methylglutaconic aciduria, Congenital neutropenia, Analytical ultracentrifugation, Electron microscopy
Journal
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
Volume 602, Issue -, Pages 21-26
Publisher
Elsevier BV
Online
2022-02-25
DOI
10.1016/j.bbrc.2022.02.101
References
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- CLPB Mutations Cause 3-Methylglutaconic Aciduria, Progressive Brain Atrophy, Intellectual Disability, Congenital Neutropenia, Cataracts, Movement Disorder
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