Idiopathic Pulmonary Fibrosis: A Genetic Disease That Involves Mucociliary Dysfunction of the Peripheral Airways

MUC5BPromoter Variant rs35705950 Affects MUC5B Expression in the Distal Airways in Idiopathic Pulmonary Fibrosis

(2016) Yasushi Nakano et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Flow Cytometry Reveals Similarities Between Lung Macrophages in Humans and Mice

(2016) Ankit Bharat et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Association Between Interstitial Lung Abnormalities and All-Cause Mortality

(2016) Rachel K. Putman et al.   JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION

Lost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease

(2015) Surafel Mulugeta et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Extensive Phenotyping of Individuals at Risk for Familial Interstitial Pneumonia Reveals Clues to the Pathogenesis of Interstitial Lung Disease

(2015) Jonathan A. Kropski et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Rare Variants inRTEL1Are Associated with Familial Interstitial Pneumonia

(2015) Joy D. Cogan et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Mucins: A biologically relevant glycan barrier in mucosal protection

(2015) Anthony P. Corfield   BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS

Autoimmunity

(2015) Marvin Schwarz   CHEST

CT Scan Findings of Probable Usual Interstitial Pneumonitis Have a High Predictive Value for Histologic Usual Interstitial Pneumonitis

(2015) Jonathan H. Chung et al.   CHEST

The MUC5B Promoter Polymorphism Is Associated With Idiopathic Pulmonary Fibrosis in a Mexican Cohort but Is Rare Among Asian Ancestries

(2015) Anna L. Peljto et al.   CHEST

Immunohistochemical Expressions of MUC2, MUC5AC, and MUC6 in Normal,Helicobacter pyloriInfected and Metaplastic Gastric Mucosa of Children and Adolescents

(2015) Ji Sook Park et al.   HELICOBACTER

Endogenous airway mucins carry glycans that bind Siglec-F and induce eosinophil apoptosis

(2015) Takumi Kiwamoto et al.   JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY

Alveolar epithelial cells undergo epithelial-to-mesenchymal transition in response to endoplasmic reticulum stress.

(2015) Harikrishna Tanjore et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Basal cells of the human airways acquire mesenchymal traits in idiopathic pulmonary fibrosis and in culture

(2015) Hulda R Jonsdottir et al.   LABORATORY INVESTIGATION

A global reference for human genetic variation

(2015) Richard A. Gibbs et al.   NATURE

Exome sequencing links mutations in PARN and RTEL1 with familial pulmonary fibrosis and telomere shortening

(2015) Bridget D Stuart et al.   NATURE GENETICS

Forced Vital Capacity in Idiopathic Pulmonary Fibrosis — FDA Review of Pirfenidone and Nintedanib

(2015) Banu A. Karimi-Shah et al.   NEW ENGLAND JOURNAL OF MEDICINE

MUC5Bpromoter polymorphism in Japanese patients with idiopathic pulmonary fibrosis

(2015) Yasushi Horimasu et al.   RESPIROLOGY

Genetics and Early Detection in Idiopathic Pulmonary Fibrosis

(2014) Rachel K. Putman et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Foxa3 Induces Goblet Cell Metaplasia and Inhibits Innate Antiviral Immunity

(2014) Gang Chen et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

The Role of Bacteria in the Pathogenesis and Progression of Idiopathic Pulmonary Fibrosis

(2014) Phillip L. Molyneaux et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Interleukin-4 and interleukin-13 pathway genetics affect disease susceptibility, serum immunoglobulin E levels, and gene expression in asthma

(2014) Jia Li et al.   ANNALS OF ALLERGY ASTHMA & IMMUNOLOGY

Cilia and Diseases

(2014) Jason M. Brown et al.   BIOSCIENCE

Genetic susceptibility and pulmonary fibrosis

(2014) Susan K. Mathai et al.   CURRENT OPINION IN PULMONARY MEDICINE

Lineage-negative progenitors mobilize to regenerate lung epithelium after major injury

