Neuronal Redox-Imbalance in Rett Syndrome Affects Mitochondria as Well as Cytosol, and Is Accompanied by Intensified Mitochondrial O2 Consumption and ROS Release

Disturbed redox homeostasis and oxidative stress: Potential players in the developmental regression in Rett syndrome

(2019) Michael Müller   NEUROSCIENCE AND BIOBEHAVIORAL REVIEWS

Stimulation of the brain serotonin receptor 7 rescues mitochondrial dysfunction in female mice from two models of Rett syndrome

(2017) Daniela Valenti et al.   NEUROPHARMACOLOGY

Increased Mitochondrial Mass and Cytosolic Redox Imbalance in Hippocampal Astrocytes of a Mouse Model of Rett Syndrome: Subcellular Changes Revealed by Ratiometric Imaging of JC-1 and roGFP1 Fluorescence

(2017) Dörthe F. Bebensee et al.   Oxidative Medicine and Cellular Longevity

Mitochondrial Dysfunction in the Pathogenesis of Rett Syndrome: Implications for Mitochondria-Targeted Therapies

(2017) Natalya Shulyakova et al.   Frontiers in Cellular Neuroscience

Redox Indicator Mice Stably Expressing Genetically Encoded Neuronal roGFP: Versatile Tools to Decipher Subcellular Redox Dynamics in Neuropathophysiology

(2016) Kerstin C. Wagener et al.   ANTIOXIDANTS & REDOX SIGNALING

Structure of Mammalian Respiratory Supercomplex I 1 III 2 IV 1

(2016) Meng Wu et al.   CELL

Cooperation between COA6 and SCO2 in COX2 Maturation during Cytochrome c Oxidase Assembly Links Two Mitochondrial Cardiomyopathies

(2015) David Pacheu-Grau et al.   Cell Metabolism

Cardiac-specific succinate dehydrogenase deficiency in Barth syndrome

(2015) J. Dudek et al.   EMBO Molecular Medicine

Mitochondrial free radical overproduction due to respiratory chain impairment in the brain of a mouse model of Rett syndrome: protective effect of CNF1

(2015) Bianca De Filippis et al.   FREE RADICAL BIOLOGY AND MEDICINE

Mitochondrial dysfunction in a transgenic mouse model expressing human amyloid precursor protein (APP) with the Arctic mutation

(2015) Annica Rönnbäck et al.   JOURNAL OF NEUROCHEMISTRY

Dysregulation of Glutamine Transporter SNAT1 in Rett Syndrome Microglia: A Mechanism for Mitochondrial Dysfunction and Neurotoxicity

(2015) L.-W. Jin et al.   JOURNAL OF NEUROSCIENCE

Aberrant redox homoeostasis and mitochondrial dysfunction in Rett syndrome: Figure 1

(2014) Michael Müller et al.   BIOCHEMICAL SOCIETY TRANSACTIONS

Mitochondrial dysfunction in the skeletal muscle of a mouse model of Rett syndrome (RTT): Implications for the disease phenotype

(2014) W.A. Gold et al.   MITOCHONDRION

Metabolic differences in hippocampal ‘Rett’ neurons revealed by ATP imaging

(2014) J. Toloe et al.   MOLECULAR AND CELLULAR NEUROSCIENCE

Oxidative brain damage in Mecp2-mutant murine models of Rett syndrome

(2014) Claudio De Felice et al.   NEUROBIOLOGY OF DISEASE

Mitochondrial dysfunction as a central actor in intellectual disability-related diseases: An overview of Down syndrome, autism, Fragile X and Rett syndrome

(2014) Daniela Valenti et al.   NEUROSCIENCE AND BIOBEHAVIORAL REVIEWS

Anaplerotic Triheptanoin Diet Enhances Mitochondrial Substrate Use to Remodel the Metabolome and Improve Lifespan, Motor Function, and Sociability in MeCP2-Null Mice

(2014) Min Jung Park et al.   PLoS One

Differential effects of complex II on mitochondrial ROS production and their relation to cardioprotective pre- and postconditioning

(2013) Stefan Dröse   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Global Transcriptional and Translational Repression in Human-Embryonic-Stem-Cell-Derived Rett Syndrome Neurons

(2013) Yun Li et al.   Cell Stem Cell

Genes Related to Mitochondrial Functions, Protein Degradation, and Chromatin Folding Are Differentially Expressed in Lymphomonocytes of Rett Syndrome Patients

(2013) Alessandra Pecorelli et al.   MEDIATORS OF INFLAMMATION

The role of oxidative stress in Rett syndrome: an overview

(2012) Claudio De Felice et al.   Annals of the New York Academy of Sciences

Identification of a Protein Mediating Respiratory Supercomplex Stability

(2012) Yu-Chan Chen et al.   Cell Metabolism

Rcf1 Mediates Cytochrome Oxidase Assembly and Respirasome Formation, Revealing Heterogeneity of the Enzyme Complex

(2012) Milena Vukotic et al.   Cell Metabolism

Oxidative burden and mitochondrial dysfunction in a mouse model of Rett syndrome

(2012) Emanuel Großer et al.   NEUROBIOLOGY OF DISEASE

Measuring reactive oxygen and nitrogen species with fluorescent probes: challenges and limitations

(2011) Balaraman Kalyanaraman et al.   FREE RADICAL BIOLOGY AND MEDICINE

Mitochondrial dysfunction in autism spectrum disorders: a systematic review and meta-analysis

(2011) D A Rossignol et al.   MOLECULAR PSYCHIATRY

Fluorescent Protein-Based Redox Probes

(2010) Andreas J. Meyer et al.   ANTIOXIDANTS & REDOX SIGNALING

Membrane potential-related effect of calcium on reactive oxygen species generation in isolated brain mitochondria

(2010) Zsofia Komary et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Downstream targets of methyl CpG binding protein 2 and their abnormal expression in the frontal cortex of the human Rett syndrome brain

(2010) Joanne H Gibson et al.   BMC NEUROSCIENCE

The sites and topology of mitochondrial superoxide production

(2010) Martin D. Brand   EXPERIMENTAL GERONTOLOGY

Quantitative reactivity profiling predicts functional cysteines in proteomes

(2010) Eranthie Weerapana et al.   NATURE

Dynamic, semi-quantitative imaging of intracellular ROS levels and redox status in rat hippocampal neurons

(2010) Frank Funke et al.   NEUROIMAGE

Hypoxia Triggers Subcellular Compartmental Redox Signaling in Vascular Smooth Muscle Cells

(2009) Gregory B. Waypa et al.   CIRCULATION RESEARCH

Systemic oxidative stress in classic Rett syndrome

(2009) Claudio De Felice et al.   FREE RADICAL BIOLOGY AND MEDICINE

Widespread changes in dendritic and axonal morphology inMecp2-mutant mouse models of rett syndrome: Evidence for disruption of neuronal networks

(2009) Pavel V. Belichenko et al.   JOURNAL OF COMPARATIVE NEUROLOGY

Enhanced Hypoxia Susceptibility in Hippocampal Slices From a Mouse Model of Rett Syndrome

(2008) Marc Fischer et al.   JOURNAL OF NEUROPHYSIOLOGY

ΔΨm-Dependent and -independent production of reactive oxygen species by rat brain mitochondria

(2003) Tatyana V. Votyakova et al.   JOURNAL OF NEUROCHEMISTRY