Peripheral muscle abnormalities in cystic fibrosis: Etiology, clinical implications and response to therapeutic interventions

Title
Peripheral muscle abnormalities in cystic fibrosis: Etiology, clinical implications and response to therapeutic interventions
Authors
Keywords
Cystic fibrosis, Muscle function, Exercise interventions, Aerobic function, CFTR, Nutritional status, Muscle metabolism
Journal
Journal of Cystic Fibrosis
Volume 16, Issue 5, Pages 538-552
Publisher
Elsevier BV
Online
2017-03-03
DOI
10.1016/j.jcf.2017.02.007

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