The Metabolomic Bioenergetic Signature of Opa1-Disrupted Mouse Embryonic Fibroblasts Highlights Aspartate Deficiency
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Title
The Metabolomic Bioenergetic Signature of Opa1-Disrupted Mouse Embryonic Fibroblasts Highlights Aspartate Deficiency
Authors
Keywords
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Journal
Scientific Reports
Volume 8, Issue 1, Pages -
Publisher
Springer Nature
Online
2018-07-26
DOI
10.1038/s41598-018-29972-9
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Note: Only part of the references are listed.- Autophagy controls the pathogenicity of OPA1 mutations in dominant optic atrophy
- (2017) Mariame Selma Kane et al. JOURNAL OF CELLULAR AND MOLECULAR MEDICINE
- OPA1 Isoforms in the Hierarchical Organization of Mitochondrial Functions
- (2017) Valentina Del Dotto et al. Cell Reports
- The metabolomic signature of Leber’s hereditary optic neuropathy reveals endoplasmic reticulum stress
- (2016) Juan Manuel Chao de la Barca et al. BRAIN
- Absolute Quantification of Matrix Metabolites Reveals the Dynamics of Mitochondrial Metabolism
- (2016) Walter W. Chen et al. CELL
- OPA1-related disorders: Diversity of clinical expression, modes of inheritance and pathophysiology
- (2016) Juan Manuel Chao de la Barca et al. NEUROBIOLOGY OF DISEASE
- Loss of functional OPA1 unbalances redox state: implications in dominant optic atrophy pathogenesis
- (2016) Aurélie M. C. Millet et al. Annals of Clinical and Translational Neurology
- An Essential Role of the Mitochondrial Electron Transport Chain in Cell Proliferation Is to Enable Aspartate Synthesis
- (2015) Kıvanç Birsoy et al. CELL
- Supporting Aspartate Biosynthesis Is an Essential Function of Respiration in Proliferating Cells
- (2015) Lucas B. Sullivan et al. CELL
- Early-onset Behr syndrome due to compound heterozygous mutations in OPA1
- (2014) Dominique Bonneau et al. BRAIN
- Improved Locus-Specific Database forOPA1Mutations Allows Inclusion of Advanced Clinical Data
- (2014) Marc Ferré et al. HUMAN MUTATION
- OPA1 loss of function affects in vitro neuronal maturation
- (2013) Ambre M. Bertholet et al. BRAIN
- The dynamin GTPase OPA1: More than mitochondria?
- (2012) Pascale Belenguer et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH
- The human OPA1delTTAG mutation induces premature age-related systemic neurodegeneration in mouse
- (2012) Emmanuelle Sarzi et al. BRAIN
- Mitochondrial Fission, Fusion, and Stress
- (2012) R. J. Youle et al. SCIENCE
- Specific deficits in visual electrophysiology in a mouse model of dominant optic atrophy
- (2011) Alun R. Barnard et al. EXPERIMENTAL EYE RESEARCH
- OPA1 links human mitochondrial genome maintenance to mtDNA replication and distribution
- (2010) G. Elachouri et al. GENOME RESEARCH
- Characterization of Ca2+Signalling in Postnatal Mouse Retinal Ganglion Cells: Involvement of OPA1 in Ca2+Clearance
- (2010) Govindan Dayanithi et al. OPHTHALMIC GENETICS
- Hereditary optic neuropathies share a common mitochondrial coupling defect
- (2008) Arnaud Chevrollier et al. ANNALS OF NEUROLOGY
- OPA1 mutations induce mitochondrial DNA instability and optic atrophy 'plus' phenotypes
- (2007) P. Amati-Bonneau et al. BRAIN
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