Disulfide Bond Formation: Sulfhydryl Oxidase ALR Controls Mitochondrial Biogenesis of Human MIA40

The MIA pathway: A tight bond between protein transport and oxidative folding in mitochondria

(2012) Diana Stojanovski et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Mitochondria: In Sickness and in Health

(2012) Jodi Nunnari et al.   CELL

In vivo evidence for cooperation of Mia40 and Erv1 in the oxidation of mitochondrial proteins

(2012) Lena Böttinger et al.   MOLECULAR BIOLOGY OF THE CELL

Dual Role of Mitofilin in Mitochondrial Membrane Organization and Protein Biogenesis

(2011) Karina von der Malsburg et al.   DEVELOPMENTAL CELL

Yeast: An Experimental Organism for 21st Century Biology

(2011) David Botstein et al.   GENETICS

Mimicking a SURF1 allele reveals uncoupling of cytochrome c oxidase assembly from translational regulation in yeast

(2011) Robert Reinhold et al.   HUMAN MOLECULAR GENETICS

Molecular recognition and substrate mimicry drive the electron-transfer process between MIA40 and ALR

(2011) L. Banci et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Mitochondrial protein import: from transport pathways to an integrated network

(2011) Thomas Becker et al.   TRENDS IN BIOCHEMICAL SCIENCES

Oxidative Protein Folding in the Mitochondrial Intermembrane Space

(2010) Dionisia P. Sideris et al.   ANTIOXIDANTS & REDOX SIGNALING

Structure of the Human Sulfhydryl Oxidase Augmenter of Liver Regeneration and Characterization of a Human Mutation Causing an Autosomal Recessive Myopathy,

(2010) Vidyadhar N. Daithankar et al.   BIOCHEMISTRY

Mitochondrial Disulfide Bond Formation Is Driven by Intersubunit Electron Transfer in Erv1 and Proofread by Glutathione

(2010) Melanie Bien et al.   MOLECULAR CELL

Molecular chaperone function of Mia40 triggers consecutive induced folding steps of the substrate in mitochondrial protein import

(2010) L. Banci et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

The Mitochondrial Disulfide Relay System Protein GFER Is Mutated in Autosomal-Recessive Myopathy with Cataract and Combined Respiratory-Chain Deficiency

(2009) Alessio Di Fonzo et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Augmenter of Liver Regeneration: Substrate Specificity of a Flavin-Dependent Oxidoreductase from the Mitochondrial Intermembrane Space

(2009) Vidyadhar N. Daithankar et al.   BIOCHEMISTRY

Importing Mitochondrial Proteins: Machineries and Mechanisms

(2009) Agnieszka Chacinska et al.   CELL

Introducing the human Leigh syndrome mutation T9176G into Saccharomyces cerevisiae mitochondrial DNA leads to severe defects in the incorporation of Atp6p into the ATP synthase and in the mitochondrial morphology

(2009) R. Kucharczyk et al.   HUMAN MOLECULAR GENETICS

Disulphide Bond Formation in the Intermembrane Space of Mitochondria

(2009) M. Deponte et al.   JOURNAL OF BIOCHEMISTRY

Deciphering Structural and Functional Roles of Individual Disulfide Bonds of the Mitochondrial Sulfhydryl Oxidase Erv1p

(2009) Swee Kim Ang et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

A novel intermembrane space–targeting signal docks cysteines onto Mia40 during mitochondrial oxidative folding

(2009) Dionisia P. Sideris et al.   JOURNAL OF CELL BIOLOGY

Systematic Analysis of the Twin Cx9C Protein Family

(2009) Sebastian Longen et al.   JOURNAL OF MOLECULAR BIOLOGY

Distinct Forms of Mitochondrial TOM-TIM Supercomplexes Define Signal-Dependent States of Preprotein Sorting

(2009) A. Chacinska et al.   MOLECULAR AND CELLULAR BIOLOGY

Reconstitution of the Mia40-Erv1 Oxidative Folding Pathway for the Small Tim Proteins

(2009) Heather L. Tienson et al.   MOLECULAR BIOLOGY OF THE CELL

Identification of the Signal Directing Tim9 and Tim10 into the Intermembrane Space of Mitochondria

(2009) Dusanka Milenkovic et al.   MOLECULAR BIOLOGY OF THE CELL

MIA40 is an oxidoreductase that catalyzes oxidative protein folding in mitochondria

(2009) Lucia Banci et al.   NATURE STRUCTURAL & MOLECULAR BIOLOGY

Structural basis of yeast Tim40/Mia40 as an oxidative translocator in the mitochondrial intermembrane space

(2009) S. Kawano et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Disulfide Formation in the ER and Mitochondria: Two Solutions to a Common Process

(2009) J. Riemer et al.   SCIENCE

Redox regulation of protein folding in the mitochondrial intermembrane space

(2008) Carla M. Koehler et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Different regulation of wild-type and mutant Cu,Zn superoxide dismutase localization in mammalian mitochondria

(2008) Hibiki Kawamata et al.   HUMAN MOLECULAR GENETICS

Structural and Functional Roles of the Conserved Cysteine Residues of the Redox-regulated Import Receptor Mia40 in the Intermembrane Space of Mitochondria

(2008) Nadia Terziyska et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mitochondrial Biogenesis, Switching the Sorting Pathway of the Intermembrane Space Receptor Mia40

(2008) Agnieszka Chacinska et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mitochondrial protein import: precursor oxidation in a ternary complex with disulfide carrier and sulfhydryl oxidase

(2008) Diana Stojanovski et al.   JOURNAL OF CELL BIOLOGY

The Erv family of sulfhydryl oxidases

(2007) Deborah Fass   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Precursor Oxidation by Mia40 and Erv1 Promotes Vectorial Transport of Proteins into the Mitochondrial Intermembrane Space

(2007) Judith M. Müller et al.   MOLECULAR BIOLOGY OF THE CELL