(2014) Andrew E. Vaughan et al.   NATURE

Emerging functions of the unfolded protein response in immunity

(2014) Sophie Janssens et al.   NATURE IMMUNOLOGY

A Phase 3 Trial of Pirfenidone in Patients with Idiopathic Pulmonary Fibrosis

(2014) Talmadge E. King et al.   NEW ENGLAND JOURNAL OF MEDICINE

Polymorphisms of MUC16 (CA125) and MUC1 (CA15.3) in Relation to Ovarian Cancer Risk and Survival

(2014) Kristina A. Williams et al.   PLoS One

A Biophysical Basis for Mucus Solids Concentration as a Candidate Biomarker for Airways Disease

(2014) David B. Hill et al.   PLoS One

The Effect of MUC1 rs4072037 Functional Polymorphism on Cancer Susceptibility: Evidence from Published Studies

(2014) Fujiao Duan et al.   PLoS One

Mucin 5B Promoter Polymorphism Is Associated with Susceptibility to Interstitial Lung Diseases in Chinese Males

(2014) Chunli Wang et al.   PLoS One

Design of the INPULSIS™ trials: Two phase 3 trials of nintedanib in patients with idiopathic pulmonary fibrosis

(2014) Luca Richeldi et al.   RESPIRATORY MEDICINE

Altered Surfactant Homeostasis and Alveolar Epithelial Cell Stress in Amiodarone-Induced Lung Fibrosis

(2014) Poornima Mahavadi et al.   TOXICOLOGICAL SCIENCES

An Official American Thoracic Society/European Respiratory Society Statement: Update of the International Multidisciplinary Classification of the Idiopathic Interstitial Pneumonias

(2013) William D. Travis et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

The Toll-like Receptor 3 L412F Polymorphism and Disease Progression in Idiopathic Pulmonary Fibrosis

(2013) David N. O’Dwyer et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Primary Ciliary Dyskinesia. Recent Advances in Diagnostics, Genetics, and Characterization of Clinical Disease

(2013) Michael R. Knowles et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Flow Cytometric Analysis of Macrophages and Dendritic Cell Subsets in the Mouse Lung

(2013) Alexander V. Misharin et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

A Multidimensional Index and Staging System for Idiopathic Pulmonary Fibrosis

(2013) Brett Ley et al.   ANNALS OF INTERNAL MEDICINE

Association Between the MUC5B Promoter Polymorphism and Survival in Patients With Idiopathic Pulmonary Fibrosis

(2013) Anna L. Peljto et al.   JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION

Type 2 alveolar cells are stem cells in adult lung

(2013) Christina E. Barkauskas et al.   JOURNAL OF CLINICAL INVESTIGATION

Comparative proteome analysis of lung tissue from patients with idiopathic pulmonary fibrosis (IPF), non-specific interstitial pneumonia (NSIP) and organ donors

(2013) Martina Korfei et al.   Journal of Proteomics

Expression of MUC2, MUC5AC, MUC5B and MUC6 mucins in colorectal cancers and their association with the CpG island methylator phenotype

(2013) Michael D Walsh et al.   MODERN PATHOLOGY

ER-stress-induced transcriptional regulation increases protein synthesis leading to cell death

(2013) Jaeseok Han et al.   NATURE CELL BIOLOGY

Genome-wide association study identifies multiple susceptibility loci for pulmonary fibrosis

(2013) Tasha E Fingerlin et al.   NATURE GENETICS

Targeting the unfolded protein response in disease

(2013) Claudio Hetz et al.   NATURE REVIEWS DRUG DISCOVERY

MUC5B Promoter Polymorphism and Interstitial Lung Abnormalities

(2013) Gary M. Hunninghake et al.   NEW ENGLAND JOURNAL OF MEDICINE

The Idiopathic Pulmonary Fibrosis Honeycomb Cyst Contains A Mucocilary Pseudostratified Epithelium

(2013) Max A. Seibold et al.   PLoS One

The MUC5B Variant Is Associated with Idiopathic Pulmonary Fibrosis but Not with Systemic Sclerosis Interstitial Lung Disease in the European Caucasian Population

(2013) Raphael Borie et al.   PLoS One

Risk Factors for Poor Treatment Outcomes in Patients with MDR-TB and XDR-TB in China: Retrospective Multi-Center Investigation

