Pulmonary arterial hypertension in connective tissue disorders: Pathophysiology and treatment

Pulmonary arterial hypertension in the setting of scleroderma is different than in the setting of lupus: A review

(2018) Isabel S. Bazan et al.   RESPIRATORY MEDICINE

Inflammatory Mediators Drive Adverse Right Ventricular Remodeling and Dysfunction and Serve as Potential Biomarkers

(2018) Akylbek Sydykov et al.   Frontiers in Physiology

Pulmonary arterial hypertension associated with connective tissue diseases: A review focusing on distinctive clinical aspects

(2017) Masaru Kato et al.   EUROPEAN JOURNAL OF CLINICAL INVESTIGATION

RESPITE: switching to riociguat in pulmonary arterial hypertension patients with inadequate response to phosphodiesterase-5 inhibitors

(2017) Marius M. Hoeper et al.   EUROPEAN RESPIRATORY JOURNAL

Selexipag for the treatment of connective tissue disease-associated pulmonary arterial hypertension

(2017) Sean Gaine et al.   EUROPEAN RESPIRATORY JOURNAL

A simple echocardiographic score for the diagnosis of pulmonary vascular disease in heart failure

(2017) Michele D’Alto et al.   Journal of Cardiovascular Medicine

Consensus best practice pathway of the UK Systemic Sclerosis Study group: management of cardiac disease in systemic sclerosis

(2017) Lesley-Anne Bissell et al.   RHEUMATOLOGY

Riociguat for the treatment of pulmonary arterial hypertension associated with connective tissue disease: results from PATENT-1 and PATENT-2

(2016) Marc Humbert et al.   ANNALS OF THE RHEUMATIC DISEASES

Initial combination therapy with ambrisentan and tadalafil in connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH): subgroup analysis from the AMBITION trial

(2016) John Gerry Coghlan et al.   ANNALS OF THE RHEUMATIC DISEASES

Vascular effects of sildenafil in patients with pulmonary fibrosis and pulmonary hypertension: anex vivo/in vitrostudy

(2016) Javier Milara et al.   EUROPEAN RESPIRATORY JOURNAL

Sildenafil for pulmonary hypertension complicating idiopathic pulmonary fibrosis: a rationale grounded in basic science

(2016) Paul M. Hassoun et al.   EUROPEAN RESPIRATORY JOURNAL

Pulmonary arterial hypertension in idiopathic inflammatory myopathies

(2016) Sébastien Sanges et al.   MEDICINE

Baseline Characteristics and Risk Factors of Pulmonary Arterial Hypertension in Systemic Lupus Erythematosus Patients

(2016) Can Huang et al.   MEDICINE

Ambrisentan response in connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH) – A subgroup analysis of the ARIES-E clinical trial

(2016) Aryeh Fischer et al.   RESPIRATORY MEDICINE

Multicentre randomised placebo-controlled trial of oral anticoagulation with apixaban in systemic sclerosis-related pulmonary arterial hypertension: the SPHInX study protocol

(2016) Alicia Calderone et al.   BMJ Open

Ambrisentan and Tadalafil Up-front Combination Therapy in Scleroderma-associated Pulmonary Arterial Hypertension

(2015) Paul M. Hassoun et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Effect of Warfarin Treatment on Survival of Patients With Pulmonary Arterial Hypertension (PAH) in the Registry to Evaluate Early and Long-Term PAH Disease Management (REVEAL)CLINICAL PERSPECTIVE

(2015) Ioana R. Preston et al.   CIRCULATION

2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension

(2015) Nazzareno Galiè et al.   EUROPEAN HEART JOURNAL

Bosentan added to sildenafil therapy in patients with pulmonary arterial hypertension

(2015) Vallerie McLaughlin et al.   EUROPEAN RESPIRATORY JOURNAL

Selexipag for the Treatment of Pulmonary Arterial Hypertension

(2015) Olivier Sitbon et al.   NEW ENGLAND JOURNAL OF MEDICINE

Initial Use of Ambrisentan plus Tadalafil in Pulmonary Arterial Hypertension

(2015) Nazzareno Galiè et al.   NEW ENGLAND JOURNAL OF MEDICINE

Interleukin-6/interleukin-21 signaling axis is critical in the pathogenesis of pulmonary arterial hypertension

(2015) Takahiro Hashimoto-Kataoka et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Diastolic dysfunction and endothelial dysfunction in systemic lupus erythematosus

(2015) Ali Yildiz et al.   RHEUMATOLOGY INTERNATIONAL

The effects of mycophenolate mofetil on cytokines and their receptors in pulmonary arterial hypertension in rats

(2015) YF Zhang et al.   SCANDINAVIAN JOURNAL OF RHEUMATOLOGY

Vascular Receptor Autoantibodies in Pulmonary Arterial Hypertension Associated with Systemic Sclerosis

