- Home
- Publications
- Publication Search
- Publication Details
Title
The Role of Skeletal Muscle in Amyotrophic Lateral Sclerosis
Authors
Keywords
-
Journal
BRAIN PATHOLOGY
Volume 26, Issue 2, Pages 227-236
Publisher
Wiley
Online
2016-01-19
DOI
10.1111/bpa.12350
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- A metabolic switch toward lipid use in glycolytic muscle is an early pathologic event in a mouse model of amyotrophic lateral sclerosis
- (2015) L. Palamiuc et al. EMBO Molecular Medicine
- Tweak regulates astrogliosis, microgliosis and skeletal muscle atrophy in a mouse model of amyotrophic lateral sclerosis
- (2015) M. Bowerman et al. HUMAN MOLECULAR GENETICS
- ALS-Linked P56S-VAPB Mutation Impairs the Formation of Multinuclear Myotube in C2C12 Cells
- (2015) Yukako Tokutake et al. INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES
- Glycoprotein nonmetastatic melanoma protein B ameliorates skeletal muscle lesions in a SOD1G93Amouse model of amyotrophic lateral sclerosis
- (2015) Yuki Nagahara et al. JOURNAL OF NEUROSCIENCE RESEARCH
- Early ALS-type gait abnormalities in AMP-dependent protein kinase-deficient mice suggest a role for this metabolic sensor in early stages of the disease
- (2015) Maxime Vergouts et al. METABOLIC BRAIN DISEASE
- Activation of the endoplasmic reticulum stress response in skeletal muscle of G93A*SOD1 amyotrophic lateral sclerosis mice
- (2015) Dapeng Chen et al. Frontiers in Cellular Neuroscience
- VCP-dependent muscle degeneration is linked to defects in a dynamic tubular lysosomal network in vivo
- (2015) Alyssa E Johnson et al. eLife
- Motoneuronal and muscle-selective removal of ALS-related misfolded proteins: Figure 1
- (2015) Valeria Crippa et al. BIOCHEMICAL SOCIETY TRANSACTIONS
- Time-Point Dependent Activation of Autophagy and the UPS in SOD1G93A Mice Skeletal Muscle
- (2015) Sara Oliván et al. PLoS One
- Perturbations in intracellular Ca2+ handling in skeletal muscle in the G93A*SOD1 mouse model of amyotrophic lateral sclerosis
- (2014) Eva R. Chin et al. AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY
- Neuronal cells but not muscle cells are resistant to oxidative stress mediated protein misfolding and cell death: Role of molecular chaperones
- (2014) Arunabh Bhattacharya et al. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
- Early Gene Expression Changes in Skeletal Muscle from SOD1G93A Amyotrophic Lateral Sclerosis Animal Model
- (2014) Gabriela P. de Oliveira et al. CELLULAR AND MOLECULAR NEUROBIOLOGY
- Changes in skeletal muscle iron metabolism outpace amyotrophic lateral sclerosis onset in transgenic rats bearing the G93A hmSOD1 gene mutation
- (2014) M. Halon et al. FREE RADICAL RESEARCH
- Extra virgin olive oil intake delays the development of amyotrophic lateral sclerosis associated with reduced reticulum stress and autophagy in muscle of SOD1G93A mice
- (2014) Sara Oliván et al. JOURNAL OF NUTRITIONAL BIOCHEMISTRY
- Skeletal muscle oxidative capacity in amyotrophic lateral sclerosis
- (2014) Terence E. Ryan et al. MUSCLE & NERVE
- Muscle Expression of Mutant Androgen Receptor Accounts for Systemic and Motor Neuron Disease Phenotypes in Spinal and Bulbar Muscular Atrophy
- (2014) Constanza J. Cortes et al. NEURON
- MicroRNA-206: A Potential Circulating Biomarker Candidate for Amyotrophic Lateral Sclerosis
- (2014) Janne M. Toivonen et al. PLoS One
- The Role of Muscle microRNAs in Repairing the Neuromuscular Junction
- (2014) Gregorio Valdez et al. PLoS One
- Fast Skeletal Muscle Troponin Activator tirasemtiv Increases Muscle Function and Performance in the B6SJL-SOD1G93A ALS Mouse Model
- (2014) Darren T. Hwee et al. PLoS One
- Skeletal Muscle Satellite Cells in Amyotrophic Lateral Sclerosis
- (2014) Annarita Scaramozza et al. ULTRASTRUCTURAL PATHOLOGY
