Genetic ablation of N-linked glycosylation reveals two key folding pathways for R345W fibulin-3, a secreted protein associated with retinal degeneration

ER-associated degradation: Protein quality control and beyond

(2014) Annamaria Ruggiano et al.   JOURNAL OF CELL BIOLOGY

Mouse genetics and proteomic analyses demonstrate a critical role for complement in a model of DHRD/ML, an inherited macular degeneration

(2013) Donita L. Garland et al.   HUMAN MOLECULAR GENETICS

Fibulin-3, -4, and -5 Are Highly Susceptible to Proteolysis, Interact with Cells and Heparin, and Form Multimers

(2013) Jelena Djokic et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

ERdj5 Is the ER Reductase that Catalyzes the Removal of Non-Native Disulfides and Correct Folding of the LDL Receptor

(2013) Ojore Benedict Valentine Oka et al.   MOLECULAR CELL

Interaction of Complement Factor H and Fibulin3 in Age-Related Macular Degeneration

(2013) M. Keith Wyatt et al.   PLoS One

Specificity and Regulation of the Endoplasmic Reticulum-Associated Degradation Machinery

(2013) Jessica Merulla et al.   TRAFFIC

Translational attenuation differentially alters the fate of disease-associated fibulin proteins

(2012) John D. Hulleman et al.   FASEB JOURNAL

The Delicate Balance Between Secreted Protein Folding and Endoplasmic Reticulum-Associated Degradation in Human Physiology

(2012) Christopher J. Guerriero et al.   PHYSIOLOGICAL REVIEWS

Applying massive parallel sequencing to molecular diagnosis of Marfan and Loeys-Dietz syndromes

(2011) Machteld Baetens et al.   HUMAN MUTATION

Compromised mutant EFEMP1 secretion associated with macular dystrophy remedied by proteostasis network alteration

(2011) John D. Hulleman et al.   MOLECULAR BIOLOGY OF THE CELL

Protein Native-State Stabilization by Placing Aromatic Side Chains in N-Glycosylated Reverse Turns

(2011) E. K. Culyba et al.   SCIENCE

Disulphide production by Ero1α–PDI relay is rapid and effectively regulated

(2010) Christian Appenzeller-Herzog et al.   EMBO JOURNAL

Focus on molecules: Fibulin-3 (EFEMP1)

(2009) Youwen Zhang et al.   EXPERIMENTAL EYE RESEARCH

ECM1 interacts with fibulin-3 and the beta 3 chain of laminin 332 through its serum albumin subdomain-like 2 domain

(2009) S. Sercu et al.   MATRIX BIOLOGY

The core trisaccharide of an N-linked glycoprotein intrinsically accelerates folding and enhances stability

(2009) S. R. Hanson et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Retracted: Lectin-deficient Calreticulin Retains Full Functionality as a Chaperone for Class I Histocompatibility Molecules

(2008) Breanna S. Ireland et al.   MOLECULAR BIOLOGY OF THE CELL

One step at a time: endoplasmic reticulum-associated degradation

(2008) Shruthi S. Vembar et al.   NATURE REVIEWS MOLECULAR CELL BIOLOGY