Alisporivir Improves Mitochondrial Function in Skeletal Muscle of mdx Mice but Suppresses Mitochondrial Dynamics and Biogenesis

Treatment with a triazole inhibitor of the mitochondrial permeability transition pore fully corrects the pathology of sapje zebrafish lacking dystrophin

(2021) Anna Stocco et al.   PHARMACOLOGICAL RESEARCH

Skeletal muscle mitochondria in health and disease

(2021) Agnese De Mario et al.   CELL CALCIUM

Skeletal Muscle Mitochondria Dysfunction in Genetic Neuromuscular Disorders with Cardiac Phenotype

(2021) Elena Ignatieva et al.   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

Givinostat as metabolic enhancer reverting mitochondrial biogenesis deficit in Duchenne Muscular Dystrophy

(2021) Matteo Giovarelli et al.   PHARMACOLOGICAL RESEARCH

Effect of the MPT Pore Inhibitor Alisporivir on the Development of Mitochondrial Dysfunction in the Heart Tissue of Diabetic Mice

(2021) Natalia V. Belosludtseva et al.   Biology-Basel

A Review of Deflazacort for Patients With Duchenne Muscular Dystrophy

(2020) Mary Bylo et al.   ANNALS OF PHARMACOTHERAPY

Duchenne muscular dystrophy is associated with the inhibition of calcium uniport in mitochondria and an increased sensitivity of the organelles to the calcium-induced permeability transition

(2020) Mikhail V. Dubinin et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Assessment of Systemic Delivery of rAAVrh74.MHCK7.micro-dystrophin in Children With Duchenne Muscular Dystrophy

(2020) Jerry R. Mendell et al.   JAMA Neurology

Cyclophilin D: An Integrator of Mitochondrial Function

(2020) Georgios Amanakis et al.   Frontiers in Physiology

Physiopathology of the Permeability Transition Pore: Molecular Mechanisms in Human Pathology

(2020) Massimo Bonora et al.   Biomolecules

Transport of Ca2+ and Ca2+-dependent permeability transition in heart mitochondria in the early stages of Duchenne muscular dystrophy

(2020) Mikhail V. Dubinin et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Itaconic acid impairs the mitochondrial function by the inhibition of complexes II and IV and induction of the permeability transition pore opening in rat liver mitochondria

(2020) Konstantin N. Belosludtsev et al.   BIOCHIMIE

The Effect of S-15176 Difumarate Salt on Ultrastructure and Functions of Liver Mitochondria of C57BL/6 Mice with Streptozotocin/High-Fat Diet-Induced Type 2 Diabetes

(2020) Natalia V. Belosludtseva et al.   Biology-Basel

The Effect of Deflazacort Treatment on the Functioning of Skeletal Muscle Mitochondria in Duchenne Muscular Dystrophy

(2020) Mikhail V. Dubinin et al.   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

Early myopathy in Duchenne muscular dystrophy is associated with elevated mitochondrial H 2 O 2 emission during impaired oxidative phosphorylation

(2019) Meghan C. Hughes et al.   Journal of Cachexia Sarcopenia and Muscle

Mitochondrial Ca2+ Transport: Mechanisms, Molecular Structures, and Role in Cells

(2019) K. N. Belosludtsev et al.   BIOCHEMISTRY-MOSCOW

Cyclosporin A inhibits mitochondrial biogenesis in Hep G2 cells

(2018) Rui Qi et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

Alisporivir rescues defective mitochondrial respiration in Duchenne muscular dystrophy

(2017) Marco Schiavone et al.   PHARMACOLOGICAL RESEARCH

Mitochondria mediate cell membrane repair and contribute to Duchenne muscular dystrophy

(2016) Maria C Vila et al.   CELL DEATH AND DIFFERENTIATION

Metabolic Dysfunction and Altered Mitochondrial Dynamics in the Utrophin-Dystrophin Deficient Mouse Model of Duchenne Muscular Dystrophy

(2015) Meghna Pant et al.   PLoS One

Mitochondrial Reactive Oxygen Species (ROS) and ROS-Induced ROS Release

(2014) Dmitry B. Zorov et al.   PHYSIOLOGICAL REVIEWS

Defects in Mitochondrial ATP Synthesis in Dystrophin-Deficient Mdx Skeletal Muscles May Be Caused by Complex I Insufficiency

(2014) Emma Rybalka et al.   PLoS One

Mitochondrial calcium uptake

(2013) G. S. B. Williams et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Measuring Motor Coordination in Mice

(2013) Robert M.J. Deacon   Jove-Journal of Visualized Experiments

Primer-BLAST: A tool to design target-specific primers for polymerase chain reaction

(2012) Jian Ye et al.   BMC BIOINFORMATICS

Implications of glucocorticoid therapy in idiopathic inflammatory myopathies

(2012) Beatriz Y. Hanaoka et al.   Nature Reviews Rheumatology

Treatment of Duchenne muscular dystrophy with ciclosporin A: a randomised, double-blind, placebo-controlled multicentre trial

(2010) Janbernd Kirschner et al.   LANCET NEUROLOGY

Debio-025 is more effective than prednisone in reducing muscular pathology in mdx mice

(2010) Erin R. Wissing et al.   NEUROMUSCULAR DISORDERS

Systemic Myostatin Inhibition via Liver-Targeted Gene Transfer in Normal and Dystrophic Mice

(2010) Kevin J. Morine et al.   PLoS One

Mechanisms of Muscle Atrophy Induced by Glucocorticoids

(2009) O. Schakman et al.   HORMONE RESEARCH

Investigation of Debio 025, a cyclophilin inhibitor, in the dystrophic mdx mouse, a model for Duchenne muscular dystrophy

(2008) J Reutenauer et al.   BRITISH JOURNAL OF PHARMACOLOGY

Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy

(2008) Douglas P Millay et al.   NATURE MEDICINE

Analyzing real-time PCR data by the comparative CT method

(2008) Thomas D Schmittgen et al.   Nature Protocols