(2013) Shenjie Tang et al.   PLoS One

Chronic Hypersensitivity Pneumonitis: Differentiation from Idiopathic Pulmonary Fibrosis and Nonspecific Interstitial Pneumonia by Using Thin-Section CT

(2013) C. Isabela S. Silva et al.   RADIOLOGY

Peripheral Blood Mononuclear Cell Gene Expression Profiles Predict Poor Outcome in Idiopathic Pulmonary Fibrosis

(2013) J. D. Herazo-Maya et al.   Science Translational Medicine

Expression of cilium-associated genes defines novel molecular subtypes of idiopathic pulmonary fibrosis

(2013) Ivana V Yang et al.   THORAX

Mucin 5B promoter polymorphism is associated with idiopathic pulmonary fibrosis but not with development of lung fibrosis in systemic sclerosis or sarcoidosis

(2013) Carmel J Stock et al.   THORAX

Premature lung aging and cellular senescence in the pathogenesis of idiopathic pulmonary fibrosis and COPD/emphysema

(2013) Marco Chilosi et al.   Translational Research

Association between MUC5B and TERT polymorphisms and different interstitial lung disease phenotypes

(2013) Rongrong Wei et al.   Translational Research

Genetic variants associated with idiopathic pulmonary fibrosis susceptibility and mortality: a genome-wide association study

(2013) Imre Noth et al.   Lancet Respiratory Medicine

Emerging evidence for endoplasmic reticulum stress in the pathogenesis of idiopathic pulmonary fibrosis

(2012) Harikrishna Tanjore et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

The Pulmonary Fibrosis-Associated MUC5B Promoter Polymorphism Does Not Influence the Development of Interstitial Pneumonia in Systemic Sclerosis

(2012) Anna L. Peljto et al.   CHEST

Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosis

(2012) J. A. Kropski et al.   Disease Models & Mechanisms

Pulmonary fibrosis: patterns and perpetrators

(2012) Paul W. Noble et al.   JOURNAL OF CLINICAL INVESTIGATION

The ER stress transducer IRE1β is required for airway epithelial mucin production

(2012) M B Martino et al.   Mucosal Immunology

Five amino acids in three HLA proteins explain most of the association between MHC and seropositive rheumatoid arthritis

(2012) Soumya Raychaudhuri et al.   NATURE GENETICS

MUC4 and MUC1 Expression in Adenocarcinoma of the Stomach Correlates with Vessel Invasion and Lymph Node Metastasis: An Immunohistochemical Study of Early Gastric Cancer

(2012) Yukihiro Tamura et al.   PLoS One

SAM-pointed domain ETS factor mediates epithelial cell-intrinsic innate immune signaling during airway mucous metaplasia

(2012) T. R. Korfhagen et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Cleaved cytokeratin-18 is a mechanistically informative biomarker in idiopathic pulmonary fibrosis

(2012) Seung-Ick Cha et al.   RESPIRATORY RESEARCH

A Periciliary Brush Promotes the Lung Health by Separating the Mucus Layer from Airway Epithelia

(2012) B. Button et al.   SCIENCE

Peripheral blood biomarkers in idiopathic pulmonary fibrosis

(2012) Rekha Vij et al.   Translational Research

Colitis development during the suckling-weaning transition in mucin Muc2-deficient mice

(2011) Nanda Burger-van Paassen et al.   AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY

Forced Vital Capacity in Patients with Idiopathic Pulmonary Fibrosis

(2011) Roland M. du Bois et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-based Guidelines for Diagnosis and Management

(2011) Ganesh Raghu et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Peripheral Blood Proteins Predict Mortality in Idiopathic Pulmonary Fibrosis

(2011) Thomas J. Richards et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Mucin Production during Prenatal and Postnatal Murine Lung Development

(2011) Michelle G. Roy et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Involvement of Endoplasmic Reticulum Stress in Myofibroblastic Differentiation of Lung Fibroblasts

(2011) Hyun Ah Baek et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Distal Airway Stem Cells Yield Alveoli In Vitro and during Lung Regeneration following H1N1 Influenza Infection

