Pregnancy and delivery in a patient with a Fontan circulation and primary ciliary dyskinesia: A case report

A patient had primary ciliary dyskinesia with a complex cardiac malformation. As a child, she had benefited from a Fontan surgery to maintain a proper cardiac function. In such patients, whether it is safe to become pregnant is controversial. This case illustrates the possibility of carrying a pregnancy to term and providing a vaginal birth if a rigorous preconception consultation is performed to ensure care by a multidisciplinary specialized team, and the patient is properly informed of the risks. (C) 2021 Elsevier Masson SAS. All rights reserved.

Automated summary

This case demonstrates the possibility of successfully carrying a pregnancy to term and providing a vaginal birth for patients with primary ciliary dyskinesia and complex cardiac malformation, as long as rigorous preconception consultation and care by a multidisciplinary specialized team are ensured, and the patient is properly informed of the risks involved.