In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder

Title
In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder
Authors
Keywords
Mitochondria, ROS, Propionic acidemia, OXPHOS, Reverse phase protein microarrays, Antioxidant, Oxidative damage, Mouse models, oxidative stress, MitoB, Lipid peroxidation, Inherited metabolic diseases
Journal
FREE RADICAL BIOLOGY AND MEDICINE
Volume 96, Issue -, Pages 1-12
Publisher
Elsevier BV
Online
2016-04-13
DOI
10.1016/j.freeradbiomed.2016.04.007

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