Why are some amyloidoses systemic? Does hepatic “chaperoning at a distance” prevent cardiac deposition in a transgenic model of human senile systemic (transthyretin) amyloidosis?

Regulation of PGC-1α, a nodal regulator of mitochondrial biogenesis

(2011) Pablo J Fernandez-Marcos et al.   AMERICAN JOURNAL OF CLINICAL NUTRITION

Amyloid fibril protein nomenclature: 2010 recommendations from the nomenclature committee of the International Society of Amyloidosis

(2010) Jean D. Sipe et al.   AMYLOID-JOURNAL OF PROTEIN FOLDING DISORDERS

Risk of transmission of systemic transthyretin amyloidosis after domino liver transplantation

(2010) Laura Lladó et al.   LIVER TRANSPLANTATION

The Nrf2 System as a Potential Target for the Development of Indirect Antioxidants

(2010) Kyeong-Ah Jung et al.   MOLECULES

Biological and Chemical Approaches to Diseases of Proteostasis Deficiency

(2009) Evan T. Powers et al.   Annual Review of Biochemistry

Regulation of Hypoxia-Inducible Genes by PGC-1α

(2009) Jonathan Shoag et al.   ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY

pXBP1(U), a Negative Regulator of the Unfolded Protein Response Activator pXBP1(S), Targets ATF6 but not ATF4 in Proteasome-mediated Degradation

(2009) Hiderou Yoshida et al.   CELL STRUCTURE AND FUNCTION

Regulated Ire1-dependent decay of messenger RNAs in mammalian cells

(2009) Julie Hollien et al.   JOURNAL OF CELL BIOLOGY

Activation of the Heat Shock Response in Familial Amyloidotic Polyneuropathy

(2009) Sofia Duque Santos et al.   JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY

The PPAR trio: Regulators of myocardial energy metabolism in health and disease

(2008) Jose A. Madrazo et al.   JOURNAL OF MOLECULAR AND CELLULAR CARDIOLOGY

The heat shock response modulates transthyretin deposition in the peripheral and autonomic nervous systems

(2008) Sofia Duque Santos et al.   NEUROBIOLOGY OF AGING

Adapting Proteostasis for Disease Intervention

(2008) William E. Balch et al.   SCIENCE