Mammalian mitochondrial RNAs are degraded in the mitochondrial intermembrane space by RNASET2

Metabolic regulation of mitochondrial dynamics

(2016) Prashant Mishra et al.   JOURNAL OF CELL BIOLOGY

Identification of LACTB2, a metallo-β-lactamase protein, as a human mitochondrial endoribonuclease

(2016) Shiri Levy et al.   NUCLEIC ACIDS RESEARCH

Mitochondrial endonuclease G mediates breakdown of paternal mitochondria upon fertilization

(2016) Q. Zhou et al.   SCIENCE

Filling the Void: Proximity-Based Labeling of Proteins in Living Cells

(2016) Dae In Kim et al.   TRENDS IN CELL BIOLOGY

SUV3 helicase is required for correct processing of mitochondrial transcripts

(2015) Paula Clemente et al.   NUCLEIC ACIDS RESEARCH

MicroRNA Directly Enhances Mitochondrial Translation during Muscle Differentiation

(2014) Xiaorong Zhang et al.   CELL

Making Proteins in the Powerhouse

(2014) B. Martin Hällberg et al.   Cell Metabolism

Targeting and plasticity of mitochondrial proteins revealed by proximity-specific ribosome profiling

(2014) C. C. Williams et al.   SCIENCE

Principles of ER cotranslational translocation revealed by proximity-specific ribosome profiling

(2014) C. H. Jan et al.   SCIENCE

Yeast and human mitochondrial helicases

(2013) Roman J. Szczesny et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

The role of microRNAs in mitochondria in cancer

(2013) Julie Bienertova-Vasku et al.   CANCER LETTERS

REXO2 Is an Oligoribonuclease Active in Human Mitochondria

(2013) Francesco Bruni et al.   PLoS One

Mutation in PNPT1 , which Encodes a Polyribonucleotide Nucleotidyltransferase, Impairs RNA Import into Mitochondria and Causes Respiratory-Chain Deficiency

(2012) Vanessa Vedrenne et al.   AMERICAN JOURNAL OF HUMAN GENETICS

A Mutation in PNPT1 , Encoding Mitochondrial-RNA-Import Protein PNPase, Causes Hereditary Hearing Loss

(2012) Simon von Ameln et al.   AMERICAN JOURNAL OF HUMAN GENETICS

A promiscuous biotin ligase fusion protein identifies proximal and interacting proteins in mammalian cells

(2012) Kyle J. Roux et al.   JOURNAL OF CELL BIOLOGY

LRPPRC/SLIRP suppresses PNPase-mediated mRNA decay and promotes polyadenylation in human mitochondria

(2012) Takeshi Chujo et al.   NUCLEIC ACIDS RESEARCH

Human mitochondrial RNA decay mediated by PNPase–hSuv3 complex takes place in distinct foci

(2012) Lukasz S. Borowski et al.   NUCLEIC ACIDS RESEARCH

RNA Degradation in Yeast and Human Mitochondria

(2011) Roman J. Szczesny et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

The Human Mitochondrial Transcriptome

(2011) Tim R. Mercer et al.   CELL

RNA processing in human mitochondria

(2011) Maria I.G. Lopez Sanchez et al.   CELL CYCLE

Biological significance of 5S rRNA import into human mitochondria: role of ribosomal protein MRP-L18

(2011) A. Smirnov et al.   GENES & DEVELOPMENT

Yeast mitochondrial RNase P, RNase Z and the RNA degradosome are part of a stable supercomplex

(2011) Rachid Daoud et al.   NUCLEIC ACIDS RESEARCH

PNPASE Regulates RNA Import into Mitochondria

(2010) Geng Wang et al.   CELL

Microenvironmental control of malignancy exerted by RNASET2, a widely conserved extracellular RNase

(2010) F. Acquati et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

T2 Family ribonucleases: ancient enzymes with diverse roles

(2010) Natalie Luhtala et al.   TRENDS IN BIOCHEMICAL SCIENCES

RNASET2-deficient cystic leukoencephalopathy resembles congenital cytomegalovirus brain infection

(2009) Marco Henneke et al.   NATURE GENETICS

Polynucleotide phosphorylase and the archaeal exosome as poly(A)-polymerases

(2008) Shimyn Slomovic et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

Import of tRNAs and aminoacyl-tRNA synthetases into mitochondria

(2008) Anne-Marie Duchêne et al.   CURRENT GENETICS

Role of SUV3 Helicase in Maintaining Mitochondrial Homeostasis in Human Cells

(2008) Lily Khidr et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mammalian mitochondria have the innate ability to import tRNAs by a mechanism distinct from protein import

(2008) M. A. T. Rubio et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA