Hearing Dysfunction in a Large Family Affected by Dominant Optic Atrophy (OPA8-Related DOA): A Human Model of Hidden Auditory Neuropathy
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Title
Hearing Dysfunction in a Large Family Affected by Dominant Optic Atrophy (OPA8-Related DOA): A Human Model of Hidden Auditory Neuropathy
Authors
Keywords
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Journal
Frontiers in Neuroscience
Volume 13, Issue -, Pages -
Publisher
Frontiers Media SA
Online
2019-05-28
DOI
10.3389/fnins.2019.00501
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- Synaptopathy in the aging cochlea: Characterizing early-neural deficits in auditory temporal envelope processing
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- Cochlear synaptopathy in acquired sensorineural hearing loss: Manifestations and mechanisms
- (2017) M. Charles Liberman et al. HEARING RESEARCH
- Inner Hair Cell Loss Disrupts Hearing and Cochlear Function Leading to Sensory Deprivation and Enhanced Central Auditory Gain
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- A neurodegenerative perspective on mitochondrial optic neuropathies
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- (2011) Valerio Carelli et al. HUMAN MOLECULAR GENETICS
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- (2010) Patrick Yu-Wai-Man et al. PROGRESS IN RETINAL AND EYE RESEARCH
- Mutation of OPA1 gene causes deafness by affecting function of auditory nerve terminals
- (2009) Taosheng Huang et al. BRAIN RESEARCH
- Neural and receptor cochlear potentials obtained by transtympanic electrocochleography in auditory neuropathy
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