Structural basis for the protective effect of the human prion protein carrying the dominant-negative E219K polymorphism

Toward the Molecular Basis of Inherited Prion Diseases: NMR Structure of the Human Prion Protein with V210I Mutation

(2011) Ivana Biljan et al.   JOURNAL OF MOLECULAR BIOLOGY

Common Structural Traits across Pathogenic Mutants of the Human Prion Protein and Their Implications for Familial Prion Diseases

(2011) Giulia Rossetti et al.   JOURNAL OF MOLECULAR BIOLOGY

Dynamic Diagnosis of Familial Prion Diseases Supports the β2-α2 Loop as a Universal Interference Target

(2011) Massimiliano Meli et al.   PLoS One

Prospective 10-year surveillance of human prion diseases in Japan

(2010) I. Nozaki et al.   BRAIN

The genetics of prion diseases

(2010) James A Mastrianni   GENETICS IN MEDICINE

Unique Structural Characteristics of the Rabbit Prion Protein

(2010) Yi Wen et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

A molecular switch controls interspecies prion disease transmission in mice

(2010) Christina J. Sigurdson et al.   JOURNAL OF CLINICAL INVESTIGATION

Horse Prion Protein NMR Structure and Comparisons with Related Variants of the Mouse Prion Protein

(2010) Daniel R. Pérez et al.   JOURNAL OF MOLECULAR BIOLOGY

NMR Structure of the Human Prion Protein with the Pathological Q212P Mutation Reveals Unique Structural Features

(2010) Gregor Ilc et al.   PLoS One

Conformational diversity in prion protein variants influences intermolecular β-sheet formation

(2009) Seungjoo Lee et al.   EMBO JOURNAL

Prediction of Xaa-Pro peptide bond conformation from sequence and chemical shifts

(2009) Yang Shen et al.   JOURNAL OF BIOMOLECULAR NMR

Spontaneous Generation of Prion Infectivity in Fatal Familial Insomnia Knockin Mice

(2009) Walker S. Jackson et al.   NEURON

Trans-Dominant Inhibition of Prion Propagation In Vitro Is Not Mediated by an Accessory Cofactor

(2009) James C. Geoghegan et al.   PLoS Pathogens

Identification of an Intracellular Site of Prion Conversion

(2009) Zrinka Marijanovic et al.   PLoS Pathogens

Molecular Mechanisms of Prion Pathogenesis

(2008) Adriano Aguzzi et al.   Annual Review of Pathology-Mechanisms of Disease

Human Prion Protein (PrP) 219K Is Converted to PrPScbut Shows Heterozygous Inhibition in Variant Creutzfeldt-Jakob Disease Infection

(2008) Masaki Hizume et al.   JOURNAL OF BIOLOGICAL CHEMISTRY