Journal
JAAPA-JOURNAL OF THE AMERICAN ACADEMY OF PHYSICIAN ASSISTANTS
Volume 30, Issue 5, Pages 23-27Publisher
LIPPINCOTT WILLIAMS & WILKINS
DOI: 10.1097/01.JAA.0000515540.36581.92
Keywords
cystic fibrosis; newborn screening; chloride sweat test; bronchiectasis; Brasfield score; airway clearance therapy
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Cystic fibrosis (CF) affects more than 30,000 people in the United States and 80,000 people worldwide. This life-threatening genetic disorder causes a buildup of thick, viscous mucus secretions in various organ systems, most commonly the gastrointestinal, pulmonary, and genitourinary systems. This article reviews the clinical manifestations, diagnosis, and monitoring of patients with CF as well as guidelines for management and emerging pharmacologic treatments.
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