Novel behavioural characteristics of the superoxide dismutase 1 G93A ( SOD1 G93A ) mouse model of amyotrophic lateral sclerosis include sex‐dependent phenotypes

The metastability of the proteome of spinal motor neurons underlies their selective vulnerability in ALS

(2019) Justin J. Yerbury et al.   NEUROSCIENCE LETTERS

Schizophrenia-relevant behaviours of female mice overexpressing neuregulin 1 type III

(2018) Juan C Olaya et al.   BEHAVIOURAL BRAIN RESEARCH

Sex specific activation of the ERα axis of the mitochondrial UPR (UPRmt) in the G93A-SOD1 mouse model of familial ALS

(2017) Amanjot K Riar et al.   HUMAN MOLECULAR GENETICS

Apathy and its impact on patient outcome in amyotrophic lateral sclerosis

(2017) J. Caga et al.   JOURNAL OF NEUROLOGY

Spinal motor neuron protein supersaturation patterns are associated with inclusion body formation in ALS

(2017) Prajwal Ciryam et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Amyotrophic lateral sclerosis - frontotemporal spectrum disorder (ALS-FTSD): Revised diagnostic criteria

(2017) Michael J. Strong et al.   Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration

Mutant Tau knock-in mice display frontotemporal dementia relevant behaviour and histopathology

(2016) David J. Koss et al.   NEUROBIOLOGY OF DISEASE

Increased anxiety-like behavior and selective learning impairments are concomitant to loss of hippocampal interneurons in the presymptomatic SOD1(G93A) ALS mouse model

(2015) Eros Quarta et al.   JOURNAL OF COMPARATIVE NEUROLOGY

Multidimensional apathy in ALS: validation of the Dimensional Apathy Scale

(2015) Ratko Radakovic et al.   JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY

Basal ganglia pathology in ALS is associated with neuropsychological deficits

(2015) Judith Machts et al.   NEUROLOGY

Novel behavioural characteristics of female APPSwe/PS1ΔE9 double transgenic mice

(2013) David Cheng et al.   BEHAVIOURAL BRAIN RESEARCH

Homologous involvement of striatum and prefrontal cortex in rodent and human water maze learning

(2013) D. G. Woolley et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Motor neuron dysfunction in a mouse model of ALS: Gender-dependent effect of P2X7 antagonism

(2013) Chiara Cervetto et al.   TOXICOLOGY

Deactivation of the parvalbumin-positive interneurons in the hippocampus after fear-like behaviour following electrical stimulation of the dorsolateral periaqueductal gray of rats

(2012) Yasin Temel et al.   BEHAVIOURAL BRAIN RESEARCH

Modulation of Astrocytic Mitochondrial Function by Dichloroacetate Improves Survival and Motor Performance in Inherited Amyotrophic Lateral Sclerosis

(2012) Ernesto Miquel et al.   PLoS One

Mesial Prefrontal Cortex Degeneration in Amyotrophic Lateral Sclerosis: A High-Field Proton MR Spectroscopy Study

(2011) U. Usman et al.   AMERICAN JOURNAL OF NEURORADIOLOGY

A comprehensive assessment of the SOD1G93A low-copy transgenic mouse, which models human amyotrophic lateral sclerosis

(2011) A. Acevedo-Arozena et al.   Disease Models & Mechanisms

Expanded GGGGCC Hexanucleotide Repeat in Noncoding Region of C9ORF72 Causes Chromosome 9p-Linked FTD and ALS

(2011) Mariely DeJesus-Hernandez et al.   NEURON

Gender-Specific Mechanism of Synaptic Impairment and Its Prevention by GCSF in a Mouse Model of ALS

(2011) Nikolay Naumenko et al.   Frontiers in Cellular Neuroscience

Degeneration of the Mid-Cingulate Cortex in Amyotrophic Lateral Sclerosis Detected In Vivo with MR Spectroscopy

(2010) N. Sudharshan et al.   AMERICAN JOURNAL OF NEURORADIOLOGY

Evaluating spatial memory function in mice: A within-subjects comparison between the water maze test and its adaptation to dry land

(2010) L. Llano Lopez et al.   BEHAVIOURAL BRAIN RESEARCH

Effects of gender in amyotrophic lateral sclerosis

(2010) Pamela A. McCombe et al.   Gender Medicine

The human G93A SOD1 phenotype closely resembles sporadic amyotrophic lateral sclerosis

(2010) M. Synofzik et al.   JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY

Intermediate- and long-term recognition memory deficits in Tg2576 mice are reversed with acute calcineurin inhibition

(2009) Giulio Taglialatela et al.   BEHAVIOURAL BRAIN RESEARCH

Oxidative stress in ALS: Key role in motor neuron injury and therapeutic target

(2009) Siân C. Barber et al.   FREE RADICAL BIOLOGY AND MEDICINE

Abnormal social behavior, hyperactivity, impaired remote spatial memory, and increased D1-mediated dopaminergic signaling in neuronal nitric oxide synthase knockout mice

(2009) Koichi Tanda et al.   Molecular Brain

Progression of hippocampal degeneration in amyotrophic lateral sclerosis with or without memory impairment: distinction from Alzheimer disease

(2008) Takahiro Takeda et al.   ACTA NEUROPATHOLOGICA

Dopamine Signaling in the Dorsal Striatum Is Essential for Motivated Behaviors

(2008) Richard D. Palmiter   Annals of the New York Academy of Sciences

Anxiety undermines quality of life in ALS patients and caregivers

(2008) A. Vignola et al.   EUROPEAN JOURNAL OF NEUROLOGY

Sex-specific behavioural effects of environmental enrichment in a transgenic mouse model of amyotrophic lateral sclerosis

(2008) Nathan C. Stam et al.   EUROPEAN JOURNAL OF NEUROSCIENCE

Abnormal medial prefrontal cortex connectivity and defective fear extinction in the presymptomatic G93A SOD1 mouse model of ALS

(2008) C. Sgobio et al.   GENES BRAIN AND BEHAVIOR

Increased social interaction in mice deficient of the striatal medium spiny neuron-specific phosphodiesterase 10A2

(2008) Hiromi Sano et al.   JOURNAL OF NEUROCHEMISTRY

Variation in Mouse Basolateral Amygdala Volume is Associated With Differences in Stress Reactivity and Fear Learning

(2008) Rebecca J Yang et al.   NEUROPSYCHOPHARMACOLOGY

Transgenics, toxicity and therapeutics in rodent models of mutant SOD1-mediated familial ALS

(2008) B TURNER et al.   PROGRESS IN NEUROBIOLOGY

Protein Aggregation and Protein Instability Govern Familial Amyotrophic Lateral Sclerosis Patient Survival

(2008) Qi Wang et al.   PLOS BIOLOGY

Effects of estrogen on lifespan and motor functions in female hSOD1 G93A transgenic mice

(2007) Chan-Il Choi et al.   JOURNAL OF THE NEUROLOGICAL SCIENCES