Bergmann glia translocation: a new disease marker for vanishing white matter identifies therapeutic effects of Guanabenz treatment

The spectrum of leukodystrophies in children: Experience at a tertiary care centre from North India

(2016) Sheffali Gulati et al.   Annals of Indian Academy of Neurology

Astrocytes are central in the pathomechanisms of vanishing white matter

(2016) Stephanie Dooves et al.   JOURNAL OF CLINICAL INVESTIGATION

Stem cell therapy for white matter disorders: don’t forget the microenvironment!

(2016) Stephanie Dooves et al.   JOURNAL OF INHERITED METABOLIC DISEASE

Genome-editing Technologies for Gene and Cell Therapy

(2016) Morgan L Maeder et al.   MOLECULAR THERAPY

Genome-wide RNA-Seq of Human Motor Neurons Implicates Selective ER Stress Activation in Spinal Muscular Atrophy

(2015) Shi-Yan Ng et al.   Cell Stem Cell

Combined gene/cell therapies provide long-term and pervasive rescue of multiple pathological symptoms in a murine model of globoid cell leukodystrophy

(2015) A. Ricca et al.   HUMAN MOLECULAR GENETICS

Inhibition of Eukaryotic Initiation Factor 2 Alpha Phosphatase Reduces Tissue Damage and Improves Learning and Memory after Experimental Traumatic Brain Injury

(2015) Pramod K. Dash et al.   JOURNAL OF NEUROTRAUMA

Preventing proteostasis diseases by selective inhibition of a phosphatase regulatory subunit

(2015) I. Das et al.   SCIENCE

Differential temporal expression of S100β in developing rat brain

(2015) Nisha Patro et al.   Frontiers in Cellular Neuroscience

Pharmaceutical integrated stress response enhancement protects oligodendrocytes and provides a potential multiple sclerosis therapeutic

(2015) Sharon W. Way et al.   Nature Communications

Stain-free detection as loading control alternative to Ponceau and housekeeping protein immunodetection in Western blotting

(2014) B. Rivero-Gutiérrez et al.   ANALYTICAL BIOCHEMISTRY

Guanabenz, which enhances the unfolded protein response, ameliorates mutant SOD1-induced amyotrophic lateral sclerosis

(2014) Lijun Wang et al.   NEUROBIOLOGY OF DISEASE

Phases of intermediate filament composition in Bergmann glia following cerebellar injury in adult rat

(2014) Istvan Adorjan et al.   EXPERIMENTAL BRAIN RESEARCH

Hyaluronan accumulation and arrested oligodendrocyte progenitor maturation in vanishing white matter disease

(2013) Marianna Bugiani et al.   BRAIN

Origin, lineage and function of cerebellar glia

(2013) Annalisa Buffo et al.   PROGRESS IN NEUROBIOLOGY

Stain-Free technology as a normalization tool in Western blot analysis

(2012) Anne Gürtler et al.   ANALYTICAL BIOCHEMISTRY

Glial Progenitor Cell-Based Treatment and Modeling of Neurological Disease

(2012) S. A. Goldman et al.   SCIENCE

Relative Incidence of Inherited White Matter Disorders in Childhood to Acquired Pediatric Demyelinating Disorders

(2012) Adeline Vanderver et al.   Seminars in Pediatric Neurology

Loss of adenomatous polyposis coli in Bergmann glia disrupts their unique architecture and leads to cell nonautonomous neurodegeneration of cerebellar Purkinje neurons

(2011) Xiaohong Wang et al.   GLIA

Selective Inhibition of a Regulatory Subunit of Protein Phosphatase 1 Restores Proteostasis

(2011) P. Tsaytler et al.   SCIENCE

Leukoencephalopathy With Vanishing White Matter: A Review

(2010) Marianna Bugiani et al.   JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY

Defective Glial Maturation in Vanishing White Matter Disease

(2010) Marianna Bugiani et al.   JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY

The burden of inherited leukodystrophies in children

(2010) J. L. Bonkowsky et al.   NEUROLOGY

Antihypertensive Drug Guanabenz Is Active In Vivo against both Yeast and Mammalian Prions

(2008) Déborah Tribouillard-Tanvier et al.   PLoS One