Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia
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Title
Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia
Authors
Keywords
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Journal
BMC Pediatrics
Volume 20, Issue 1, Pages -
Publisher
Springer Science and Business Media LLC
Online
2020-04-13
DOI
10.1186/s12887-020-02062-4
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Note: Only part of the references are listed.- International consensus guideline for reporting transmission electron microscopy results in the diagnosis of Primary Ciliary Dyskinesia (BEAT PCD TEM Criteria)
- (2020) Amelia Shoemark et al. EUROPEAN RESPIRATORY JOURNAL
- Clinical impact of Pseudomonas aeruginosa colonization in patients with Primary Ciliary Dyskinesia
- (2017) Malena Cohen-Cymberknoh et al. RESPIRATORY MEDICINE
- Bacterial infections in patients with primary ciliary dyskinesia: Comparison with cystic fibrosis
- (2017) Christiaan DM Wijers et al. Chronic Respiratory Disease
- Predicting high risk of exacerbations in bronchiectasis: the E-FACED score
- (2017) Miguel Angel Martinez-Garcia et al. International Journal of Chronic Obstructive Pulmonary Disease
- Review: Quality of Life in Children with Non-cystic Fibrosis Bronchiectasis
- (2017) Anna Marie Nathan et al. Frontiers in Pediatrics
- European Respiratory Society guidelines for the diagnosis of primary ciliary dyskinesia
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- A longitudinal study characterising a large adult primary ciliary dyskinesia population
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- Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia
- (2016) Meera Sunther et al. PEDIATRIC PULMONOLOGY
- Clinical characteristics, functional respiratory decline and follow-up in adult patients with primary ciliary dyskinesia
- (2016) Justine Frija-Masson et al. THORAX
- A longitudinal study of lung bacterial pathogens in patients with primary ciliary dyskinesia
- (2015) M.C. Alanin et al. CLINICAL MICROBIOLOGY AND INFECTION
- Changes in airway inflammation during pulmonary exacerbations in patients with cystic fibrosis and primary ciliary dyskinesia
- (2015) Felix Ratjen et al. EUROPEAN RESPIRATORY JOURNAL
- Accuracy of diagnostic testing in primary ciliary dyskinesia
- (2015) Claire L. Jackson et al. EUROPEAN RESPIRATORY JOURNAL
- Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review
- (2015) Adam J. Shapiro et al. PEDIATRIC PULMONOLOGY
- The Bronchiectasis Severity Index. An International Derivation and Validation Study
- (2014) James D. Chalmers et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Primary Ciliary Dyskinesia. Recent Advances in Diagnostics, Genetics, and Characterization of Clinical Disease
- (2013) Michael R. Knowles et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Multidimensional approach to non-cystic fibrosis bronchiectasis: the FACED score
- (2013) M. A. Martinez-Garcia et al. EUROPEAN RESPIRATORY JOURNAL
- Longitudinal lung function and structural changes in children with primary ciliary dyskinesia
- (2012) Marie Lémery Magnin et al. PEDIATRIC PULMONOLOGY
- Inner dynein arm defects causing primary ciliary dyskinesia: repeat testing required
- (2011) C. O'Callaghan et al. EUROPEAN RESPIRATORY JOURNAL
- The Changing Microbial Epidemiology in Cystic Fibrosis
- (2010) J. J. LiPuma CLINICAL MICROBIOLOGY REVIEWS
- A 20-year experience of electron microscopy in the diagnosis of primary ciliary dyskinesia
- (2009) J. F. Papon et al. EUROPEAN RESPIRATORY JOURNAL
- Structural and Functional Lung Disease in Primary Ciliary Dyskinesia
- (2008) Francesca Santamaria et al. CHEST
- Mutations in dynein genes in patients affected by isolated non-syndromic asthenozoospermia
- (2008) D. Zuccarello et al. HUMAN REPRODUCTION
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