- ALS as a distal axonopathy: molecular mechanisms affecting neuromuscular junction stability in the presymptomatic stages of the disease
- (2014) Elizabeth B. Moloney et al. Frontiers in Neuroscience
- Mitochondrial abnormalities and low grade inflammation are present in the skeletal muscle of a minority of patients with amyotrophic lateral sclerosis; an observational myopathology study
- (2014) Safa Al-Sarraj et al. Acta Neuropathologica Communications
- Protein aggregation in amyotrophic lateral sclerosis
- (2013) Anna M. Blokhuis et al. ACTA NEUROPATHOLOGICA
- Differential effects of mutant SOD1 on protein structure of skeletal muscle and spinal cord of familial amyotrophic lateral sclerosis: Role of chaperone network
- (2013) Rochelle Wei et al. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
- Muscle histone deacetylase 4 upregulation in amyotrophic lateral sclerosis: potential role in reinnervation ability and disease progression
- (2013) Gaëlle Bruneteau et al. BRAIN
- Axonal degeneration in the peripheral nervous system: Implications for the pathogenesis of amyotrophic lateral sclerosis
- (2013) Lindsey R. Fischer-Hayes et al. EXPERIMENTAL NEUROLOGY
- Synergistic Effects of GDNF and VEGF on Lifespan and Disease Progression in a Familial ALS Rat Model
- (2013) Dan Krakora et al. MOLECULAR THERAPY
- State of play in amyotrophic lateral sclerosis genetics
- (2013) Alan E Renton et al. NATURE NEUROSCIENCE
- Converging Mechanisms in ALS and FTD: Disrupted RNA and Protein Homeostasis
- (2013) Shuo-Chien Ling et al. NEURON
- Spinal inhibitory circuits and their role in motor neuron degeneration
- (2013) Uri Nimrod Ramírez-Jarquín et al. NEUROPHARMACOLOGY
- Absence of Nrf2 or Its Selective Overexpression in Neurons and Muscle Does Not Affect Survival in ALS-Linked Mutant hSOD1 Mouse Models
- (2013) Marcelo R. Vargas et al. PLoS One
- Systemic Down-Regulation of Delta-9 Desaturase Promotes Muscle Oxidative Metabolism and Accelerates Muscle Function Recovery following Nerve Injury
- (2013) Ghulam Hussain et al. PLoS One
- Early Changes of Neuromuscular Transmission in the SOD1(G93A) Mice Model of ALS Start Long before Motor Symptoms Onset
- (2013) Mariana C. Rocha et al. PLoS One
- TDP-43, an ALS Linked Protein, Regulates Fat Deposition and Glucose Homeostasis
- (2013) Nancy R. Stallings et al. PLoS One
- Defective Mitochondrial Dynamics Is an Early Event in Skeletal Muscle of an Amyotrophic Lateral Sclerosis Mouse Model
- (2013) Guo Luo et al. PLoS One
- Bone Marrow Transplantation in Hindlimb Muscles of Motoneuron Degenerative Mice Reduces Neuronal Death and Improves Motor Function
- (2013) Diego Pastor et al. STEM CELLS AND DEVELOPMENT
- Differential autophagy power in the spinal cord and muscle of transgenic ALS mice
- (2013) Valeria Crippa et al. Frontiers in Cellular Neuroscience
- Postnatal muscle modification by myogenic factors modulates neuropathology and survival in an ALS mouse model
- (2013) Kevin H. J. Park et al. Nature Communications
- VAPB/ALS8 MSP Ligands Regulate Striated Muscle Energy Metabolism Critical for Adult Survival in Caenorhabditis elegans
- (2013) Sung Min Han et al. PLoS Genetics
- Safety, tolerability and pharmacodynamics of a skeletal muscle activator in amyotrophic lateral sclerosis
- (2012) Jeremy Shefner et al. Amyotrophic Lateral Sclerosis
- The molecular basis of the frontotemporal lobar degeneration–amyotrophic lateral sclerosis spectrum
- (2012) Tim van Langenhove et al. ANNALS OF MEDICINE
- Molecular Signatures of Amyotrophic Lateral Sclerosis Disease Progression in Hind and Forelimb Muscles of an SOD1G93A Mouse Model
- (2012) Daniele Capitanio et al. ANTIOXIDANTS & REDOX SIGNALING
- Protein misfolding, mitochondrial dysfunction and muscle loss are not directly dependent on soluble and aggregation state of mSOD1 protein in skeletal muscle of ALS
