A randomized trial to study the comparative efficacy of phenylbutyrate and benzoate on nitrogen excretion and ureagenesis in healthy volunteers

Averting the foul taste of pediatric medicines improves adherence and can be lifesaving – Pheburane® (sodium phenylbutyrate)

(2016) Gideon Koren et al.   Patient Preference and Adherence

Phenylbutyric Acid: Simple Structure - Multiple Effects

(2015) Magdalena Kusaczuk et al.   CURRENT PHARMACEUTICAL DESIGN

The therapeutic effects of 4-phenylbutyric acid in maintaining proteostasis

(2015) P.S. Kolb et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

Blood ammonia and glutamine as predictors of hyperammonemic crises in patients with urea cycle disorder

(2014) Brendan Lee et al.   GENETICS IN MEDICINE

Sodium phenylbutyrate decreases plasma branched-chain amino acids in patients with urea cycle disorders

(2014) Lindsay C. Burrage et al.   MOLECULAR GENETICS AND METABOLISM

Results from a Nationwide Cohort Temporary Utilization Authorization (ATU) Survey of Patients in France Treated with Pheburane® (Sodium Phenylbutyrate) Taste-Masked Granules

(2014) Yves Kibleur et al.   PEDIATRIC DRUGS

Clinical and Experimental Applications of Sodium Phenylbutyrate

(2013) Tommaso Iannitti et al.   Drugs in research & development

Suggested guidelines for the diagnosis and management of urea cycle disorders

(2012) Johannes Häberle et al.   Orphanet Journal of Rare Diseases

Phenylbutyrate improves nitrogen disposal via an alternative pathway without eliciting an increase in protein breakdown and catabolism in control and ornithine transcarbamylase–deficient patients

(2011) Juan C Marini et al.   AMERICAN JOURNAL OF CLINICAL NUTRITION

Quantitative analysis of 15N-labeled positional isomers of glutamine and citrulline via electrospray ionization tandem mass spectrometry of their dansyl derivatives

(2011) Juan C. Marini   RAPID COMMUNICATIONS IN MASS SPECTROMETRY

Alternative pathway or diversion therapy for urea cycle disorders now and in the future

(2010) Stephen Cederbaum et al.   MOLECULAR GENETICS AND METABOLISM

Nitrogen sparing therapy revisited 2009

(2010) Gregory M. Enns   MOLECULAR GENETICS AND METABOLISM

Phase 2 comparison of a novel ammonia scavenging agent with sodium phenylbutyrate in patients with urea cycle disorders: Safety, pharmacokinetics and ammonia control

(2010) Brendan Lee et al.   MOLECULAR GENETICS AND METABOLISM