Dermal fibroblast-to-myofibroblast transition sustained by αvß3 integrin-ILK-Snail1/Slug signaling is a common feature for hypermobile Ehlers-Danlos syndrome and hypermobility spectrum disorders

Title
Dermal fibroblast-to-myofibroblast transition sustained by αvß3 integrin-ILK-Snail1/Slug signaling is a common feature for hypermobile Ehlers-Danlos syndrome and hypermobility spectrum disorders
Authors
Keywords
Hypermobile Ehlers-Danlos syndrome, Hypermobility Spectrum Disorders, Fibroblast-to-myofibroblast transition, αvβ3 integrin, Snail1/Slug, Chronic generalized inflammation
Journal
Publisher
Elsevier BV
Online
2018-01-06
DOI
10.1016/j.bbadis.2018.01.005

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