Increasing life expectancy in cystic fibrosis: Advances and challenges
Published 2021 View Full Article
- Home
- Publications
- Publication Search
- Publication Details
Title
Increasing life expectancy in cystic fibrosis: Advances and challenges
Authors
Keywords
-
Journal
PEDIATRIC PULMONOLOGY
Volume 57, Issue S1, Pages -
Publisher
Wiley
Online
2021-10-21
DOI
10.1002/ppul.25733
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- Cystic Fibrosis Patients of Minority Race and Ethnicity Less Likely Eligible for CFTR Modulators Based on CFTR Genotype
- (2021) Meghan E. McGarry et al. PEDIATRIC PULMONOLOGY
- Long-term safety and efficacy of tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study
- (2021) Patrick A Flume et al. Lancet Respiratory Medicine
- The Future of Highly Effective Modulator Therapy in Cystic Fibrosis
- (2021) Cori L. Daines et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Racially equitable diagnosis of cystic fibrosis using next-generation DNA sequencing: a case report
- (2021) Bennett O. V. Shum et al. BMC Pediatrics
- Normal pancreatic function and false-negative CF newborn screen in a child born to a mother taking CFTR modulator therapy during pregnancy
- (2021) Christopher N. Fortner et al. Journal of Cystic Fibrosis
- Outcomes of infants born during the first 9 years of CF newborn screening in the United States: A retrospective Cystic Fibrosis Foundation Patient Registry cohort study
- (2021) Stacey L. Martiniano et al. PEDIATRIC PULMONOLOGY
- Cystic fibrosis in the year 2020: A disease with a new face
- (2020) Kris De Boeck ACTA PAEDIATRICA
- Lung Transplantation for Cystic Fibrosis
- (2020) Jonathan C Yeung et al. JOURNAL OF HEART AND LUNG TRANSPLANTATION
- Restoration of exocrine pancreatic function in older children with cystic fibrosis on ivacaftor
- (2020) A.L. Nichols et al. Paediatric Respiratory Reviews
- The Impact of the CFTR Gene Discovery on Cystic Fibrosis Diagnosis, Counseling, and Preventive Therapy
- (2020) Philip M. Farrell et al. Genes
- The Changing Epidemiology of Cystic Fibrosis: Incidence, Survival and Impact of the CFTR Gene Discovery
- (2020) Virginie Scotet et al. Genes
- Impact of CFTR modulator use on outcomes in people with severe cystic fibrosis lung disease
- (2020) Michal Shteinberg et al. European Respiratory Review
- Persistent recovery of pancreatic function in patients with cystic fibrosis after ivacaftor
- (2020) Danielle Munce et al. PEDIATRIC PULMONOLOGY
- Noninvasive Ventilation in Cystic Fibrosis: Clinical Indications and Outcomes in a Large UK Adult Cystic Fibrosis Center
- (2020) Giulia Spoletini et al. Respiratory Care
- Real-World Safety of CFTR Modulators in the Treatment of Cystic Fibrosis: A Systematic Review
- (2020) Renée V. E. Dagenais et al. Journal of Clinical Medicine
- Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation
- (2020) J.S. Guimbellot et al. Journal of Cystic Fibrosis
- An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2–5 years (KLIMB)
- (2019) Margaret Rosenfeld et al. Journal of Cystic Fibrosis
- Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries
- (2019) Nataliya Volkova et al. Journal of Cystic Fibrosis
- Pregnancy outcome in women with cystic fibrosis and poor pulmonary function
- (2019) Quitterie Reynaud et al. Journal of Cystic Fibrosis
- Elexacaftor–Tezacaftor–Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele
- (2019) Peter G. Middleton et al. NEW ENGLAND JOURNAL OF MEDICINE
- Disparities in Mortality of Hispanic Cystic Fibrosis Patients in the United States: A National and Regional Cohort Study
- (2018) Jason Rho et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Liver disease in patients with cystic fibrosis
