The Dystrophin-Glycoprotein Complex in the Prevention of Muscle Damage

Transgenic Expression of Laminin α1 Chain Does Not Prevent Muscle Disease in the mdx Mouse Model for Duchenne Muscular Dystrophy

(2011) Kinga I. Gawlik et al.   AMERICAN JOURNAL OF PATHOLOGY

Activation of AKT signaling promotes cell growth and survival in α7β1 integrin-mediated alleviation of muscular dystrophy

(2011) Marni D. Boppart et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Muscle-specific expression of insulin-like growth factor 1 improves outcome in Lama2Dy-w mice, a model for congenital muscular dystrophy type 1A

(2011) A. Kumar et al.   HUMAN MOLECULAR GENETICS

Lateral transmission of force is impaired in skeletal muscles of dystrophic mice and very old rats

(2011) Krishnan S. Ramaswamy et al.   JOURNAL OF PHYSIOLOGY-LONDON

A Dystroglycan Mutation Associated with Limb-Girdle Muscular Dystrophy

(2011) Yuji Hara et al.   NEW ENGLAND JOURNAL OF MEDICINE

Soleus muscle in glycosylation-deficient muscular dystrophy is protected from contraction-induced injury

(2010) Jessica D. Gumerson et al.   AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

Leupeptin-based inhibitors do not improve the mdx phenotype

(2010) Joshua Selsby et al.   AMERICAN JOURNAL OF PHYSIOLOGY-REGULATORY INTEGRATIVE AND COMPARATIVE PHYSIOLOGY

Intracellular Ca2+ Signaling in Skeletal Muscle

(2010) Eva R. Chin   EXERCISE AND SPORT SCIENCES REVIEWS

Proteasome inhibition improves the muscle of laminin α2 chain-deficient mice

(2010) Virginie Carmignac et al.   HUMAN MOLECULAR GENETICS

Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy

(2010) Sara Menazza et al.   HUMAN MOLECULAR GENETICS

Duchenne muscular dystrophy – What causes the increased membrane permeability in skeletal muscle?

(2010) David G. Allen et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

Transgenic overexpression of laminin α1 chain in laminin α2 chain-deficient mice rescues the disease throughout the lifespan

(2010) Kinga I. Gawlik et al.   MUSCLE & NERVE

Distinct Roles for Laminin Globular Domains in Laminin α1 Chain Mediated Rescue of Murine Laminin α2 Chain Deficiency

(2010) Kinga I. Gawlik et al.   PLoS One

Sildenafil reverses cardiac dysfunction in the mdx mouse model of Duchenne muscular dystrophy

(2010) C. M. Adamo et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Malformed mdx myofibers have normal cytoskeletal architecture yet altered EC coupling and stress-induced Ca2+ signaling

(2009) Richard M. Lovering et al.   AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

Extensive mononuclear infiltration and myogenesis characterize recovery of dysferlin-null skeletal muscle from contraction-induced injuries

(2009) Joseph A. Roche et al.   AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

Green tea extract decreases muscle pathology and NF-κB immunostaining in regenerating muscle fibers of mdx mice

(2009) Nicholas P. Evans et al.   CLINICAL NUTRITION

‘Congenital muscular dystrophy caused by integrin α7 deficiency’

(2009) Hideyuki Nakashima et al.   DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY

Dystrophin glycoprotein complex-associated Gβγ subunits activate phosphatidylinositol-3-kinase/Akt signaling in skeletal muscle in a laminin-dependent manner

(2009) Yongmin Xiong et al.   JOURNAL OF CELLULAR PHYSIOLOGY

Omigapil Ameliorates the Pathology of Muscle Dystrophy Caused by Laminin- 2 Deficiency

(2009) M. Erb et al.   JOURNAL OF PHARMACOLOGY AND EXPERIMENTAL THERAPEUTICS

Hypernitrosylated ryanodine receptor calcium release channels are leaky in dystrophic muscle

(2009) Andrew M Bellinger et al.   NATURE MEDICINE

Reciprocal amplification of ROS and Ca2+ signals in stressed mdx dystrophic skeletal muscle fibers

(2009) Vyacheslav M. Shkryl et al.   PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY

Basal lamina strengthens cell membrane integrity via the laminin G domain-binding motif of  -dystroglycan

(2009) R. Han et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Calcium influx is sufficient to induce muscular dystrophy through a TRPC-dependent mechanism

(2009) Douglas P. Millay et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Laminin-111 protein therapy prevents muscle disease in the mdx mouse model for Duchenne muscular dystrophy

(2009) J. E. Rooney et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Pathology is alleviated by doxycycline in a laminin-α2-null model of congenital muscular dystrophy

(2008) Mahasweta Girgenrath et al.   ANNALS OF NEUROLOGY

Mechanisms of Muscle Degeneration, Regeneration, and Repair in the Muscular Dystrophies

(2008) Gregory Q. Wallace et al.   Annual Review of Physiology

Effect of calpain and proteasome inhibition on Ca2+-dependent proteolysis and muscle histopathology in the mdx mouse

(2008) Alexandre Briguet et al.   FASEB JOURNAL

Akt activation prevents the force drop induced by eccentric contractions in dystrophin-deficient skeletal muscle

(2008) Bert Blaauw et al.   HUMAN MOLECULAR GENETICS

Dominant-negative inhibition of Ca2+ influx via TRPV2 ameliorates muscular dystrophy in animal models

(2008) Yuko Iwata et al.   HUMAN MOLECULAR GENETICS

Role of the calcium-calpain pathway in cytoskeletal damage after eccentric contractions

(2008) Bao-Ting Zhang et al.   JOURNAL OF APPLIED PHYSIOLOGY

TRPC1 binds to caveolin-3 and is regulated by Src kinase - role in Duchenne muscular dystrophy

(2008) O. L. Gervasio et al.   JOURNAL OF CELL SCIENCE

N-Acetylcysteine ameliorates skeletal muscle pathophysiology inmdxmice

(2008) Nicholas P. Whitehead et al.   JOURNAL OF PHYSIOLOGY-LONDON

Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy

(2008) Douglas P Millay et al.   NATURE MEDICINE

Impaired recovery of dysferlin-null skeletal muscle after contraction-induced injury in vivo

(2008) Joseph A. Roche et al.   NEUROREPORT

Muscular dystrophies due to glycosylation defects

(2008) Francesco Muntoni et al.   Neurotherapeutics