Journal
ASIAN JOURNAL OF SURGERY
Volume 39, Issue 3, Pages 187-190Publisher
ELSEVIER SINGAPORE PTE LTD
DOI: 10.1016/j.asjsur.2012.11.003
Keywords
adrenalectomy; adrenal tumor; malignant peripheral nerve sheath tumor; pheochromocytoma; spontaneous rupture
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Funding
- Grants-in-Aid for Scientific Research [24116506, 24390239] Funding Source: KAKEN
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Adrenal tumors with more than one cellular component are uncommon. Furthermore, an adrenal tumor composed of a pheochromocytoma and a malignant peripheral nerve sheath tumor is extremely rare. A composite pheochromocytoma with malignant peripheral nerve sheath tumor in a 42-year-old man is reported here. After adequate preoperative control, left adrenalectomy was performed simultaneously with resection of the ipsilateral kidney for spontaneous rupture of the left adrenal tumor. Pathological findings demonstrated pheochromocytoma and malignant peripheral nerve sheath tumor in a ruptured adrenal tumor. To date, there have been only four reported cases of composite pheochromocytoma with malignant peripheral nerve sheath tumor, so the present case is only the fifth case in the world. Despite. the very poor prognosis of patients with pheochromocytoma and malignant peripheral nerve sheath tumors reported in the literature, the patient remains well without evidence of recurrence or new metastatic lesions at 36 months postoperatively. Copyright (C) 2012, Asian Surgical Association. Published by Elsevier Taiwan LLC.
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