- (2018) Natasha Kamal et al. CURRENT OPINION IN GASTROENTEROLOGY
- Ivacaftor withdrawal syndrome in cystic fibrosis patients with the G551D mutation
- (2018) Aaron T. Trimble et al. Journal of Cystic Fibrosis
- Recovery of lung function following a pulmonary exacerbation in patients with cystic fibrosis and the G551D - CFTR mutation treated with ivacaftor
- (2018) Patrick A. Flume et al. Journal of Cystic Fibrosis
- Effects of a partially supervised conditioning programme in cystic fibrosis: an international multi-centre randomised controlled trial (ACTIVATE-CF): study protocol
- (2018) Helge Hebestreit et al. BMC Pulmonary Medicine
- Ivacaftor treatment of cystic fibrosis in children aged 12 to
- (2018) Margaret Rosenfeld et al. Lancet Respiratory Medicine
- Cystic Fibrosis Diagnostic Challenges over 4 Decades: Historical Perspectives and Lessons Learned
- (2017) Philip M. Farrell et al. JOURNAL OF PEDIATRICS
- Tezacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del
- (2017) Jennifer L. Taylor-Cousar et al. NEW ENGLAND JOURNAL OF MEDICINE
- Pulmonary function disparities exist and persist in Hispanic patients with cystic fibrosis: A longitudinal analysis
- (2017) Meghan E. McGarry et al. PEDIATRIC PULMONOLOGY
- Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study
- (2017) Michael W Konstan et al. Lancet Respiratory Medicine
- Critical illness among adults with cystic fibrosis in Texas, 2004–2013: Patterns of ICU utilization, characteristics, and outcomes
- (2017) Lavi Oud PLoS One
- Assessing Differences in Mortality Rates and Risk Factors Between Hispanic and Non-Hispanic Patients With Cystic Fibrosis in California
- (2016) MyMy C. Buu et al. CHEST
- Cystic fibrosis newborn screening programs: implications of the CFTR variant spectrum in nonwhite patients
- (2016) Lynn Pique et al. GENETICS IN MEDICINE
- The Spectrum of CFTR Variants in Nonwhite Cystic Fibrosis Patients
- (2016) Iris Schrijver et al. JOURNAL OF MOLECULAR DIAGNOSTICS
- Sustained Benefit from Ivacaftor Demonstrated by Combining Clinical Trial and Cystic Fibrosis Patient Registry Data
- (2015) Gregory S. Sawicki et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Improving newborn screening for cystic fibrosis using next-generation sequencing technology: a technical feasibility study
- (2015) Mei W. Baker et al. GENETICS IN MEDICINE
- Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
- (2015) Claire E. Wainwright et al. NEW ENGLAND JOURNAL OF MEDICINE
- US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis
- (2015) R Andres Floto et al. THORAX
- A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation
- (2011) Bonnie W. Ramsey et al. NEW ENGLAND JOURNAL OF MEDICINE
- Cystic Fibrosis Pulmonary Guidelines
- (2010) Patrick A. Flume et al. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE
- Association of Socioeconomic Status with the Use of Chronic Therapies and Healthcare Utilization in Children with Cystic Fibrosis
- (2009) Michael S. Schechter et al. JOURNAL OF PEDIATRICS
- Update on fat-soluble vitamins in cystic fibrosis
- (2008) Asim Maqbool et al. CURRENT OPINION IN PULMONARY MEDICINE
- Guidelines for Diagnosis of Cystic Fibrosis in Newborns through Older Adults: Cystic Fibrosis Foundation Consensus Report
- (2008) Philip M. Farrell et al. JOURNAL OF PEDIATRICS
Find Funding. Review Successful Grants.
Explore over 25,000 new funding opportunities and over 6,000,000 successful grants.
ExploreAdd your recorded webinar
Do you already have a recorded webinar? Grow your audience and get more views by easily listing your recording on Peeref.
Upload Now