(2011) Pooja A. Kumar et al.   CELL

Idiopathic pulmonary fibrosis: guidelines for diagnosis and clinical management have advanced from consensus-based in 2000 to evidence-based in 2011

(2011) G. Raghu   EUROPEAN RESPIRATORY JOURNAL

Comparative Proteomic Analysis of Lung Tissue from Patients with Idiopathic Pulmonary Fibrosis (IPF) and Lung Transplant Donor Lungs

(2011) Martina Korfei et al.   JOURNAL OF PROTEOME RESEARCH

Idiopathic pulmonary fibrosis

(2011) Talmadge E King et al.   LANCET

Idiopathic Pulmonary Fibrosis — A Sticky Business

(2011) Richard C. Boucher   NEW ENGLAND JOURNAL OF MEDICINE

Lung Volumes and Emphysema in Smokers with Interstitial Lung Abnormalities

(2011) George R. Washko et al.   NEW ENGLAND JOURNAL OF MEDICINE

A Variant in the Promoter ofMUC5Band Idiopathic Pulmonary Fibrosis

(2011) Yingze Zhang et al.   NEW ENGLAND JOURNAL OF MEDICINE

A CommonMUC5BPromoter Polymorphism and Pulmonary Fibrosis

(2011) Max A. Seibold et al.   NEW ENGLAND JOURNAL OF MEDICINE

Endoplasmic reticulum stress enhances fibrotic remodeling in the lungs

(2011) W. E. Lawson et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Multiple stromal populations contribute to pulmonary fibrosis without evidence for epithelial to mesenchymal transition

(2011) J. R. Rock et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Ectopic respiratory epithelial cell differentiation in bronchiolised distal airspaces in idiopathic pulmonary fibrosis

(2011) L. Plantier et al.   THORAX

The rising incidence of idiopathic pulmonary fibrosis in the UK

(2011) V. Navaratnam et al.   THORAX

MUC4 stabilizes HER2 expression and maintains the cancer stem cell population in ovarian cancer cells

(2011) Moorthy P Ponnusamy et al.   Journal of Ovarian Research

Surfactant Protein C Mutations Are the Basis of a Significant Portion of Adult Familial Pulmonary Fibrosis in a Dutch Cohort

(2010) Coline H. M. van Moorsel et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Clinical Predictors of a Diagnosis of Idiopathic Pulmonary Fibrosis

(2010) Charlene D. Fell et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

The H Antigen at Epithelial Surfaces Is Associated with Susceptibility to Asthma Exacerbation

(2010) Anh L. Innes et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Clinical Course and Prediction of Survival in Idiopathic Pulmonary Fibrosis

(2010) Brett Ley et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Temporal Relationship between Primary and Motile Ciliogenesis in Airway Epithelial Cells

(2010) Raksha Jain et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Role of Endoplasmic Reticulum Stress in Epithelial–Mesenchymal Transition of Alveolar Epithelial Cells

(2010) Qian Zhong et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Connective Tissue Disease-Associated Interstitial Lung Disease

(2010) Aryeh Fischer et al.   CHEST

Acute exacerbation of idiopathic pulmonary fibrosis: incidence, risk factors and outcome

(2010) J. W. Song et al.   EUROPEAN RESPIRATORY JOURNAL

Risk factors in malignant transformation of gastric epithelial neoplasia categorized by the revised Vienna classification: endoscopic, pathological, and immunophenotypic features

(2010) Sung Hoon Jung et al.   Gastric Cancer

Mendelian disorders and multifactorial traits: the big divide or one for all?

(2010) Stylianos E. Antonarakis et al.   NATURE REVIEWS GENETICS

The primary cilium: a signalling centre during vertebrate development

(2010) Sarah C. Goetz et al.   NATURE REVIEWS GENETICS

A Controlled Trial of Sildenafil in Advanced Idiopathic Pulmonary Fibrosis

(2010)   NEW ENGLAND JOURNAL OF MEDICINE

Airway Mucus Function and Dysfunction

(2010) John V. Fahy et al.   NEW ENGLAND JOURNAL OF MEDICINE

Inhibition of Wnt/ -catenin/CREB binding protein (CBP) signaling reverses pulmonary fibrosis

