Cystic fibrosis-related diabetes: an update on pathophysiology, diagnosis, and treatment

The future of cystic fibrosis care: a global perspective

(2019) Scott C Bell et al.   Lancet Respiratory Medicine

Cystic fibrosis related diabetes: Medical management

(2019) Katie Larson Ode et al.   Journal of Cystic Fibrosis

Cystic fibrosis related diabetes: Pathophysiology, screening and diagnosis

(2019) Andrea Granados et al.   Journal of Cystic Fibrosis

Continuous glucose monitoring in cystic fibrosis – A practical guide

(2019) Christine L. Chan et al.   Journal of Cystic Fibrosis

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR

(2018) Scott H. Donaldson et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Ion Channel Modulators in Cystic Fibrosis

(2018) Martina Gentzsch et al.   CHEST

Hemoglobin A1cAccurately Predicts Continuous Glucose Monitoring–Derived Average Glucose in Youth and Young Adults With Cystic Fibrosis

(2018) Christine L. Chan et al.   DIABETES CARE

Cystic fibrosis-related education: Are we meeting patient and caregiver expectations?

(2018) Kevin P. Lonabaugh et al.   PATIENT EDUCATION AND COUNSELING

Pharmacological management of cystic fibrosis related diabetes

(2018) Amir Moheet et al.   Expert Review of Clinical Pharmacology

Repaglinide versus insulin for newly diagnosed diabetes in patients with cystic fibrosis: a multicentre, open-label, randomised trial

(2018) Manfred Ballmann et al.   Lancet Diabetes & Endocrinology

Cystic Fibrosis-Related Diabetes

(2018) Kayani Kayani et al.   Frontiers in Endocrinology

Islet Hormone and Incretin Secretion in Cystic Fibrosis Following 4-months of Ivacaftor Therapy

(2018) Andrea Kelly et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Exenatide corrects postprandial hyperglycaemia in youth with cystic fibrosis and impaired glucose tolerance: a crossover randomised trial

(2018) Myfanwy Clare Geyer et al.   DIABETES OBESITY & METABOLISM

Glucose intolerance in children with cystic fibrosis: a developing country’s perspective

(2018) Lakshmipathi Naik Banavath et al.   JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM

ISPAD Clinical Practice Consensus Guidelines 2018 Compendium Management of cystic fibrosis related diabetes in children and adolescents

(2018) Antoinette Moran et al.   PEDIATRIC DIABETES

Cystic Fibrosis: Emerging Understanding and Therapies

(2018) Michael M. Rey et al.   Annual Review of Medicine

12. Older Adults: Standards of Medical Care in Diabetes—2019

(2018)   DIABETES CARE

The Mechanistic Links between Insulin and Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Cl− Channel

(2017) Yoshinori Marunaka   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

Tezacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del

(2017) Jennifer L. Taylor-Cousar et al.   NEW ENGLAND JOURNAL OF MEDICINE

Structural abnormalities in islets from very young children with cystic fibrosis may contribute to cystic fibrosis-related diabetes

(2017) Marika Bogdani et al.   Scientific Reports

CFTR silencing in pancreatic β-cells reveals a functional impact on glucose-stimulated insulin secretion and oxidative stress response

(2016) Thierry Ntimbane et al.   AMERICAN JOURNAL OF PHYSIOLOGY-ENDOCRINOLOGY AND METABOLISM

Islet-intrinsic effects of CFTR mutation

(2016) Fiona N. Manderson Koivula et al.   DIABETOLOGIA

Glycated hemoglobin cannot yet be proposed as a screening tool for cystic fibrosis related diabetes

(2016) Valérie Boudreau et al.   Journal of Cystic Fibrosis

Advanced glycation end products are elevated in cystic fibrosis-related diabetes and correlate with worse lung function

(2016) William R. Hunt et al.   Journal of Cystic Fibrosis

Cystic fibrosis in Latin America—Improving the awareness

(2016) Luiz Vicente Ribeiro F. Silva Filho et al.   Journal of Cystic Fibrosis

Background and Epidemiology

(2016) Don B. Sanders et al.   PEDIATRIC CLINICS OF NORTH AMERICA

Diabetes-related Mortality in Adults with Cystic Fibrosis. Role of Genotype and Sex

(2015) Connor Lewis et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR

(2015) Claire E. Wainwright et al.   NEW ENGLAND JOURNAL OF MEDICINE

CFTR and Anoctamin 1 (ANO1) contribute to cAMP amplified exocytosis and insulin secretion in human and murine pancreatic beta-cells

(2014) Anna Edlund et al.   BMC Medicine

Why is insulin pump treatment rarely used in adolescents and young adults with cystic fibrosis-related diabetes?

(2014) Nicole Scheuing et al.   PEDIATRIC DIABETES

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial

(2014) Michael P Boyle et al.   Lancet Respiratory Medicine

Genetic Modifiers of Cystic Fibrosis-Related Diabetes

(2013) S. M. Blackman et al.   DIABETES

Exogenous insulin requirements do not differ between youth and adults with cystic fibrosis related diabetes

(2013) Muna Sunni et al.   PEDIATRIC DIABETES

Insulin secretion improves in cystic fibrosis following ivacaftor correction of CFTR: a small pilot study

(2013) Melena D Bellin et al.   PEDIATRIC DIABETES

Gastric Emptying, Incretin Hormone Secretion, and Postprandial Glycemia in Cystic Fibrosis—Effects of Pancreatic Enzyme Supplementation

(2011) Paul Kuo et al.   JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM

A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation

(2011) Bonnie W. Ramsey et al.   NEW ENGLAND JOURNAL OF MEDICINE

Epidemiology, Pathophysiology, and Prognostic Implications of Cystic Fibrosis-Related Diabetes: A technical review

(2010) A. Moran et al.   DIABETES CARE

Validation of Continuous Glucose Monitoring in Children and Adolescents With Cystic Fibrosis: A prospective cohort study

(2009) S. M.P. O'Riordan et al.   DIABETES CARE

Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality

(2009) A. Moran et al.   DIABETES CARE

Incidence of cystic fibrosis in five different states of Brazil as determined by screening of p.F508del, mutation at the CFTR gene in newborns and patients

(2007) Salmo Raskin et al.   Journal of Cystic Fibrosis