Pathological mitochondrial copper overload in livers of Wilson's disease patients and related animal models
Published 2014 View Full Article
- Home
- Publications
- Publication Search
- Publication Details
Title
Pathological mitochondrial copper overload in livers of Wilson's disease patients and related animal models
Authors
Keywords
-
Journal
Annals of the New York Academy of Sciences
Volume 1315, Issue 1, Pages 6-15
Publisher
Wiley
Online
2014-02-12
DOI
10.1111/nyas.12347
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- A semi-automated method for isolating functionally intact mitochondria from cultured cells and tissue biopsies
- (2013) Sabine Schmitt et al. ANALYTICAL BIOCHEMISTRY
- Iron and Copper in Mitochondrial Diseases
- (2013) Wenjing Xu et al. Cell Metabolism
- Copper Import into the Mitochondrial Matrix in Saccharomyces cerevisiae Is Mediated by Pic2, a Mitochondrial Carrier Family Protein
- (2013) Katherine E. Vest et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Brain metal accumulation in Wilson's disease
- (2013) T. Litwin et al. JOURNAL OF THE NEUROLOGICAL SCIENCES
- Neurochemical and Behavioral Characteristics of Toxic Milk Mice: An Animal Model of Wilson’s Disease
- (2013) Adam Przybyłkowski et al. NEUROCHEMICAL RESEARCH
- The treatment of Wilson's disease, a rare genetic disorder of copper metabolism
- (2013) Rupert Purchase SCIENCE PROGRESS
- Inherited Copper Transport Disorders: Biochemical Mechanisms, Diagnosis, and Treatment
- (2012) Hiroko Kodama et al. CURRENT DRUG METABOLISM
- Severe dysfunction of respiratory chain and cholesterol metabolism in Atp7b−/− mice as a model for Wilson disease
- (2011) Sven W. Sauer et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE
- Systems biology approach to Wilson’s disease
- (2011) Jason L. Burkhead et al. BIOMETALS
- SOD1 and mitochondria in ALS: a dangerous liaison
- (2011) Maria Teresa Carrì et al. JOURNAL OF BIOENERGETICS AND BIOMEMBRANES
- Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease
- (2011) Hans Zischka et al. JOURNAL OF CLINICAL INVESTIGATION
- Neuroinflammatory and behavioural changes in the Atp7B mutant mouse model of Wilson’s disease
- (2011) Dick Terwel et al. JOURNAL OF NEUROCHEMISTRY
- In vitro modulation of heavy metal-induced rat liver mitochondria dysfunction: A comparison of copper and mercury with cadmium
- (2010) Elena A. Belyaeva et al. JOURNAL OF TRACE ELEMENTS IN MEDICINE AND BIOLOGY
- The puzzle posed by COMMD1, a newly discovered protein binding Cu(ii)
- (2010) Bibudhendra Sarkar et al. Metallomics
- Affinity gradients drive copper to cellular destinations
- (2010) Lucia Banci et al. NATURE
- Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1
- (2009) Scot C. Leary et al. HUMAN MOLECULAR GENETICS
- Mitochondrial gateways to cancer
- (2009) Lorenzo Galluzzi et al. MOLECULAR ASPECTS OF MEDICINE
- Electrophoretic Analysis of the Mitochondrial Outer Membrane Rupture Induced by Permeability Transition
- (2008) Hans Zischka et al. ANALYTICAL CHEMISTRY
- How mitochondria produce reactive oxygen species
- (2008) Michael P. Murphy BIOCHEMICAL JOURNAL
- Cu(I)–Glutathione complex: A potential source of superoxide radicals generation
- (2008) Hernán Speisky et al. BIOORGANIC & MEDICINAL CHEMISTRY
- Diagnosis and treatment of Wilson disease: An update
- (2008) Eve A. Roberts et al. HEPATOLOGY
- Role of genotyping in Wilson’s disease
- (2008) Hartmut H.-J. Schmidt JOURNAL OF HEPATOLOGY
- Mechanisms for copper acquisition, distribution and regulation
- (2008) Byung-Eun Kim et al. Nature Chemical Biology
- Mitochondrial structure and function in the untreated Jackson toxic milk (tx-j) mouse, a model for Wilson disease
- (2007) Eve A. Roberts et al. MOLECULAR GENETICS AND METABOLISM
Discover Peeref hubs
Discuss science. Find collaborators. Network.
Join a conversationCreate your own webinar
Interested in hosting your own webinar? Check the schedule and propose your idea to the Peeref Content Team.
Create Now