Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease
Published 2013 View Full Article
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Title
Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease
Authors
Keywords
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Journal
JOURNAL OF INHERITED METABOLIC DISEASE
Volume 37, Issue 3, Pages 369-381
Publisher
Springer Nature
Online
2013-11-28
DOI
10.1007/s10545-013-9663-6
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Note: Only part of the references are listed.- Canavan disease, a rare early-onset human spongiform leukodystrophy: Insights into its genesis and possible clinical interventions
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- Glyceryl triacetate for Canavan disease: A low-dose trial in infants and evaluation of a higher dose for toxicity in the tremor rat model
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- Myelin Lipid Abnormalities in the Aspartoacylase-Deficient Tremor Rat
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