The Mitochondrial Complex I Activity Is Reduced in Cells with Impaired Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Function

Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry

(2011) Ángel G. Valdivieso et al.   ANALYTICAL BIOCHEMISTRY

Microplate-based kinetic method for assay of mitochondrial NADH– and succinate–cytochrome c reductase activities

(2011) Apurva Kumar R. Joshi et al.   ANALYTICAL BIOCHEMISTRY

The Cystic Fibrosis Neutrophil: A Specialized Yet Potentially Defective Cell

(2011) Elaine Hayes et al.   ARCHIVUM IMMUNOLOGIAE ET THERAPIAE EXPERIMENTALIS

Mitochondria in innate immunity

(2011) Damien Arnoult et al.   EMBO REPORTS

GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models

(2011) M. Kelly-Aubert et al.   HUMAN MOLECULAR GENETICS

Novel ligands that target the mitochondrial membrane protein mitoNEET

(2011) Robert M. Bieganski et al.   JOURNAL OF MOLECULAR GRAPHICS & MODELLING

Interdomain communication revealed in the diabetes drug target mitoNEET

(2011) E. L. Baxter et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Role of calpain in the regulation of CFTR (cystic fibrosis transmembrane conductance regulator) turnover

(2010) Monica Averna et al.   BIOCHEMICAL JOURNAL

Binding of Reduced Nicotinamide Adenine Dinucleotide Phosphate Destabilizes the Iron−Sulfur Clusters of Human MitoNEET

(2010) Tao Zhou et al.   BIOCHEMISTRY

Calpain digestion and HSP90-based chaperone protection modulate the level of plasma membrane F508del-CFTR

(2010) Monica Averna et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Peroxisome proliferator-activated receptor gamma agonists as neuroprotective agents

(2010) R.K. Kaundal et al.   DRUG NEWS & PERSPECTIVES

Mitochondrial complex I in the network of known and unknown facts

(2010) M. Chomova et al.   GENERAL PHYSIOLOGY AND BIOPHYSICS

Effects of rotenone and pyridaben on complex I electron transfer and on mitochondrial nitric oxide synthase functional activity

(2010) Ana Navarro et al.   JOURNAL OF BIOENERGETICS AND BIOMEMBRANES

Cystic Fibrosis Transmembrane Regulator Inhibitors CFTRinh-172 and GlyH-101 Target Mitochondrial Functions, Independently of Chloride Channel Inhibition

(2010) M. Kelly et al.   JOURNAL OF PHARMACOLOGY AND EXPERIMENTAL THERAPEUTICS

Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition

(2010) Alessandro Luciani et al.   NATURE CELL BIOLOGY

The novel 2Fe–2S outer mitochondrial protein mitoNEET displays conformational flexibility in its N-terminal cytoplasmic tethering domain

(2009) Andrea R. Conlan et al.   Acta Crystallographica Section F-Structural Biology and Crystallization Communications

Redox Characterization of the FeS Protein MitoNEET and Impact of Thiazolidinedione Drug Binding

(2009) Daniel W. Bak et al.   BIOCHEMISTRY

Dysfunction of mitochondria Ca2+ uptake in cystic fibrosis airway epithelial cells

(2009) Fabrice Antigny et al.   MITOCHONDRION

Skeletal muscle weakness, exercise tolerance and physical activity in adults with cystic fibrosis

(2008) T. Troosters et al.   EUROPEAN RESPIRATORY JOURNAL

CISD1 codifies a mitochondrial protein upregulated by the CFTR channel

(2007) Guillermo L. Taminelli et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

Chloride transporting capability of Calu-3 epithelia following persistent knockdown of the cystic fibrosis transmembrane conductance regulator, CFTR

(2007) L J MacVinish et al.   BRITISH JOURNAL OF PHARMACOLOGY