Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease
出版年份 2013 全文链接
标题
Dietary triheptanoin rescues oligodendrocyte loss, dysmyelination and motor function in the nur7 mouse model of Canavan disease
作者
关键词
-
出版物
JOURNAL OF INHERITED METABOLIC DISEASE
Volume 37, Issue 3, Pages 369-381
出版商
Springer Nature
发表日期
2013-11-28
DOI
10.1007/s10545-013-9663-6
参考文献
相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。- Canavan disease, a rare early-onset human spongiform leukodystrophy: Insights into its genesis and possible clinical interventions
- (2012) M.H. Baslow et al. BIOCHIMIE
- Lithium Citrate as Treatment of Canavan Disease
- (2012) María Dolores Edo Solsona et al. CLINICAL NEUROPHARMACOLOGY
- Triheptanoin in acute mouse seizure models
- (2012) Nicola K. Thomas et al. EPILEPSY RESEARCH
- Aspartoacylase Supports Oxidative Energy Metabolism during Myelination
- (2012) Jeremy S Francis et al. JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM
- Heptanoate as a Neural Fuel: Energetic and Neurotransmitter Precursors in Normal and Glucose Transporter I-Deficient (G1D) Brain
- (2012) Isaac Marin-Valencia et al. JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM
- Oligodendroglia metabolically support axons and contribute to neurodegeneration
- (2012) Youngjin Lee et al. NATURE
- A call for transparent reporting to optimize the predictive value of preclinical research
- (2012) Story C. Landis et al. NATURE
- Therapy of Pelizaeus-Merzbacher disease in mice by feeding a cholesterol-enriched diet
- (2012) Gesine Saher et al. NATURE MEDICINE
- Long-Term Follow-Up After Gene Therapy for Canavan Disease
- (2012) P. Leone et al. Science Translational Medicine
- Astrocyte-Neuron Lactate Transport Is Required for Long-Term Memory Formation
- (2011) Akinobu Suzuki et al. CELL
- A safety trial of high dose glyceryl triacetate for Canavan disease
- (2011) Reeval Segel et al. MOLECULAR GENETICS AND METABOLISM
- Lithium citrate reduces excessive intra-cerebral N-acetyl aspartate in Canavan disease
- (2010) Mitra Assadi et al. EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY
- Metabolic acetate therapy improves phenotype in the tremor rat model of Canavan disease
- (2010) Peethambaran Arun et al. JOURNAL OF INHERITED METABOLIC DISEASE
- Pyruvate carboxylase deficiency: Mechanisms, mimics and anaplerosis
- (2010) Isaac Marin-Valencia et al. MOLECULAR GENETICS AND METABOLISM
- Anticonvulsant effects of a triheptanoin diet in two mouse chronic seizure models
- (2010) Sarah Willis et al. NEUROBIOLOGY OF DISEASE
- Glyceryl triacetate for Canavan disease: A low-dose trial in infants and evaluation of a higher dose for toxicity in the tremor rat model
- (2009) C. N. Madhavarao et al. JOURNAL OF INHERITED METABOLIC DISEASE
- Nur7 Is a Nonsense Mutation in the Mouse Aspartoacylase Gene That Causes Spongy Degeneration of the CNS
- (2008) M. Traka et al. JOURNAL OF NEUROSCIENCE
- Myelin Lipid Abnormalities in the Aspartoacylase-Deficient Tremor Rat
- (2008) Jianfeng Wang et al. NEUROCHEMICAL RESEARCH
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