Variation in lung function is associated with worse clinical outcomes in cystic fibrosis

Children and young adults with CF in the USA have better lung function compared with the UK

(2014) C. H. Goss et al.   THORAX

Multi-ethnic reference values for spirometry for the 3–95-yr age range: the global lung function 2012 equations

(2012) Philip H. Quanjer et al.   EUROPEAN RESPIRATORY JOURNAL

Risk factors for rate of decline in FEV1 in adults with cystic fibrosis

(2012) Michael W. Konstan et al.   Journal of Cystic Fibrosis

Understanding the natural progression in %FEV1decline in patients with cystic fibrosis: a longitudinal study

(2012) David Taylor-Robinson et al.   THORAX

Shwachman-Kulczycki score still useful to monitor cystic fibrosis severity

(2011) Fabíola Stollar et al.   Clinics

Effect of pulmonary exacerbations on long-term lung function decline in cystic fibrosis

(2011) Valerie Waters et al.   EUROPEAN RESPIRATORY JOURNAL

Six minute walk test Z score: Correlations with cystic fibrosis severity markers

(2011) Fabíola Stollar et al.   Journal of Cystic Fibrosis

Exacerbation frequency and clinical outcomes in adult patients with cystic fibrosis

(2011) K. de Boer et al.   THORAX

Design and powering of cystic fibrosis clinical trials using rate of FEV1 decline as an efficacy endpoint

(2010) M.W. Konstan et al.   Journal of Cystic Fibrosis

Year-to-year changes in lung function in individuals with cystic fibrosis

(2010) Theodore G. Liou et al.   Journal of Cystic Fibrosis

Pulmonary exacerbations are associated with subsequent FEV1 decline in both adults and children with cystic fibrosis

(2010) Don B. Sanders et al.   PEDIATRIC PULMONOLOGY

The six-minute walk test and body weight-walk distance product in healthy Brazilian subjects

(2009) A.M. Iwama et al.   BRAZILIAN JOURNAL OF MEDICAL AND BIOLOGICAL RESEARCH

Reference values for the 6-min walk test in healthy children aged 6–12 years

(2009) Camila Varella Priesnitz et al.   PEDIATRIC PULMONOLOGY

Clinical Changes of Patients with Cystic Fibrosis during Transition from Pediatric to Adult Care

(2008) Ingrid Duguépéroux et al.   JOURNAL OF ADOLESCENT HEALTH

Reproducibility of spirometry during cystic fibrosis pulmonary exacerbations

(2008) Don B. Sanders et al.   PEDIATRIC PULMONOLOGY

Lung function in 3-5-year-old children with cystic fibrosis

(2008) Oscar H. Mayer et al.   PEDIATRIC PULMONOLOGY

Recurrent exacerbations affect FEV1 decline in adult patients with cystic fibrosis

(2008) Anna Amadori et al.   RESPIRATORY MEDICINE