- (2012) Rochelle Wei et al. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
- Degeneration of serotonergic neurons in amyotrophic lateral sclerosis: a link to spasticity
- (2012) Christel Dentel et al. BRAIN
- Elevated PGC-1α Activity Sustains Mitochondrial Biogenesis and Muscle Function without Extending Survival in a Mouse Model of Inherited ALS
- (2012) Sandrine Da Cruz et al. Cell Metabolism
- Amyotrophic Lateral Sclerosis and Excitotoxicity: From Pathological Mechanism to Therapeutic Target
- (2012) E. Bogaert et al. CNS & Neurological Disorders-Drug Targets
- Decreased mRNA Expression of PGC-1α and PGC-1α-Regulated Factors in the SOD1G93AALS Mouse Model and in Human Sporadic ALS
- (2012) Nadine Thau et al. JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY
- Analysis of neuromuscular junctions and effects of anabolic steroid administration in the SOD1G93A mouse model of ALS
- (2012) Valentina Cappello et al. MOLECULAR AND CELLULAR NEUROSCIENCE
- Alterations of signaling pathways in muscle tissues of patients with amyotrophic lateral sclerosis
- (2012) Fei Yin et al. MUSCLE & NERVE
- Disruption of skeletal muscle mitochondrial network genes and miRNAs in amyotrophic lateral sclerosis
- (2012) Aaron P. Russell et al. NEUROBIOLOGY OF DISEASE
- Altered in vitro Proliferation of Mouse SOD1-G93A Skeletal Muscle Satellite Cells
- (2012) Raquel Manzano et al. Neurodegenerative Diseases
- Dihydrotestosterone Ameliorates Degeneration in Muscle, Axons and Motoneurons and Improves Motor Function in Amyotrophic Lateral Sclerosis Model Mice
- (2012) Young-Eun Yoo et al. PLoS One
- Mitochondrial genome aberrations in skeletal muscle of patients with motor neuron disease
- (2012) Lucia Artuso et al. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
- Intramuscular administration of a VEGF zinc finger transcription factor activator (VEGF-ZFP-TF) improves functional outcomes in SOD1 rats
- (2011) Michele A. Kliem et al. Amyotrophic Lateral Sclerosis
- Abnormalities of satellite cells function in amyotrophic lateral sclerosis
- (2011) Pierre-François Pradat et al. Amyotrophic Lateral Sclerosis
- Proteomic analysis of muscle affected by motor neuron degeneration: The wobbler mouse model of amyotrophic lateral sclerosis
- (2011) Lisa Staunton et al. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
- Hind limb muscle atrophy precedes cerebral neuronal degeneration in G93A-SOD1 mouse model of amyotrophic lateral sclerosis: A longitudinal MRI study
- (2011) Stefania Marcuzzo et al. EXPERIMENTAL NEUROLOGY
- Amyotrophic lateral sclerosis
- (2011) Matthew C Kiernan et al. LANCET
- Neuroinflammation in amyotrophic lateral sclerosis: role of glial activation in motor neuron disease
- (2011) Thomas Philips et al. LANCET NEUROLOGY
- Impaired expression of insulin-like growth factor-1 system in skeletal muscle of amyotrophic lateral sclerosis patients
- (2011) Christian Lunetta et al. MUSCLE & NERVE
- Altered Expression of Myogenic Regulatory Factors in the Mouse Model of Amyotrophic Lateral Sclerosis
- (2011) Raquel Manzano et al. Neurodegenerative Diseases
- Expanded GGGGCC Hexanucleotide Repeat in Noncoding Region of C9ORF72 Causes Chromosome 9p-Linked FTD and ALS
- (2011) Mariely DeJesus-Hernandez et al. NEURON
- The anabolic/androgenic steroid nandrolone exacerbates gene expression modifications induced by mutant SOD1 in muscles of mice models of amyotrophic lateral sclerosis
- (2011) Mariarita Galbiati et al. PHARMACOLOGICAL RESEARCH
- Physiological characterization of human muscle acetylcholine receptors from ALS patients
- (2011) E. Palma et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Mitochondrial dysfunction in ALS
- (2011) Mauro Cozzolino et al. PROGRESS IN NEUROBIOLOGY
- Muscle atrophy induced by SOD1G93A expression does not involve the activation of caspase in the absence of denervation
