Fatal Prion Disease in a Mouse Model of Genetic E200K Creutzfeldt-Jakob Disease

Genetic Creutzfeldt-Jakob disease associated with the E200K mutation: characterization of a complex proteinopathy

(2010) Gabor G. Kovacs et al.   ACTA NEUROPATHOLOGICA

Transgenic animal models of neurodegeneration based on human genetic studies

(2010) Brandon K. Harvey et al.   JOURNAL OF NEURAL TRANSMISSION

Probing the Biology of Alzheimer's Disease in Mice

(2010) Karen H. Ashe et al.   NEURON

Oxidation of Helix-3 Methionines Precedes the Formation of PK Resistant PrPSc

(2010) Tamar Canello et al.   PLoS Pathogens

RNAi for the Treatment of Prion Disease: A Window for Intervention in Neurodegeneration?

(2009) Melanie White et al.   CNS & Neurological Disorders-Drug Targets

Molecular Pathology of Human Prion Diseases

(2009) Gabor Kovacs et al.   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

Absence of spontaneous disease and comparative prion susceptibility of transgenic mice expressing mutant human prion proteins

(2009) E. A. Asante et al.   JOURNAL OF GENERAL VIROLOGY

A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP

(2009) W. Yang et al.   JOURNAL OF NEUROSCIENCE

Prion Protein Glycosylation Is Not Required for Strain-Specific Neurotropism

(2009) J. R. Piro et al.   JOURNAL OF VIROLOGY

Clinical trials for prion disease: difficult challenges, but hope for the future

(2009) Michael D Geschwind   LANCET NEUROLOGY

Spontaneous Generation of Prion Infectivity in Fatal Familial Insomnia Knockin Mice

(2009) Walker S. Jackson et al.   NEURON

Induced Neuroprotection Independently From PrPSc Accumulation in a Mouse Model for Prion Disease Treated With Simvastatin

(2008) Yaron Haviv et al.   ARCHIVES OF NEUROLOGY

Systematic review of therapeutic interventions in human prion disease

(2008) L. A. Stewart et al.   NEUROLOGY

Mutant Prion Protein Expression Causes Motor and Memory Deficits and Abnormal Sleep Patterns in a Transgenic Mouse Model

(2008) Sara Dossena et al.   NEURON

Rodent models for prion diseases

(2008) Martin H. Groschup et al.   VETERINARY RESEARCH