(2014) Mike O. Becker et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Pulmonary Arterial Hypertension

(2014) Yen-Chun Lai et al.   CIRCULATION RESEARCH

Upfront triple combination therapy in pulmonary arterial hypertension: a pilot study

(2014) O. Sitbon et al.   EUROPEAN RESPIRATORY JOURNAL

Long-term results from the EARLY study of bosentan in WHO functional class II pulmonary arterial hypertension patients

(2014) Gérald Simonneau et al.   INTERNATIONAL JOURNAL OF CARDIOLOGY

Cardiac involvement in mixed connective tissue disease: A systematic review

(2014) Patompong Ungprasert et al.   INTERNATIONAL JOURNAL OF CARDIOLOGY

Prognostic Factors for Myositis-Associated Interstitial Lung Disease

(2014) Tomoyuki Fujisawa et al.   PLoS One

Addition of Sildenafil to Long-Term Intravenous Epoprostenol Therapy in Patients with Pulmonary Arterial Hypertension

(2013) Gérald Simonneau   ANNALS OF INTERNAL MEDICINE

Treatment of Idiopathic Pulmonary Fibrosis With Ambrisentan

(2013) Ganesh Raghu   ANNALS OF INTERNAL MEDICINE

Anticoagulation and Survival in Pulmonary Arterial Hypertension

(2013) Karen M. Olsson et al.   CIRCULATION

Macitentan and Morbidity and Mortality in Pulmonary Arterial Hypertension

(2013) Tomás Pulido et al.   NEW ENGLAND JOURNAL OF MEDICINE

Riociguat for the Treatment of Pulmonary Arterial Hypertension

(2013) Hossein-Ardeschir Ghofrani et al.   NEW ENGLAND JOURNAL OF MEDICINE

Survival in systemic sclerosis-associated pulmonary arterial hypertension in the modern management era

(2012) David Launay et al.   ANNALS OF THE RHEUMATIC DISEASES

Computed tomography findings of pulmonary venoocclusive disease in scleroderma patients presenting with precapillary pulmonary hypertension

(2012) S. Günther et al.   ARTHRITIS AND RHEUMATISM

Pulmonary Arterial Hypertension in Systemic Lupus Erythematosus: Current Status and Future Direction

(2012) Atiya Dhala   Clinical & Developmental Immunology

Riociguat for interstitial lung disease and pulmonary hypertension: a pilot trial

(2012) Marius M. Hoeper et al.   EUROPEAN RESPIRATORY JOURNAL

Major bleeding with vitamin K antagonist anticoagulants in pulmonary hypertension

(2012) Ivo R. Henkens et al.   EUROPEAN RESPIRATORY JOURNAL

Safety and Efficacy of Bosentan in Combination With Sildenafil in PAH Patients Who Experience Inadequate Clinical Response to Monotherapy: The COMPASS-3 Study

(2011) Raymond L. Benza et al.   CHEST

The short-term role of corticosteroid therapy for pulmonary arterial hypertension associated with connective tissue diseases: report of five cases and a literature review

(2011) M Kato et al.   LUPUS

A Histopathological Study of Pulmonary Hypertension in Connective Tissue Disease

(2011) Nobuhito Sasaki et al.   ALLERGOLOGY INTERNATIONAL

Validation of the 6 min walk test according to the OMERACT filter: a systematic literature review by the EPOSS-OMERACT group

(2010) J. Avouac et al.   ANNALS OF THE RHEUMATIC DISEASES

Elevated Levels of Inflammatory Cytokines Predict Survival in Idiopathic and Familial Pulmonary Arterial Hypertension

(2010) Elaine Soon et al.   CIRCULATION

Long-term response to calcium-channel blockers in non-idiopathic pulmonary arterial hypertension

(2010) D. Montani et al.   EUROPEAN HEART JOURNAL

Tadalafil Therapy for Pulmonary Arterial Hypertension

(2009) Nazzareno Galiè et al.   CIRCULATION

The effects and mechanisms of mycophenolate mofetil on pulmonary arterial hypertension in rats

(2009) Yi Zheng et al.   RHEUMATOLOGY INTERNATIONAL

Immunosuppressive therapy in lupus- and mixed connective tissue disease–associated pulmonary arterial hypertension: A retrospective analysis of twenty-three cases

(2008) Xavier Jais et al.   ARTHRITIS AND RHEUMATISM

Ambrisentan for the Treatment of Pulmonary Arterial Hypertension

(2008) Nazzareno Galiè et al.   CIRCULATION

Treatment of patients with mildly symptomatic pulmonary arterial hypertension with bosentan (EARLY study): a double-blind, randomised controlled trial

(2008) N Galiè et al.   LANCET

Rituximab treatment of pulmonary arterial hypertension associated with systemic lupus erythematosus: a case report

(2008) S Hennigan et al.   LUPUS