(2010) W. R. Henderson et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Increased expression of YKL-40, a chitinase-like protein, in serum and lung of patients with idiopathic pulmonary fibrosis

(2010) Kazuki Furuhashi et al.   RESPIRATORY MEDICINE

Serum and BALF YKL-40 levels are predictors of survival in idiopathic pulmonary fibrosis

(2010) Nicoline M. Korthagen et al.   RESPIRATORY MEDICINE

Ciliary biology: Understanding the cellular and genetic basis of human ciliopathies

(2009) Magdalena Cardenas-Rodriguez et al.   AMERICAN JOURNAL OF MEDICAL GENETICS PART C-SEMINARS IN MEDICAL GENETICS

Ex VivoSputum Analysis Reveals Impairment of Protease-dependent Mucus Degradation by Plasma Proteins in Acute Asthma

(2009) Anh L. Innes et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

T-helper Type 2–driven Inflammation Defines Major Subphenotypes of Asthma

(2009) Prescott G. Woodruff et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

WNT5A Is a Regulator of Fibroblast Proliferation and Resistance to Apoptosis

(2009) Louis J. Vuga et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Small Airway Mucous Metaplasia and Inflammation in Chronic Obstructive Pulmonary Disease

(2009) Victor Kim et al.   COPD-Journal of Chronic Obstructive Pulmonary Disease

Marginal decline in forced vital capacity is associated with a poor outcome in idiopathic pulmonary fibrosis

(2009) C. J. Zappala et al.   EUROPEAN RESPIRATORY JOURNAL

MUC5AC expression is increased in bronchial submucosal glands of stable COPD patients

(2009) Gaetano Caramori et al.   HISTOPATHOLOGY

Tonicity-dependent induction of Sgk1 expression has a potential role in dehydration-induced natriuresis in rodents

(2009) Songcang Chen et al.   JOURNAL OF CLINICAL INVESTIGATION

CT Evaluation of Diffuse Infiltrative Lung Disease

(2009) John R. Mayo   JOURNAL OF THORACIC IMAGING

Basal cells as stem cells of the mouse trachea and human airway epithelium

(2009) J. R. Rock et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Exposures and Idiopathic Lung Disease

(2009) Varsha Taskar et al.   SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE

Genetic Defects in Surfactant Protein A2 Are Associated with Pulmonary Fibrosis and Lung Cancer

(2008) Yongyu Wang et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection

(2008) William E. Lawson et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Epithelial Endoplasmic Reticulum Stress and Apoptosis in Sporadic Idiopathic Pulmonary Fibrosis

(2008) Martina Korfei et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Idiopathic Nonspecific Interstitial Pneumonia

(2008) William D. Travis et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

MUC5B Is the Major Mucin in the Gel Phase of Sputum in Chronic Obstructive Pulmonary Disease

(2008) Sara Kirkham et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Genetic regulation of MUC1 alternative splicing in human tissues

(2008) W Ng et al.   BRITISH JOURNAL OF CANCER

HLA DR-DQ Haplotypes and Genotypes and Type 1 Diabetes Risk: Analysis of the Type 1 Diabetes Genetics Consortium Families

(2008) H. Erlich et al.   DIABETES

Clinicopathological and prognostic significance of mucin phenotype in gastric cancer

(2008) Kohei Wakatsuki et al.   JOURNAL OF SURGICAL ONCOLOGY

Functional Wnt Signaling Is Increased in Idiopathic Pulmonary Fibrosis

(2008) Melanie Königshoff et al.   PLoS One

Idiopathic Pulmonary Fibrosis: Aberrant Recapitulation of Developmental Programs?

(2008) Moisés Selman et al.   PLOS MEDICINE

MMP1 and MMP7 as Potential Peripheral Blood Biomarkers in Idiopathic Pulmonary Fibrosis

(2008) Ivan O Rosas et al.   PLOS MEDICINE

Structure and Function of the Polymeric Mucins in Airways Mucus

(2007) David J. Thornton et al.   Annual Review of Physiology

Is Metalloproteinase-7 Specific for Idiopathic Pulmonary Fibrosis?

(2007) Jin Won Huh et al.   CHEST