- (2011) Gabriella Dobrowolny et al. Skeletal Muscle
- Investigation of MGF mRNA expression in patients with amyotrophic lateral sclerosis using parallel in vivo and in vitro approaches
- (2010) Richard M. Evans et al. Amyotrophic Lateral Sclerosis
- Mitochondrial Respiratory Chain Dysfunction in Muscle From Patients With Amyotrophic Lateral Sclerosis
- (2010) Veronica Crugnola et al. ARCHIVES OF NEUROLOGY
- Oxidative stress in skeletal muscle stimulates early expression of Rad in a mouse model of amyotrophic lateral sclerosis
- (2010) Benoît Halter et al. FREE RADICAL BIOLOGY AND MEDICINE
- Skeletal muscle-restricted expression of human SOD1 causes motor neuron degeneration in transgenic mice
- (2010) Margaret Wong et al. HUMAN MOLECULAR GENETICS
- Neuronal NOS is dislocated during muscle atrophy in amyotrophic lateral sclerosis
- (2010) Naoki Suzuki et al. JOURNAL OF THE NEUROLOGICAL SCIENCES
- Astrogliosis in amyotrophic lateral sclerosis: Role and therapeutic potential of astrocytes
- (2010) Marcelo R. Vargas et al. Neurotherapeutics
- A soluble activin type IIB receptor improves function in a mouse model of amyotrophic lateral sclerosis
- (2009) Brett M. Morrison et al. EXPERIMENTAL NEUROLOGY
- Oxidative stress in ALS: Key role in motor neuron injury and therapeutic target
- (2009) Siân C. Barber et al. FREE RADICAL BIOLOGY AND MEDICINE
- Hyperactive Intracellular Calcium Signaling Associated with Localized Mitochondrial Defects in Skeletal Muscle of an Animal Model of Amyotrophic Lateral Sclerosis
- (2009) Jingsong Zhou et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Progressive motor unit loss in the G93A mouse model of amyotrophic lateral sclerosis is unaffected by gender
- (2009) J. Hegedus et al. MUSCLE & NERVE
- Functional over-load saves motor units in the SOD1-G93A transgenic mouse model of amyotrophic lateral sclerosis
- (2009) T. Gordon et al. NEUROBIOLOGY OF DISEASE
- Muscle Mitochondrial Uncoupling Dismantles Neuromuscular Junction and Triggers Distal Degeneration of Motor Neurons
- (2009) Luc Dupuis et al. PLoS One
- MicroRNA-206 Delays ALS Progression and Promotes Regeneration of Neuromuscular Synapses in Mice
- (2009) A. H. Williams et al. SCIENCE
- Mutations in the FUS/TLS Gene on Chromosome 16 Cause Familial Amyotrophic Lateral Sclerosis
- (2009) T. J. Kwiatkowski et al. SCIENCE
- Presymptomatic biochemical changes in hindlimb muscle of G93A human Cu/Zn superoxide dismutase 1 transgenic mouse model of amyotrophic lateral sclerosis
- (2008) Kevin H.J. Park et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE
- Skeletal Muscle Is a Primary Target of SOD1G93A-Mediated Toxicity
- (2008) Gabriella Dobrowolny et al. Cell Metabolism
- Mechano-growth factor, an IGF-I splice variant, rescues motoneurons and improves muscle function in SOD1G93A mice
- (2008) Joanna Riddoch-Contreras et al. EXPERIMENTAL NEUROLOGY
- The deacetylase HDAC4 controls myocyte enhancing factor-2-dependent structural gene expression in response to neural activity
- (2008) Todd J. Cohen et al. FASEB JOURNAL
- Direct Muscle Delivery of GDNF With Human Mesenchymal Stem Cells Improves Motor Neuron Survival and Function in a Rat Model of Familial ALS
- (2008) Masatoshi Suzuki et al. MOLECULAR THERAPY
- Local expression of mIgf-1 modulates ubiquitin, caspase and CDK5 expression in skeletal muscle of an ALS mouse model
- (2008) Gabriella Dobrowolny et al. NEUROLOGICAL RESEARCH
- TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis
- (2008) J. Sreedharan et al. SCIENCE
Find Funding. Review Successful Grants.
Explore over 25,000 new funding opportunities and over 6,000,000 successful grants.
ExploreBecome a Peeref-certified reviewer
The Peeref Institute provides free reviewer training that teaches the core competencies of the academic peer review process.
Get Started