Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease

Activation of Trpv4 Reduces the Hyperproliferative Phenotype of Cystic Cholangiocytes From an Animal Model of ARPKD

(2010) Sergio A. Gradilone et al.   GASTROENTEROLOGY

Curcumin improves sclerosing cholangitis in Mdr2-/- mice by inhibition of cholangiocyte inflammatory response and portal myofibroblast proliferation

(2010) A. Baghdasaryan et al.   GUT

Renin-angiotensin System Activation in Congenital Hepatic Fibrosis in the PCK Rat Model of Autosomal Recessive Polycystic Kidney Disease

(2010) Miwa Goto et al.   JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION

Rapamycin Ameliorates PKD Resulting from Conditional Inactivation of Pkd1

(2010) J. M. Shillingford et al.   JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY

Sirolimus attenuates disease progression in an orthologous mouse model of human autosomal dominant polycystic kidney disease

(2010) Iram Zafar et al.   KIDNEY INTERNATIONAL

Evolving challenges in hepatic fibrosis

(2010) Scott L. Friedman   Nature Reviews Gastroenterology & Hepatology

Inhibition of mTOR with sirolimus does not attenuate progression of liver and kidney disease in PCK rats

(2010) C. Renken et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Sirolimus and Kidney Growth in Autosomal Dominant Polycystic Kidney Disease

(2010) Andreas L. Serra et al.   NEW ENGLAND JOURNAL OF MEDICINE

Everolimus in Patients with Autosomal Dominant Polycystic Kidney Disease

(2010) Gerd Walz et al.   NEW ENGLAND JOURNAL OF MEDICINE

The renin-angiotensin system and hypertension in autosomal recessive polycystic kidney disease

(2010) Miwa Goto et al.   PEDIATRIC NEPHROLOGY

Chronic treatment with lisinopril decreases proliferative and apoptotic pathways in autosomal recessive polycystic kidney disease

(2010) Guangfu Jia et al.   PEDIATRIC NEPHROLOGY

Impact of Mammalian Target of Rapamycin Inhibition on Autosomal-Dominant Polycystic Kidney Disease

(2010) R.P. Wüthrich et al.   TRANSPLANTATION PROCEEDINGS

Mammalian target of rapamycin regulates vascular endothelial growth factor-dependent liver cyst growth in polycystin-2-defective mice

(2009) Carlo Spirli et al.   HEPATOLOGY

Portal fibroblasts: Underappreciated mediators of biliary fibrosis

(2009) Jonathan A. Dranoff et al.   HEPATOLOGY

PKHD1 sequence variations in 78 children and adults with autosomal recessive polycystic kidney disease and congenital hepatic fibrosis

(2009) Meral Gunay-Aygun et al.   MOLECULAR GENETICS AND METABOLISM

Activation of the AKT/mTOR pathway in autosomal recessive polycystic kidney disease (ARPKD)

(2009) D.-C. Fischer et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Primary Cilia and Signaling Pathways in Mammalian Development, Health and Disease

(2009) Iben R. Veland et al.   NEPHRON PHYSIOLOGY

Biliary and Pancreatic Dysgenesis in Mice Harboring a Mutation in Pkhd1

(2008) Anna-Rachel Gallagher et al.   AMERICAN JOURNAL OF PATHOLOGY

Polycystic Kidney Disease

(2008) Peter C. Harris et al.   Annual Review of Medicine

PPARs and the Cardiovascular System

(2008) Milton Hamblin et al.   ANTIOXIDANTS & REDOX SIGNALING

Cytokines and Renin-Angiotensin System Signaling in Hepatic Fibrosis

(2008) Montserrat Moreno et al.   Clinics in Liver Disease

Ciliary dysfunction in polycystic kidney disease: an emerging model with polarizing potential

(2008) Robert et al.   Frontiers in Bioscience-Landmark

The cAMP effectors Epac and protein kinase a (PKA) are involved in the hepatic cystogenesis of an animal model of autosomal recessive polycystic kidney disease (ARPKD)

(2008) Jesús M. Banales et al.   HEPATOLOGY

Role of peroxisome proliferator-activated receptor-gamma (PPARγ) during liver regeneration in rats

(2008) Yoshio Yamamoto et al.   JOURNAL OF GASTROENTEROLOGY AND HEPATOLOGY

Sirolimus Reduces Polycystic Liver Volume in ADPKD Patients

(2008) Q. Qian et al.   JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY

PPAR-γ agonist attenuates renal interstitial fibrosis and inflammation through reduction of TGF-β

(2008) Toru Kawai et al.   LABORATORY INVESTIGATION

Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)

(2008) Baris Turkbey et al.   PEDIATRIC RADIOLOGY