Overexpression of Mutant Ataxin-3 in Mouse Cerebellum Induces Ataxia and Cerebellar Neuropathology

Pathoanatomy of Cerebellar Degeneration in Spinocerebellar Ataxia Type 2 (SCA2) and Type 3 (SCA3)

(2011) W. Scherzed et al.   CEREBELLUM

High Transgene Expression by Lentiviral Vectors Causes Maldevelopment of Purkinje Cells In Vivo

(2010) Yusuke Sawada et al.   CEREBELLUM

Motor uncoordination and neuropathology in a transgenic mouse model of Machado–Joseph disease lacking intranuclear inclusions and ataxin-3 cleavage products

(2010) Anabela Silva-Fernandes et al.   NEUROBIOLOGY OF DISEASE

Reversibility of symptoms in a conditional mouse model of spinocerebellar ataxia type 3

(2009) Jana Boy et al.   HUMAN MOLECULAR GENETICS

A transgenic mouse model of spinocerebellar ataxia type 3 resembling late disease onset and gender-specific instability of CAG repeats

(2009) Jana Boy et al.   NEUROBIOLOGY OF DISEASE

Characterization of mutant mice that express polyglutamine in cerebellar Purkinje cells

(2008) Miho Oue et al.   BRAIN RESEARCH

Progress in transduction of cerebellar Purkinje cells in vivo using viral vectors

(2008) Hirokazu Hirai   CEREBELLUM

Molecular Genetics and Biomarkers of Polyglutamine Diseases

(2008) Masahisa Katsuno et al.   CURRENT MOLECULAR MEDICINE

Lentivector-mediated rescue from cerebellar ataxia in a mouse model of spinocerebellar ataxia

(2008) Takashi Torashima et al.   EMBO REPORTS

Striatal and nigral pathology in a lentiviral rat model of Machado-Joseph disease

(2008) Sandro Alves et al.   HUMAN MOLECULAR GENETICS

Polyglutamine-expanded ataxin-3 causes cerebellar dysfunction of SCA3 transgenic mice by inducing transcriptional dysregulation

(2008) An-Hsun Chou et al.   NEUROBIOLOGY OF DISEASE

Purkinje-cell-preferential transduction by lentiviral vectors with the murine stem cell virus promoter

(2008) Kiyohiko Takayama et al.   NEUROSCIENCE LETTERS

Allele-Specific RNA Silencing of Mutant Ataxin-3 Mediates Neuroprotection in a Rat Model of Machado-Joseph Disease

(2008) Sandro Alves et al.   PLoS One