Denufosol Tetrasodium in Patients with Cystic Fibrosis and Normal to Mildly Impaired Lung Function

Failure to Recover to Baseline Pulmonary Function after Cystic Fibrosis Pulmonary Exacerbation

(2010) Don B. Sanders et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Effect of Azithromycin on Pulmonary Function in Patients With Cystic Fibrosis Uninfected With Pseudomonas aeruginosaA Randomized Controlled Trial

(2010) Lisa Saiman   JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION

Denufosol improves lung function in adolescent CF patients

(2010) R.B. Moss et al.   Journal of Cystic Fibrosis

Potential of denufosol as an early intervention in CF lung disease: efficacy in patients with minimal pharmacotherapy in a US phase 3 clinical trial

(2010) F.J. Accurso et al.   Journal of Cystic Fibrosis

Aerosol and pharmacokinetic properties of denufosol support its use for early intervention in CF lung disease

(2010) T. Navratil et al.   Journal of Cystic Fibrosis

Return of FEV1after pulmonary exacerbation in children with cystic fibrosis

(2010) Don B. Sanders et al.   PEDIATRIC PULMONOLOGY

Cystic fibrosis lung disease starts in the small airways: Can we treat it more effectively?

(2010) Harm A.W.M. Tiddens et al.   PEDIATRIC PULMONOLOGY

Lung Disease at Diagnosis in Infants with Cystic Fibrosis Detected by Newborn Screening

(2009) Peter D. Sly et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Purinergic receptors in airway epithelia

(2009) Eduardo R Lazarowski et al.   CURRENT OPINION IN PHARMACOLOGY

Transmembrane Protein 16A (TMEM16A) Is a Ca2+-regulated Cl–Secretory Channel in Mouse Airways

(2009) Jason R. Rock et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Measuring and improving respiratory outcomes in cystic fibrosis lung disease: Opportunities and challenges to therapy

(2009) Edith T. Zemanick et al.   Journal of Cystic Fibrosis

Bronchiectasis in Infants and Preschool Children Diagnosed with Cystic Fibrosis after Newborn Screening

(2009) Stephen M. Stick et al.   JOURNAL OF PEDIATRICS

Lung Function in Infants with Cystic Fibrosis Diagnosed by Newborn Screening

(2008) Barry M. Linnane et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Lung Function from Infancy to the Preschool Years after Clinical Diagnosis of Cystic Fibrosis

(2008) Wanda J. Kozlowska et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

CFTR Function and Prospects for Therapy

(2008) John R. Riordan   Annual Review of Biochemistry

Expression Cloning of TMEM16A as a Calcium-Activated Chloride Channel Subunit

(2008) Björn Christian Schroeder et al.   CELL

Early referral to cystic fibrosis specialist centre impacts on respiratory outcome

(2008) P. Lebecque et al.   Journal of Cystic Fibrosis

TMEM16A confers receptor-activated calcium-dependent chloride conductance

(2008) Young Duk Yang et al.   NATURE

Early Detection of Lung Disease in Children with Cystic Fibrosis Using Lung Function

(2008) Sarath Ranganathan et al.   Paediatric Respiratory Reviews

Denufosol: A review of studies with inhaled P2Y2 agonists that led to Phase 3

(2008) Donald Kellerman et al.   PULMONARY PHARMACOLOGY & THERAPEUTICS

Recurrent exacerbations affect FEV1 decline in adult patients with cystic fibrosis

(2008) Anna Amadori et al.   RESPIRATORY MEDICINE

TMEM16A, A Membrane Protein Associated with Calcium-Dependent Chloride Channel Activity

(2008) A. Caputo et al.   SCIENCE

Reference Ranges for Spirometry Across All Ages

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