Impaired autophagic and mitochondrial functions are partially restored by ERT in Gaucher and Fabry diseases
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Title
Impaired autophagic and mitochondrial functions are partially restored by ERT in Gaucher and Fabry diseases
Authors
Keywords
Mitochondria, Lysosomes, Autophagic cell death, Fibroblasts, Mitochondrial DNA, Fluorescence, Fabry disease, Gaucher's disease
Journal
PLoS One
Volume 14, Issue 1, Pages e0210617
Publisher
Public Library of Science (PLoS)
Online
2019-01-12
DOI
10.1371/journal.pone.0210617
References
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