Mitochondrial complex III Rieske Fe-S protein processing and assembly

LYRM7 - associated complex III deficiency: A clinical, molecular genetic, MR tomographic, and biochemical study

(2017) Maja Hempel et al.   MITOCHONDRION

TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III

(2017) Emanuela Bottani et al.   MOLECULAR CELL

LYRM7mutations cause a multifocal cavitating leukoencephalopathy with distinct MRI appearance

(2016) Cristina Dallabona et al.   BRAIN

The membrane scaffold SLP2 anchors a proteolytic hub in mitochondria containing PARL and the i ‐AAA protease YME1L

(2016) Timothy Wai et al.   EMBO REPORTS

Hydrogen Bonding to the Substrate Is Not Required for Rieske Iron-Sulfur Protein Docking to the Quinol Oxidation Site of Complex III

(2016) Lothar Esser et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Severe respiratory complex III defect prevents liver adaptation to prolonged fasting

(2016) Laura S. Kremer et al.   JOURNAL OF HEPATOLOGY

New paradigms for understanding and step changes in treating active and chronic, persistent apicomplexan infections

(2016) Martin McPhillie et al.   Scientific Reports

Phenotypic variation ofTTC19-deficient mitochondrial complex III deficiency: A case report and literature review

(2015) Dylan A. Mordaunt et al.   AMERICAN JOURNAL OF MEDICAL GENETICS PART A

Respiratory chain protein turnover rates in mice are highly heterogeneous but strikingly conserved across tissues, ages, and treatments

(2015) Pabalu P. Karunadharma et al.   FASEB JOURNAL

Antimalarial 4(1H)-pyridones bind to the Qisite of cytochromebc1

(2015) Michael J. Capper et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Nuclear gene mutations as the cause of mitochondrial complex III deficiency

(2015) Erika Fernández-Vizarra et al.   Frontiers in Genetics

Cochaperone Binding to LYR Motifs Confers Specificity of Iron Sulfur Cluster Delivery

(2014) Nunziata Maio et al.   Cell Metabolism

A mutation in the human CBP4 ortholog UQCC3 impairs complex III assembly, activity and cytochrome b stability

(2014) Bas F.J. Wanschers et al.   HUMAN MOLECULAR GENETICS

Assembly factors monitor sequential hemylation of cytochromebto regulate mitochondrial translation

(2014) Markus Hildenbeutel et al.   JOURNAL OF CELL BIOLOGY

Unanswered questions about the structure of cytochrome bc1 complexes

(2013) Edward A. Berry et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

A Homozygous Mutation inLYRM7/MZM1LAssociated with Early Onset Encephalopathy, Lactic Acidosis, and Severe Reduction of Mitochondrial Complex III Activity

(2013) Federica Invernizzi et al.   HUMAN MUTATION

Mutations in the UQCC1-Interacting Protein, UQCC2, Cause Human Complex III Deficiency Associated with Perturbed Cytochrome b Protein Expression

(2013) Elena J. Tucker et al.   PLoS Genetics

LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells

(2012) Ester Sánchez et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

The Cbp3–Cbp6 complex coordinates cytochromebsynthesis withbc1complex assembly in yeast mitochondria

(2012) Steffi Gruschke et al.   JOURNAL OF CELL BIOLOGY

Computational Discovery of Picomolar Qo Site Inhibitors of Cytochrome bc1 Complex

(2012) Ge-Fei Hao et al.   JOURNAL OF THE AMERICAN CHEMICAL SOCIETY

Late-Stage Maturation of the Rieske Fe/S Protein: Mzm1 Stabilizes Rip1 but Does Not Facilitate Its Translocation by the AAA ATPase Bcs1

(2012) T.-Z. Cui et al.   MOLECULAR AND CELLULAR BIOLOGY

The Q cycle of cytochrome bc complexes: A structure perspective

(2011) William A. Cramer et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Biogenesis of the cytochrome bc1 complex and role of assembly factors

(2011) Pamela M. Smith et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Cbp3–Cbp6 interacts with the yeast mitochondrial ribosomal tunnel exit and promotes cytochromebsynthesis and assembly

(2011) Steffi Gruschke et al.   JOURNAL OF CELL BIOLOGY

A Pathway of Protein Translocation in Mitochondria Mediated by the AAA-ATPase Bcs1

(2011) Nikola Wagener et al.   MOLECULAR CELL

Mutations in TTC19 cause mitochondrial complex III deficiency and neurological impairment in humans and flies

(2011) Daniele Ghezzi et al.   NATURE GENETICS

Ascochlorin is a novel, specific inhibitor of the mitochondrial cytochrome bc1 complex

(2009) Edward A. Berry et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Importing Mitochondrial Proteins: Machineries and Mechanisms

(2009) Agnieszka Chacinska et al.   CELL

The Q-cycle reviewed: How well does a monomeric mechanism of the bc1 complex account for the function of a dimeric complex?

(2008) Antony R. Crofts et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Biogenesis of the yeast cytochrome bc1 complex

(2008) Vincenzo Zara et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

The role of molecular modeling in the design of analogues of the fungicidal natural products crocacins A and D

(2008) Patrick J. Crowley et al.   BIOORGANIC & MEDICINAL CHEMISTRY